{
  "id": 4725,
  "label": "pediatric fibrosarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0002678",
  "properties": {
    "xrefs": [
      "DOID:3520",
      "GARD:0023211",
      "MEDGEN:124685",
      "NANDO:2200060",
      "NCIT:C8088",
      "UMLS:C0279981"
    ],
    "synonyms": [
      "fibrosarcoma",
      "childhood fibrosarcoma",
      "pediatric fibrosarcoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "A malignant neoplasm arising from the deep soft tissues in children. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 6886,
      "label": "fibrosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7762,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3355",
          "EFO:0002087",
          "GARD:0002327",
          "HP:0100244",
          "ICD9:171.9",
          "ICDO:8810/3",
          "MEDGEN:5178",
          "MESH:D005354",
          "MedDRA:10016632",
          "NANDO:2200060",
          "NCIT:C3043",
          "ONCOTREE:FIBS",
          "Orphanet:2030",
          "SCTID:443250000",
          "UMLS:C0016057"
        ],
        "synonyms": [
          "fibrocytic tumor",
          "fibrocytic tumour",
          "fibrosarcoma",
          "fibrosarcoma (disease)",
          "fibrosarcoma (excluding infantile fibrosarcoma)",
          "fibrosarcoma - not infantile",
          "fibrosarcoma, malignant",
          "malignant fibromatous neoplasm"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A malignant mesenchymal fibroblastic neoplasm affecting the soft tissue and bone."
      },
      "child_count": 22,
      "reference_id": "MONDO:0005164"
    },
    {
      "id": 8005,
      "label": "childhood malignant neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6733,
        20320
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:1000654",
          "MEDGEN:82962",
          "NCIT:C4005",
          "UMLS:C0278704"
        ],
        "synonyms": [
          "childhood cancer",
          "childhood malignant neoplasm",
          "childhood neoplasm, malignant",
          "malignant childhood neoplasm",
          "malignant childhood tumor",
          "malignant childhood tumour",
          "malignant paediatric neoplasm",
          "malignant paediatric tumour",
          "malignant pediatric neoplasm",
          "malignant pediatric tumor",
          "paediatric cancer",
          "pediatric cancer",
          "malignant neoplasm"
        ],
        "definition": "A malignant tumor that occurs in children. Representative examples include soft tissue and bone sarcomas (e.g. osteosarcoma) and embryonal neoplasms (e.g. hepatoblastoma and rhabdoid tumor)."
      },
      "child_count": 60,
      "reference_id": "MONDO:0006517"
    }
  ],
  "children": [
    {
      "id": 6355,
      "label": "congenital fibrosarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4724,
        4725
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8418",
          "GARD:0024067",
          "ICD9:171.9",
          "ICDO:8814/3",
          "MEDGEN:87246",
          "NCIT:C4244",
          "ONCOTREE:IFS",
          "SCTID:403996004",
          "UMLS:C0334459"
        ],
        "synonyms": [
          "congenital fibrosarcoma",
          "infantile fibrosarcoma",
          "infantile fibrosarcoma (congenital fibrosarcoma)",
          "infantile fibrosarcoma (morphologic abnormality)",
          "IFS"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004557"
    }
  ],
  "roots": [
    {
      "id": 6886,
      "label": "fibrosarcoma"
    },
    {
      "id": 8005,
      "label": "childhood malignant neoplasm"
    }
  ]
}