{
  "id": 4274,
  "label": "cutaneous undifferentiated pleomorphic sarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002141",
  "properties": {
    "xrefs": [
      "DOID:1906",
      "GARD:0023075",
      "ICD9:171.9",
      "MEDGEN:224813",
      "NCIT:C5576",
      "SCTID:404014008",
      "UMLS:C1275254",
      "icd11.foundation:361875781"
    ],
    "synonyms": [
      "cutaneous malignant fibrous histiocytoma",
      "cutaneous unclassified pleomorphic sarcoma",
      "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous \"MFH\")",
      "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous \"malignant fibrous histiocytoma\")",
      "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous)",
      "cutaneous undifferentiated pleomorphic sarcoma",
      "malignant cutaneous fibrous histiocytoma",
      "malignant fibrous histiocytoma of skin",
      "malignant fibrous histiocytoma of the skin",
      "malignant skin fibrous histiocytoma",
      "undifferentiated pleomorphic sarcoma of zone of skin",
      "zone of skin undifferentiated pleomorphic sarcoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "An undifferentiated pleomorphic sarcoma arising from the skin. It is characterized by the presence of spindle cells in a storiform pattern and histiocytes with abundant cytoplasm."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4275,
      "label": "undifferentiated pleomorphic sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7165,
        18239,
        20297
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1907",
          "EFO:1001972",
          "GARD:0006963",
          "HGNC:16982",
          "ICD9:171.9",
          "ICDO:8830/3",
          "MEDGEN:87248",
          "MESH:D051677",
          "MedDRA:10025552",
          "NCIT:C114541",
          "NCIT:C4247",
          "ONCOTREE:MFH",
          "Orphanet:2023",
          "SCTID:443439001",
          "UMLS:C0334463"
        ],
        "synonyms": [
          "MFH",
          "Storiform-pleomorphic MFH",
          "Storiform-pleomorphic fibrous histiocytoma",
          "Storiform-pleomorphic malignant fibrous histiocytoma",
          "UPS",
          "Unclassified Pleomorphic sarcoma (formerly \"MFH\")",
          "Unclassified Pleomorphic sarcoma (formerly \"malignant fibrous histiocytoma\")",
          "adult malignant fibrous histiocytoma",
          "adult unclassified pleomorphic sarcoma",
          "adult undifferentiated pleomorphic sarcoma",
          "fibrous histiocytoma, malignant",
          "fibrous histiocytoma, malignant (morphologic abnormality)",
          "fibroxanthosarcoma",
          "fibroxanthosarcoma (morphologic abnormality)",
          "histiocytoma, fibrous, malignant",
          "malignant fibrous cytoma",
          "malignant fibrous histiocytoma",
          "malignant fibrous histiocytoma of soft tissue and bone",
          "malignant fibrous histiocytoma of the soft tissue and bone",
          "malignant fibroxanthoma",
          "unclassified pleomorphic sarcoma",
          "undifferentiated pleomorphic sarcoma",
          "undifferentiated pleomorphic soft tissue sarcoma",
          "malignant fibrohistiocytic tumors",
          "malignant fibrohistiocytic tumours",
          "undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma."
      },
      "child_count": 9,
      "reference_id": "MONDO:0002142"
    },
    {
      "id": 7932,
      "label": "skin sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5298,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2687",
          "EFO:1000531",
          "GARD:0024403",
          "MEDGEN:208989",
          "NCIT:C5585",
          "UMLS:C0856900"
        ],
        "synonyms": [
          "cutaneous sarcoma",
          "sarcoma of skin",
          "sarcoma of the skin",
          "sarcoma of zone of skin",
          "skin sarcoma",
          "zone of skin sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          }
        ],
        "definition": "A sarcoma that arises from the skin. Representative examples include Kaposi sarcoma, angiosarcoma, lymphangiosarcoma, liposarcoma, and leiomyosarcoma."
      },
      "child_count": 10,
      "reference_id": "MONDO:0006414"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4275,
      "label": "undifferentiated pleomorphic sarcoma"
    },
    {
      "id": 7932,
      "label": "skin sarcoma"
    }
  ]
}