{
  "id": 4495,
  "label": "hepatic vascular disorder",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002405",
  "properties": {
    "xrefs": [
      "DOID:272",
      "ICD9:573.8",
      "MEDGEN:140779",
      "NCIT:C35442",
      "SCTID:235878005",
      "UMLS:C0400923"
    ],
    "synonyms": [
      "hepatic vascular disorder",
      "liver vascular disorder"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "A non-neoplastic or neoplastic vascular disorder that affects the liver. Representative examples include veno-occlusive disease, hemangioma, lymphangioma, and angiosarcoma."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 11,
  "parents": [
    {
      "id": 6878,
      "label": "liver disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4586,
        6875
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:409",
          "EFO:0001421",
          "ICD10CM:K70-K77",
          "ICD9:573.8",
          "ICD9:573.9",
          "MEDGEN:893061",
          "MESH:D008107",
          "NCIT:C3196",
          "SCTID:235856003",
          "UMLS:C4021780",
          "icd11.foundation:1784240230"
        ],
        "synonyms": [
          "disease of liver",
          "disease or disorder of liver",
          "disorder of liver",
          "hepatic disease",
          "hepatic disorder",
          "liver and intrahepatic bile duct disorder",
          "liver disease",
          "liver disease or disorder",
          "liver disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A disease involving the liver."
      },
      "child_count": 64,
      "reference_id": "MONDO:0005154"
    },
    {
      "id": 7065,
      "label": "vascular disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6736
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:178",
          "EFO:0004264",
          "ICD10CM:I00-I99",
          "ICD10CM:I70-I79",
          "ICD9:442.9",
          "MEDGEN:22621",
          "MESH:D014652",
          "NANDO:2100294",
          "NCIT:C35117",
          "SCTID:27550009",
          "UMLS:C0042373"
        ],
        "synonyms": [
          "disease of vasculature",
          "disease or disorder of vasculature",
          "disorder of vasculature",
          "vascular disorder",
          "vasculature disease",
          "vasculature disease or disorder",
          "vasculopathy"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A general term used to describe any disease affecting blood vessels]. It includes vascular abnormalities caused by degenerative, metabolic and inflammatory conditions, embolic diseases, coagulative disorders, and functional disorders such as posteri or reversible encephalopathy syndrome."
      },
      "child_count": 60,
      "reference_id": "MONDO:0005385"
    }
  ],
  "children": [
    {
      "id": 3567,
      "label": "portal vein thrombosis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3150,
        4495,
        6420
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:11695",
          "ICD10CM:I81",
          "ICD10WHO:I81",
          "ICD9:452",
          "MEDGEN:56372",
          "NCIT:C78565",
          "SCTID:17920008",
          "UMLS:C0155773",
          "icd11.foundation:866276949"
        ],
        "synonyms": [
          "portal vein thrombotic disease",
          "thrombotic disease of portal vein"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "The formation of a blood clot (thrombus) in the portal vein."
      },
      "child_count": 0,
      "reference_id": "MONDO:0001339"
    },
    {
      "id": 3971,
      "label": "hepatic infarction",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:13738",
          "ICD9:573.4",
          "MEDGEN:508812",
          "MESH:D000081011",
          "SCTID:17890003",
          "UMLS:C0151731",
          "icd11.foundation:1003389114"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0001787"
    },
    {
      "id": 3972,
      "label": "nutmeg liver",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:13739",
          "ICD10CM:K76.1",
          "ICD9:573.0",
          "MEDGEN:510207",
          "SCTID:34736002",
          "UMLS:C0156195",
          "icd11.foundation:707272147"
        ],
        "synonyms": [
          "chronic passive congestion of liver"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0001788"
    },
    {
      "id": 4483,
      "label": "liver angiosarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4487,
        4495,
        17394
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:268",
          "GARD:0005813",
          "ICD10CM:C22.3",
          "ICDO:9124/3",
          "MEDGEN:138027",
          "NCIT:C4438",
          "ONCOTREE:LIAS",
          "SCTID:109844006",
          "UMLS:C0345907",
          "icd11.foundation:965491615"
        ],
        "synonyms": [
          "angiosarcoma (disease) of liver",
          "angiosarcoma of liver",
          "angiosarcoma of the liver",
          "hemangiosarcoma of liver",
          "hemangiosarcoma of the liver",
          "hepatic angiosarcoma",
          "hepatic hemangiosarcoma",
          "liver angiosarcoma",
          "liver angiosarcoma (disease)",
          "liver hemangiosarcoma",
          "primary angiosarcoma of liver",
          "primary angiosarcoma of the liver",
          "Lias"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A malignant vascular neoplasm arising from the liver."
