{
  "id": 4724,
  "label": "conventional fibrosarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002677",
  "properties": {
    "xrefs": [
      "DOID:3517",
      "GARD:0023210",
      "MEDGEN:232393",
      "NCIT:C9429",
      "UMLS:C1333156"
    ],
    "synonyms": [
      "classic fibrosarcoma",
      "classical fibrosarcoma",
      "conventional fibrosarcoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "A malignant mesenchymal neoplasm composed of fibroblasts, and characterized by collagen production and usually a herringbone architectural pattern."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 6886,
      "label": "fibrosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7762,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3355",
          "EFO:0002087",
          "GARD:0002327",
          "HP:0100244",
          "ICD9:171.9",
          "ICDO:8810/3",
          "MEDGEN:5178",
          "MESH:D005354",
          "MedDRA:10016632",
          "NANDO:2200060",
          "NCIT:C3043",
          "ONCOTREE:FIBS",
          "Orphanet:2030",
          "SCTID:443250000",
          "UMLS:C0016057"
        ],
        "synonyms": [
          "fibrocytic tumor",
          "fibrocytic tumour",
          "fibrosarcoma",
          "fibrosarcoma (disease)",
          "fibrosarcoma (excluding infantile fibrosarcoma)",
          "fibrosarcoma - not infantile",
          "fibrosarcoma, malignant",
          "malignant fibromatous neoplasm"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A malignant mesenchymal fibroblastic neoplasm affecting the soft tissue and bone."
      },
      "child_count": 22,
      "reference_id": "MONDO:0005164"
    }
  ],
  "children": [
    {
      "id": 4723,
      "label": "adult fibrosarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4724
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3516",
          "GARD:0023209",
          "MEDGEN:75840",
          "NANDO:2200060",
          "NCIT:C7809",
          "UMLS:C0278595"
        ],
        "synonyms": [
          "fibrosarcoma",
          "adult fibrosarcoma",
          "adult fibrosarcoma (disease)",
          "fibrosarcoma (disease) of adults"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A malignant mesenchymal neoplasm composed of fibroblasts. It is characterized by collagen production and a herringbone architectural pattern. It is more commonly seen in middle-aged and older adults. It usually affects the deep soft tissues of extremities, trunk, head and neck. Adult fibrosarcomas may recur and metastasize to the lungs and bones."
      },
      "child_count": 0,
      "reference_id": "MONDO:0002676"
    },
    {
      "id": 6355,
      "label": "congenital fibrosarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4724,
        4725
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8418",
          "GARD:0024067",
          "ICD9:171.9",
          "ICDO:8814/3",
          "MEDGEN:87246",
          "NCIT:C4244",
          "ONCOTREE:IFS",
          "SCTID:403996004",
          "UMLS:C0334459"
        ],
        "synonyms": [
          "congenital fibrosarcoma",
          "infantile fibrosarcoma",
          "infantile fibrosarcoma (congenital fibrosarcoma)",
          "infantile fibrosarcoma (morphologic abnormality)",
          "IFS"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004557"
    }
  ],
  "roots": [
    {
      "id": 6886,
      "label": "fibrosarcoma"
    }
  ]
}