{
  "id": 3282,
  "label": "prolymphocytic leukemia",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0001023",
  "properties": {
    "xrefs": [
      "DOID:1039",
      "GARD:0011965",
      "ICD9:204.80",
      "ICDO:9832/3",
      "MEDGEN:6062",
      "MESH:D015463",
      "NCIT:C3181",
      "SCTID:110006004",
      "UMLS:C0023486"
    ],
    "synonyms": [
      "prolymphocytic leukaemia (B or T)",
      "prolymphocytic leukaemia (B or T-cell)",
      "prolymphocytic leukemia",
      "prolymphocytic leukemia (B or T)",
      "prolymphocytic leukemia (B or T-cell)"
    ],
    "categories": [
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "A mature B- or T- cell leukemia with progressive clinical course. It is characterized by the presence of medium-sized lymphocytes with visible nucleoli (prolymphocytes) in the peripheral blood, bone marrow, and spleen."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 3,
  "parents": [
    {
      "id": 3274,
      "label": "chronic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6789
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1036",
          "ICD9:208.10",
          "MEDGEN:220905",
          "NCIT:C3483",
          "SCTID:92812005",
          "UMLS:C1279296"
        ],
        "synonyms": [
          "chronic leukaemia (disease)",
          "chronic leukemia",
          "chronic leukemia (disease)",
          "leukaemia (disease), chronic",
          "leukemia (disease), chronic",
          "adult chronic leukaemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A slowly progressing leukemia characterized by a clonal (malignant) proliferation of maturing and mature myeloid cells or mature lymphocytes. When the clonal cellular population is composed of myeloid cells, the process is called chronic myelogenous leukemia. When the clonal cellular population is composed of lymphocytes, it is classified as chronic lymphocytic leukemia, hairy cell leukemia, or T-cell large granular lymphocyte leukemia."
      },
      "child_count": 8,
      "reference_id": "MONDO:0001014"
    },
    {
      "id": 6710,
      "label": "acute lymphoblastic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5444,
        6890,
        7079,
        11789,
        18836
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:9952",
          "EFO:0000220",
          "GARD:0000522",
          "HP:0006721",
          "ICD10CM:C91.0",
          "ICD9:204",
          "ICD9:204.0",
          "ICD9:204.00",
          "ICD9:204.9",
          "ICDO:9835/3",
          "MEDGEN:7317",
          "NCIT:C3167",
          "Orphanet:513",
          "SCTID:91857003",
          "UMLS:C0023449"
        ],
        "synonyms": [
          "lymphoblastic leukaemia",
          "lymphoblastic leukemia",
          "ALL",
          "ALL - acute lymphocytic leukaemia",
          "ALL - acute lymphocytic leukemia",
          "acute lymphoblastic leukaemia (ALL)",
          "acute lymphoblastic leukaemia (disease)",
          "acute lymphoblastic leukemia",
          "acute lymphoblastic leukemia (ALL)",
          "acute lymphoblastic leukemia (disease)",
          "acute lymphoblastic leukemia/lymphoma",
          "acute lymphocytic leukaemia",
          "acute lymphocytic leukemia",
          "acute lymphocytic leukemias",
          "acute lymphogenous leukaemia",
          "acute lymphogenous leukemia",
          "acute lymphoid leukaemia",
          "acute lymphoid leukemia",
          "leukemia, lymphoblastic, malignant",
          "lymphoblastic leukemia, acute",
          "precursor Lymphoblasic leukaemia",
          "precursor Lymphoblasic leukemia",
          "precursor cell lymphoblastic leukaemia",
          "precursor cell lymphoblastic leukemia",
          "precursor lymphoblastic leukaemia",
          "precursor lymphoblastic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "Leukemia with an acute onset, characterized by the presence of lymphoblasts in the bone marrow and the peripheral blood. It includes the acute B lymphoblastic leukemia and acute T lymphoblastic leukemia."
      },
      "child_count": 60,
      "reference_id": "MONDO:0004967"
    }
  ],
  "children": [
    {
      "id": 4970,
      "label": "splenic manifestation of prolymphocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3282,
        5941,
        6479
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:4334",
          "GARD:0023310",
          "MEDGEN:277663",
          "NCIT:C7297",
          "UMLS:C1336066"
        ],
        "synonyms": [
          "prolymphocytic leukaemia of spleen",
          "prolymphocytic leukemia of spleen",
          "spleen prolymphocytic leukaemia",
          "spleen prolymphocytic leukemia",
          "splenic manifestation of prolymphocytic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A prolymphocytic leukemia that involves the spleen."
      },
      "child_count": 0,
      "reference_id": "MONDO:0002966"
    },
    {
      "id": 19286,
      "label": "B-cell prolymphocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3282,
        6694,
        17875
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0081041",
          "EFO:1000102",
          "GARD:0008223",
          "ICDO:9833/3",
          "MEDGEN:105396",
          "MESH:D054403",
          "NCIT:C4753",
          "ONCOTREE:BPLL",
          "Orphanet:86852",
          "SCTID:277619001",
          "UMLS:C0475801",
          "icd11.foundation:1997215876"
        ],
        "synonyms": [
          "B prolymphocytic leukaemia",
          "B prolymphocytic leukemia",
          "B-PLL",
          "B-cell prolymphocytic leukemia",
          "BPLL"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A neoplasm of prolymphocytes affecting the blood, bone marrow, and spleen. It is characterized by prolymphocytes exceeding 55% of the lymphoid cells in the blood and profound splenomegaly."
      },
      "child_count": 0,
      "reference_id": "MONDO:0019461"
    },
    {
      "id": 19293,
      "label": "T-cell prolymphocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2906,
        3282,
        5443,
        6706
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0081042",
          "EFO:1000560",
          "GARD:0013731",
          "ICDO:9834/3",
          "MEDGEN:391707",
          "MESH:D015461",
          "MedDRA:10042985",
          "NCIT:C4752",
          "ONCOTREE:TPLL",
          "Orphanet:86871",
          "SCTID:277545003",
          "SCTID:277567002",
          "UMLS:C2363142",
          "icd11.foundation:352523899"
        ],
        "synonyms": [
          "CLL, T-cell",
          "T cell CLL",
          "T cell chronic lymphocytic leukaemia",
          "T cell chronic lymphocytic leukemia",
          "T cell prolymphocytic leukaemia",
          "T cell prolymphocytic leukemia",
          "T prolymphocytic leukaemia",
          "T prolymphocytic leukemia",
          "T-PLL",
          "T-cell CLL",
          "T-cell chronic lymphocytic leukaemia",
          "T-cell chronic lymphocytic leukemia",
          "T-cell prolymphocytic leukemia",
          "chronic T-cell leukaemia",
          "chronic T-cell leukemia",
          "chronic T-cell lymphocytic leukaemia",
          "chronic T-cell lymphocytic leukemia",
          "TPLL",
          "leukemia, T-cell, chronic"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A slow-growing type of leukemia (blood cancer) in which too many lymphocytes are found in the bone marrow and/or blood. The T-cell is specified as the defective cell line."
      },
      "child_count": 0,
      "reference_id": "MONDO:0019468"
    }
  ],
  "roots": [
    {
      "id": 3274,
      "label": "chronic leukemia"
    },
    {
      "id": 6710,
      "label": "acute lymphoblastic leukemia"
    }
  ]
}