      },
      "child_count": 0,
      "reference_id": "MONDO:0002387"
    },
    {
      "id": 6495,
      "label": "peliosis hepatis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:914",
          "EFO:1001387",
          "ICD10CM:K76.4",
          "MEDGEN:10618",
          "MESH:D010382",
          "SCTID:58008004",
          "UMLS:C0030781",
          "icd11.foundation:1210061614"
        ],
        "synonyms": [
          "hepatic peliosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A vascular disease of the liver characterized by the occurrence of multiple blood-filled cysts or cavities. The cysts are lined with endothelial cells; the cavities lined with hepatic parenchymal cells (hepatocytes). Peliosis hepatis has been associated with use of anabolic steroids (anabolic agents) and certain drugs."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004717"
    },
    {
      "id": 6808,
      "label": "portal hypertension",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:10762",
          "EFO:0000666",
          "ICD10CM:K76.6",
          "ICD9:572.3",
          "MEDGEN:9375",
          "MESH:D006975",
          "NCIT:C3119",
          "SCTID:34742003",
          "UMLS:C0020541",
          "icd11.foundation:1506184775"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "Increased blood pressure in the portal venous system. It is most commonly caused by cirrhosis. Other causes include portal vein thrombosis, Budd-Chiari syndrome, and right heart failure. Complications include ascites, esophageal varices, encephalopathy, and splenomegaly."
      },
      "child_count": 0,
      "reference_id": "MONDO:0005080"
    },
    {
      "id": 8235,
      "label": "hepatic vein thrombosis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:11512",
          "EFO:1000966",
          "MEDGEN:9217",
          "MedDRA:10006537",
          "MedDRA:10019713",
          "SCTID:38739001",
          "UMLS:C0019154",
          "icd11.foundation:2131410813"
        ],
        "synonyms": [
          "hepatic vein thrombosis",
          "Budd-Chiari syndrome"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A condition in which the hepatic venous outflow is obstructed anywhere from the small hepatic veins to the junction of the inferior vena cava and the right atrium. Usually the blockage is extrahepatic and caused by blood clots (thrombus) or fibrous webs. Parenchymal fibrosis is uncommon."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006786"
    },
    {
      "id": 12077,
      "label": "Budd-Chiari syndrome",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0005968",
          "ICD10CM:I82.0",
          "ICD9:453.0",
          "MEDGEN:163632",
          "MESH:D006502",
          "MedDRA:10006537",
          "NANDO:1200437",
          "OMIM:600880",
          "Orphanet:131",
          "SCTID:82385007",
          "UMLS:C0856761",
          "icd11.foundation:1300118676"
        ],
        "synonyms": [
          "Budd-Chiari syndrome",
          "Budd-Chiari syndrome, somatic",
          "BDCHS",
          "membranous obstruction of Inferior vena cava",
          "membranous obstruction of the inferior vena cava"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava."
      },
      "child_count": 0,
      "reference_id": "MONDO:0010947"
    },
    {
      "id": 19328,
      "label": "hepatic veno-occlusive disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080177",
          "GARD:0013004",
          "ICD10CM:K76.5",
          "ICD9:453.89",
          "MEDGEN:5514",
          "MESH:D006504",
          "MedDRA:10047216",
          "NCIT:C26793",
          "NORD:879",
          "Orphanet:890",
          "SCTID:65617004",
          "UMLS:C0019156",
          "icd11.foundation:762044088",
          "icd11.foundation:901464792"
        ],
        "synonyms": [
          "Budd Chiari Syndrome",
          "hepatic Vod",
          "liver veno-occlusive disease",
          "sinusoidal obstruction syndrome",
          "veno-occlusive disease"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "Hepatic veno-occlusive disease (hepatic VOD) is a condition resulting from toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins."
      },
      "child_count": 1,
      "reference_id": "MONDO:0019514"
    },
    {
      "id": 22828,
      "label": "portosinusoidal vascular disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0022393",
          "MEDGEN:1807080",
          "Orphanet:596937",
          "UMLS:C5691366"
        ],
        "synonyms": [
          "PSVD"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ]
      },
      "child_count": 1,
      "reference_id": "MONDO:0035357"
    },
    {
      "id": 26283,
      "label": "Fontan-associated liver disease",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4495
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:1713226",
          "Orphanet:699068",
          "UMLS:C5396814"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "Chronic disease that occur as a complication of the Fontan procedure, a palliative surgery for patients with congenital heart disease that results in a single-ventricle circulation."
      },
      "child_count": 0,
      "reference_id": "MONDO:0979326"
    }
  ],
  "roots": [
    {
      "id": 6878,
      "label": "liver disorder"
    },
    {
      "id": 7065,
      "label": "vascular disorder"
    }
  ]
}