{
  "id": 4275,
  "label": "undifferentiated pleomorphic sarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002142",
  "properties": {
    "xrefs": [
      "DOID:1907",
      "EFO:1001972",
      "GARD:0006963",
      "HGNC:16982",
      "ICD9:171.9",
      "ICDO:8830/3",
      "MEDGEN:87248",
      "MESH:D051677",
      "MedDRA:10025552",
      "NCIT:C114541",
      "NCIT:C4247",
      "ONCOTREE:MFH",
      "Orphanet:2023",
      "SCTID:443439001",
      "UMLS:C0334463"
    ],
    "synonyms": [
      "MFH",
      "Storiform-pleomorphic MFH",
      "Storiform-pleomorphic fibrous histiocytoma",
      "Storiform-pleomorphic malignant fibrous histiocytoma",
      "UPS",
      "Unclassified Pleomorphic sarcoma (formerly \"MFH\")",
      "Unclassified Pleomorphic sarcoma (formerly \"malignant fibrous histiocytoma\")",
      "adult malignant fibrous histiocytoma",
      "adult unclassified pleomorphic sarcoma",
      "adult undifferentiated pleomorphic sarcoma",
      "fibrous histiocytoma, malignant",
      "fibrous histiocytoma, malignant (morphologic abnormality)",
      "fibroxanthosarcoma",
      "fibroxanthosarcoma (morphologic abnormality)",
      "histiocytoma, fibrous, malignant",
      "malignant fibrous cytoma",
      "malignant fibrous histiocytoma",
      "malignant fibrous histiocytoma of soft tissue and bone",
      "malignant fibrous histiocytoma of the soft tissue and bone",
      "malignant fibroxanthoma",
      "unclassified pleomorphic sarcoma",
      "undifferentiated pleomorphic sarcoma",
      "undifferentiated pleomorphic soft tissue sarcoma",
      "malignant fibrohistiocytic tumors",
      "malignant fibrohistiocytic tumours",
      "undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 3,
  "parents": [
    {
      "id": 7165,
      "label": "histiocytoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6798
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:4231",
          "EFO:0005561",
          "ICDO:8831/0",
          "MEDGEN:267592",
          "MESH:D051642",
          "NCIT:C35765",
          "UMLS:C1509147",
          "icd11.foundation:1211753554"
        ],
        "synonyms": [
          "histiocytoma"
        ],
        "definition": "A mesenchymal tumor composed of fibroblastic and histiocytic cells."
      },
      "child_count": 3,
      "reference_id": "MONDO:0005509"
    },
    {
      "id": 18239,
      "label": "soft tissue sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6816,
        21548
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0070663",
          "EFO:1001968",
          "GARD:0004898",
          "MEDGEN:1642116",
          "NCIT:C9306",
          "NORD:1953",
          "Orphanet:3394",
          "SCTID:424952003",
          "UMLS:C4551687"
        ],
        "synonyms": [
          "malignant soft tissue tumor",
          "malignant soft tissue tumour",
          "connective tissue sarcoma",
          "malignant mesenchymal tumor",
          "malignant mesenchymal tumour",
          "non-Rhabdo. soft tissue sarcoma",
          "sarcoma of soft tissue",
          "sarcoma of the soft tissue",
          "soft part sarcoma",
          "soft tissue sarcoma"
        ],
        "definition": "A malignant neoplasm arising from muscle tissue, adipose tissue, blood vessels, fibrous tissue, or other supportive tissues excluding the bones."
      },
      "child_count": 92,
      "reference_id": "MONDO:0018078"
    },
    {
      "id": 20297,
      "label": "bone sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4262,
        6816
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080639",
          "GARD:0020547",
          "ICD9:170.9",
          "MEDGEN:352831",
          "MedDRA:10006007",
          "NCIT:C9312",
          "Orphanet:223727",
          "SCTID:448710000",
          "UMLS:C1704327"
        ],
        "synonyms": [
          "bone sarcoma",
          "osseous sarcoma",
          "sarcoma of bone",
          "sarcoma of the bone",
          "skeletal sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A sarcoma that arises from the bone. Representative examples are osteosarcoma and chondrosarcoma."
      },
      "child_count": 26,
      "reference_id": "MONDO:0021054"
    }
  ],
  "children": [
    {
      "id": 4274,
      "label": "cutaneous undifferentiated pleomorphic sarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4275,
        7932
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1906",
          "GARD:0023075",
          "ICD9:171.9",
          "MEDGEN:224813",
          "NCIT:C5576",
          "SCTID:404014008",
          "UMLS:C1275254",
          "icd11.foundation:361875781"
        ],
        "synonyms": [
          "cutaneous malignant fibrous histiocytoma",
          "cutaneous unclassified pleomorphic sarcoma",
          "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous \"MFH\")",
          "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous \"malignant fibrous histiocytoma\")",
          "cutaneous unclassified pleomorphic sarcoma (formerly cutaneous)",
          "cutaneous undifferentiated pleomorphic sarcoma",
          "malignant cutaneous fibrous histiocytoma",
          "malignant fibrous histiocytoma of skin",
          "malignant fibrous histiocytoma of the skin",
          "malignant skin fibrous histiocytoma",
          "undifferentiated pleomorphic sarcoma of zone of skin",
          "zone of skin undifferentiated pleomorphic sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "An undifferentiated pleomorphic sarcoma arising from the skin. It is characterized by the presence of spindle cells in a storiform pattern and histiocytes with abundant cytoplasm."
      },
      "child_count": 0,
      "reference_id": "MONDO:0002141"
    },
    {
      "id": 5462,
      "label": "malignant giant cell tumor of soft parts",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4275,
        4492
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5638",
          "GARD:0023564",
          "ICDO:9251/3",
          "MEDGEN:90807",
          "NCIT:C8380",
          "UMLS:C0334554"
        ],
        "synonyms": [
          "giant cell fibrous histiocytoma",
          "giant cell malignant fibrous histiocytoma",
          "malignant Osteoclastoma",
          "malignant giant cell neoplasm of soft parts",
          "malignant giant cell tumor of soft parts",
          "malignant giant cell tumor of soft parts (morphologic abnormality)",
          "malignant giant cell tumour of soft parts (morphologic abnormality)",
          "undifferentiated pleomorphic sarcoma with osteoclast-like giant cells"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "An undifferentiated pleomorphic sarcoma characterized by the presence of osteoclast-like giant cells and cellular pleomorphism."
      },
      "child_count": 0,
      "reference_id": "MONDO:0003561"
    },
    {
      "id": 7977,
      "label": "undifferentiated pleomorphic sarcoma, inflammatory variant",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4275
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:6192",
          "EFO:1000608",
          "GARD:0024429",
          "MEDGEN:235211",
          "NCIT:C6497",
          "UMLS:C1334180"
        ],
        "synonyms": [
          "inflammatory MFH",
          "inflammatory malignant fibrous histiocytoma",
          "malignant xanthogranuloma",
          "undifferentiated pleomorphic sarcoma, inflammatory variant"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "An undifferentiated pleomorphic sarcoma characterized by the presence of numerous inflammatory cells."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006480"
    }
  ],
  "roots": [
    {
      "id": 7165,
      "label": "histiocytoma"
    },
    {
      "id": 18239,
      "label": "soft tissue sarcoma"
    },
    {
      "id": 20297,
      "label": "bone sarcoma"
    }
  ]
}