{
  "id": 2879,
  "label": "paranasal sinus carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0000380",
  "properties": {
    "xrefs": [
      "DOID:0050619",
      "GARD:0009354",
      "MEDGEN:167751",
      "NCIT:C6014",
      "UMLS:C0854995"
    ],
    "synonyms": [
      "malignant neoplasm of paranasal sinus",
      "malignant paranasal sinus neoplasm",
      "paranasal sinus cancer",
      "accessory sinus cancer",
      "accessory sinus carcinoma",
      "cancer of paranasal sinus",
      "carcinoma of accessory sinus",
      "carcinoma of paranasal sinus",
      "carcinoma of the accessory sinus",
      "carcinoma of the paranasal sinus",
      "paranasal sinus carcinoma",
      "adenoid cystic carcinoma of accessory sinus",
      "epidermoid carcinoma of the paranasal sinus",
      "mucoepidermoid carcinoma of accessory sinus",
      "paranasal sinus adenocarcinoma",
      "paranasal sinus adenoid cystic carcinoma",
      "paranasal sinus mucoepidermoid carcinoma",
      "paranasal sinus squamous cell carcinoma",
      "squamous cell carcinoma of paranasal sinus"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      },
      {
        "ref": "MONDO:0005087",
        "name": "respiratory system disorder"
      },
      {
        "ref": "MONDO:0024623",
        "name": "otorhinolaryngologic disease"
      }
    ],
    "definition": "A malignant epithelial neoplasm arising in the paranasal sinus."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 8,
  "parents": [
    {
      "id": 4505,
      "label": "bone carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4262,
        6734
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2762",
          "GARD:0023132"
        ],
        "synonyms": [
          "bone element carcinoma",
          "carcinoma of bone element"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A carcinoma that involves the bone element."
      },
      "child_count": 14,
      "reference_id": "MONDO:0002415"
    },
    {
      "id": 20081,
      "label": "paranasal sinus cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2875,
        3050,
        4265,
        6984
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0025207",
          "MEDGEN:56305",
          "NCIT:C7487",
          "UMLS:C0153474"
        ],
        "synonyms": [
          "malignant accessory sinus neoplasm",
          "malignant accessory sinus tumor",
          "malignant accessory sinus tumour",
          "malignant neoplasm of accessory sinus",
          "malignant neoplasm of paranasal sinus",
          "malignant neoplasm of the accessory sinus",
          "malignant neoplasm of the paranasal sinus",
          "malignant paranasal sinus neoplasm",
          "malignant paranasal sinus tumor",
          "malignant paranasal sinus tumour",
          "malignant tumor of accessory sinus",
          "malignant tumor of paranasal sinus",
          "malignant tumor of the accessory sinus",
          "malignant tumor of the paranasal sinus",
          "malignant tumour of accessory sinus",
          "malignant tumour of paranasal sinus",
          "malignant tumour of the accessory sinus",
          "malignant tumour of the paranasal sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A primary or metastatic malignant neoplasm involving the paranasal sinuses."
      },
      "child_count": 8,
      "reference_id": "MONDO:0020669"
    },
    {
      "id": 23674,
      "label": "nasal cavity and paranasal sinus carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4185,
        23675
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0007650",
          "MEDGEN:328032",
          "NCIT:C54293",
          "UMLS:C1710095"
        ],
        "synonyms": [
          "nasal cavity and paranasal sinus cancer",
          "nasal cavity and paranasal sinus carcinoma",
          "paranasal sinus and nasal cavity cancer",
          "sinonasal carcinoma"
        ],
        "definition": "A carcinoma arising from the nasal cavity or paranasal sinuses."
