{
  "id": 3165,
  "label": "adult acute monocytic leukemia",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0000875",
  "properties": {
    "xrefs": [
      "DOID:0080149",
      "EFO:1001933",
      "GARD:0022837",
      "MEDGEN:128856",
      "NANDO:2200008",
      "NANDO:2200009",
      "NCIT:C8263",
      "UMLS:C0280634"
    ],
    "synonyms": [
      "acute monocytic leukaemia",
      "acute monocytic leukemia",
      "M5b adult acute differentiated monocytic leukaemia",
      "M5b adult acute differentiated monocytic leukemia",
      "M5b adult acute leukaemia",
      "M5b adult acute leukemia",
      "acute monocytic leukaemia of adults",
      "acute monocytic leukemia of adults",
      "adult acute differentiated monocytic leukaemia (M5b)",
      "adult acute differentiated monocytic leukemia (M5b)",
      "adult acute monocytic leukemia"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      },
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "A acute monocytic leukemia that occurs in an adult."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 9231,
      "label": "acute monocytic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6392,
        18806
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "CSP:2004-2820",
          "DOID:8864",
          "EFO:0000221",
          "GARD:0000525",
          "ICD10CM:C93.0",
          "ICD9:206.0",
          "ICDO:9891/3",
          "MEDGEN:7319",
          "MESH:D007948",
          "MedDRA:10000871",
          "MedDRA:10059439",
          "NANDO:2200008",
          "NANDO:2200009",
          "NCIT:C4861",
          "OMIM:151380",
          "ONCOTREE:AMOL",
          "Orphanet:514",
          "SCTID:413441006",
          "UMLS:C0023465",
          "icd11.foundation:517546180"
        ],
        "synonyms": [
          "monocytic leukaemia",
          "monocytic leukemia",
          "AML M5",
          "acute monoblastic leukaemia and acute monocytic leukaemia",
          "acute monocytic leukaemia (FAB M5B)",
          "acute monocytic leukaemia (FAB M5b)",
          "acute monocytic leukemia",
          "acute monocytic leukemia (FAB M5B)",
          "acute monocytic leukemia (FAB M5b)",
          "acute monocytic leukemia, morphology (morphologic abnormality)",
          "leukemia, monocytic, malignant",
          "monocytic leukemia, acute",
          "AML-M5",
          "acute monoblastic leukaemia",
          "acute monoblastic leukemia",
          "acute monoblastic/monocytic leukaemia",
          "acute monoblastic/monocytic leukemia",
          "acute myeloblastic leukaemia type 5",
          "acute myeloblastic leukemia type 5",
          "leukemia, acute monocytic"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "Acute monoblastic leukemia (AML-M5), is one of the most common subtypes of acute myeloid leukemia (AML) that is either comprised of more than 80% of monoblasts (AML-M5a) or 30-80% monoblasts with (pro)monocytic differentiation (AML-M5b). AML-M5 presents with asthenia, pallor, fever, and dizziness. Specific features of AML-M5 include hyperleukocytosis, propensity for extramedullary infiltrates, coagulation abnormalities including disseminated intravascular coagulation and neurological disorders. Leukemia cutis and gingival infiltration can also be seen. A characteristic translocation observed in AML-M5 is t(9;11)."
      },
      "child_count": 6,
      "reference_id": "MONDO:0007896"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 9231,
      "label": "acute monocytic leukemia"
    }
  ]
}