{
  "id": 4194,
  "label": "pulmonary systemic sclerosis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002047",
  "properties": {
    "xrefs": [
      "DOID:1578",
      "GARD:0023060",
      "ICD9:517.2",
      "MEDGEN:573414",
      "SCTID:196133001",
      "UMLS:C0339904"
    ],
    "synonyms": [
      "lung involvement in systemic sclerosis",
      "scleroderma lung disease",
      "scleroderma of lung"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      },
      {
        "ref": "MONDO:0005087",
        "name": "respiratory system disorder"
      }
    ]
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 6827,
      "label": "systemic sclerosis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6820,
        19180
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:418",
          "EFO:0000717",
          "GARD:0009748",
          "ICD10CM:M34",
          "ICD10WHO:M34",
          "ICD9:710.1",
          "MEDGEN:19897",
          "MESH:D012595",
          "MedDRA:10042953",
          "NANDO:1200277",
          "NANDO:2200429",
          "NCIT:C72070",
          "NORD:2007",
          "Orphanet:90291",
          "SCTID:89155008",
          "UMLS:C0036421",
          "icd11.foundation:1084365812"
        ],
        "synonyms": [
          "Scleroderma",
          "PSS (progressive systemic sclerosis)",
          "SSc",
          "SSc, diffuse sclerosis",
          "Scleroderma (& [systemic sclerosis])",
          "Scleroderma, diffuse",
          "Scleroderma, systemic",
          "Systemic Scleroderma",
          "diffuse Scleroderma",
          "diffuse sclerosis",
          "systemic Scleroderma",
          "systemic scleroderma",
          "systemic sclerosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. The two types of systemic scleroderma, limited cutaneous and diffuse cutaneous are classified with focus on the extent of affected skin. A relationship exists between the extent of skin area affected and degree of internal organ/system involvement. Systemic scleroderma can manifest itself in pulmonary fibrosis, Raynaud's syndrome, digestive system telangiectasias, renal hypertension and/or pulmonary hypertension."
      },
      "child_count": 12,
      "reference_id": "MONDO:0005100"
    },
    {
      "id": 6971,
      "label": "lung disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2809
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:850",
          "EFO:0003818",
          "ICD9:518.89",
          "MEDGEN:7399",
          "MESH:D008171",
          "NCIT:C3198",
          "SCTID:19829001",
          "UMLS:C0024115"
        ],
        "synonyms": [
          "disease of lung",
          "disease or disorder of lung",
          "disorder of lung",
          "lung disease",
          "lung disease or disorder",
          "lung disorder",
          "lung disorders",
          "pulmonary disease",
          "pulmonary diseases",
          "pulmonary disorder",
          "pulmonary disorders"
        ],
        "categories": [
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          }
        ],
        "definition": "A disease involving the lung."
      },
      "child_count": 33,
      "reference_id": "MONDO:0005275"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 6827,
      "label": "systemic sclerosis"
    },
    {
      "id": 6971,
      "label": "lung disorder"
    }
  ]
}