      },
      "child_count": 4,
      "reference_id": "MONDO:0056819"
    }
  ],
  "children": [
    {
      "id": 3934,
      "label": "maxillary sinus carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        4264,
        7738,
        8294
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1357",
          "GARD:0023002",
          "ICD9:160.2",
          "MEDGEN:196632",
          "NCIT:C3540",
          "NCIT:C9332",
          "SCTID:363425008",
          "UMLS:C0740487"
        ],
        "synonyms": [
          "cancer of maxillary sinus",
          "carcinoma of maxillary sinus",
          "malignant maxillary sinus neoplasm",
          "malignant maxillary sinus tumor",
          "malignant maxillary sinus tumour",
          "malignant neoplasm of maxillary sinus",
          "malignant neoplasm of the maxillary sinus",
          "malignant tumor of maxillary sinus",
          "malignant tumor of the maxillary sinus",
          "malignant tumour of maxillary sinus",
          "malignant tumour of the maxillary sinus",
          "maxillary sinus cancer",
          "maxillary sinus carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0006858",
            "name": "mouth disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A carcinoma that arises from the maxillary sinus. Representative examples include squamous cell carcinoma, adenocarcinoma, and adenoid cystic carcinoma."
      },
      "child_count": 12,
      "reference_id": "MONDO:0001748"
    },
    {
      "id": 3941,
      "label": "frontal sinus cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        3942
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1360",
          "GARD:0023003",
          "ICD10CM:C31.2",
          "ICD9:160.4",
          "MEDGEN:57786",
          "NCIT:C3542",
          "SCTID:363427000",
          "UMLS:C0153478"
        ],
        "synonyms": [
          "cancer of frontal sinus",
          "frontal sinus cancer",
          "malignant frontal sinus neoplasm",
          "malignant frontal sinus tumor",
          "malignant frontal sinus tumour",
          "malignant neoplasm of frontal sinus",
          "malignant neoplasm of the frontal sinus",
          "malignant tumor of frontal sinus",
          "malignant tumor of the frontal sinus",
          "malignant tumour of frontal sinus",
          "malignant tumour of the frontal sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A malignant neoplasm involving the frontal sinus."
      },
      "child_count": 2,
      "reference_id": "MONDO:0001756"
    },
    {
      "id": 3943,
      "label": "paranasal sinus sarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2879,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1362",
          "GARD:0023005",
          "MEDGEN:233842",
          "NCIT:C6849",
          "UMLS:C1335342"
        ],
        "synonyms": [
          "accessory sinus sarcoma",
          "paranasal sinus sarcoma",
          "sarcoma of accessory sinus",
          "sarcoma of paranasal sinus",
          "sarcoma of the accessory sinus",
          "sarcoma of the paranasal sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A malignant soft tissue neoplasm that arises from the paranasal sinus."
      },
      "child_count": 0,
      "reference_id": "MONDO:0001758"
    },
    {
      "id": 3947,
      "label": "ethmoid sinus cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        3948
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1363",
          "GARD:0023007",
          "ICD10CM:C31.1",
          "ICD9:160.3",
          "MEDGEN:102272",
          "NCIT:C3541",
          "SCTID:363426009",
          "UMLS:C0153477"
        ],
        "synonyms": [
          "cancer of ethmoid sinus",
          "ethmoid sinus cancer",
          "malignant ethmoid sinus neoplasm",
          "malignant ethmoid sinus tumor",
          "malignant ethmoid sinus tumour",
          "malignant ethmoidal sinus neoplasm",
          "malignant ethmoidal sinus tumor",
          "malignant ethmoidal sinus tumour",
          "malignant neoplasm of ethmoid sinus",
          "malignant neoplasm of ethmoidal sinus",
          "malignant neoplasm of the ethmoid sinus",
          "malignant neoplasm of the ethmoidal sinus",
          "malignant tumor of ethmoid sinus",
          "malignant tumor of ethmoidal sinus",
          "malignant tumor of the ethmoid sinus",
          "malignant tumor of the ethmoidal sinus",
          "malignant tumour of ethmoid sinus",
          "malignant tumour of ethmoidal sinus",
          "malignant tumour of the ethmoid sinus",
          "malignant tumour of the ethmoidal sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A malignant neoplasm involving the ethmoid sinus."
      },
      "child_count": 6,
      "reference_id": "MONDO:0001763"
    },
    {
      "id": 4153,
      "label": "sphenoidal sinus cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        5888
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:14546",
          "GARD:0023054",
          "ICD10CM:C31.3",
          "ICD9:160.5",
          "MEDGEN:102273",
          "NCIT:C3543",
          "SCTID:363428005",
          "UMLS:C0153479"
        ],
        "synonyms": [
          "cancer of sphenoidal sinus",
          "malignant neoplasm of sphenoid sinus",
          "malignant neoplasm of sphenoidal sinus",
          "malignant neoplasm of the sphenoid sinus",
          "malignant neoplasm of the sphenoidal sinus",
          "malignant sphenoid sinus neoplasm",
          "malignant sphenoid sinus tumor",
          "malignant sphenoid sinus tumour",
          "malignant sphenoidal sinus neoplasm",
          "malignant sphenoidal sinus tumor",
          "malignant sphenoidal sinus tumour",
          "malignant tumor of sphenoid sinus",
          "malignant tumor of sphenoidal sinus",
          "malignant tumor of the sphenoid sinus",
          "malignant tumor of the sphenoidal sinus",
          "malignant tumour of sphenoid sinus",
          "malignant tumour of sphenoidal sinus",
          "malignant tumour of the sphenoid sinus",
          "malignant tumour of the sphenoidal sinus",
          "sphenoidal sinus cancer"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A malignant neoplasm involving the sphenoidal sinus."
      },
      "child_count": 2,
      "reference_id": "MONDO:0001994"
    },
    {
      "id": 7878,
      "label": "paranasal sinus adenoid cystic carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        6713
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0024379",
          "MEDGEN:233840",
          "NCIT:C6019",
          "UMLS:C1335337"
        ],
        "synonyms": [
          "accessory sinus adenoid cystic carcinoma",
          "adenoid cystic carcinoma of accessory sinus",
          "adenoid cystic carcinoma of paranasal sinus",
          "adenoid cystic carcinoma of the accessory sinus",
          "adenoid cystic carcinoma of the paranasal sinus",
          "paranasal sinus adenoid cystic carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A rare adenoid cystic carcinoma that arises from the paranasal sinuses. It usually has an aggressive clinical course characterized by high recurrence rates and distant metastases."
      },
      "child_count": 4,
      "reference_id": "MONDO:0006352"
    },
    {
      "id": 23399,
      "label": "paranasal sinus squamous cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2879,
        2965,
        11332
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2442",
          "GARD:0017927",
          "MEDGEN:79105",
          "NCIT:C8193",
          "Orphanet:500464",
          "UMLS:C0280334"
        ],
        "synonyms": [
          "epidermoid carcinoma of paranasal sinus",
          "epidermoid carcinoma of the paranasal sinus",
          "paranasal sinus epidermoid carcinoma",
          "paranasal sinus squamous cell carcinoma",
          "squamous cell carcinoma of paranasal sinus",
          "squamous cell carcinoma of the nasal cavity and sinuses",
          "squamous cell carcinoma of the paranasal sinus",
          "squamous cell carcinoma of the nasal cavity and paranasal sinuses"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A squamous cell carcinoma that arises from the mucosal epithelial surface of the ethmoid, frontal, maxillary, or sphenoid sinus. Patients may present with nasal fullness, obstruction, and/or epistaxis."
      },
      "child_count": 12,
      "reference_id": "MONDO:0044705"
    },
    {
      "id": 23486,
      "label": "paranasal sinus mucoepidermoid carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2879,
        5029
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0025925",
          "MEDGEN:235461",
          "NCIT:C6018",
          "UMLS:C1335340"
        ],
        "synonyms": [
          "accessory sinus mucoepidermoid carcinoma",
          "mucoepidermoid carcinoma of accessory sinus",
          "mucoepidermoid carcinoma of paranasal sinus",
          "mucoepidermoid carcinoma of the accessory sinus",
          "mucoepidermoid carcinoma of the paranasal sinus",
          "paranasal sinus mucoepidermoid carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A rare carcinoma that arises from the paranasal sinus. It is characterized by the presence of epidermoid cells, mucus producing cells, and cells of intermediate type."
      },
      "child_count": 0,
      "reference_id": "MONDO:0044956"
    }
  ],
  "roots": [
    {
      "id": 4505,
      "label": "bone carcinoma"
    },
    {
      "id": 20081,
      "label": "paranasal sinus cancer"
    },
    {
      "id": 23674,
      "label": "nasal cavity and paranasal sinus carcinoma"
    }
  ]
}