{
  "id": 5025,
  "label": "superior vena cava angiosarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0003032",
  "properties": {
    "xrefs": [
      "DOID:4522",
      "GARD:0023338",
      "MEDGEN:234373",
      "NCIT:C5378",
      "UMLS:C1336530"
    ],
    "synonyms": [
      "angiosarcoma (disease) of anterior vena cava",
      "angiosarcoma of Superior vena cava",
      "angiosarcoma of the Superior vena cava",
      "anterior vena cava angiosarcoma (disease)"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "A malignant vascular neoplasm arising from the superior vena cava."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 6420,
      "label": "vein disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7065
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:866",
          "ICD9:453",
          "MEDGEN:115992",
          "NCIT:C35279",
          "SCTID:90507008",
          "UMLS:C0235522"
        ],
        "synonyms": [
          "disease of vein",
          "disease or disorder of vein",
          "disorder of vein",
          "vein disease",
          "vein disease or disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A disease involving the vein."
      },
      "child_count": 13,
      "reference_id": "MONDO:0004634"
    },
    {
      "id": 17394,
      "label": "angiosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4233,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0001816",
          "EFO:0003968",
          "GARD:0020900",
          "HP:0200058",
          "ICD9:171.9",
          "ICDO:9120/3",
          "MEDGEN:42385",
          "MESH:D006394",
          "MedDRA:10002476",
          "NCIT:C3088",
          "ONCOTREE:ANGS",
          "Orphanet:263413",
          "SCTID:403977003",
          "UMLS:C0018923"
        ],
        "synonyms": [
          "angiosarcoma",
          "angiosarcoma (disease)",
          "blood vessel sarcoma",
          "hemangiosarcoma",
          "hemangiosarcoma, malignant",
          "malignant angioendothelioma",
          "malignant hemangioendothelioma",
          "sarcoma of blood vessel",
          "vascular sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A malignant tumor arising from the endothelial cells of the blood vessels. Microscopically, it is characterized by frequently open vascular anastomosing and branching channels. The malignant cells that line the vascular channels are spindle or epithelioid and often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin and breast. Patients with long-standing lymphedema are at increased risk of developing angiosarcoma."
      },
      "child_count": 38,
      "reference_id": "MONDO:0016982"
    },
    {
      "id": 23003,
      "label": "great vessel cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4233
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:777096",
          "NCIT:C4575",
          "UMLS:C3665405"
        ],
        "synonyms": [
          "cancer of great vessel of heart",
          "great vessel cancer",
          "great vessel of heart cancer",
          "malignant great vessel neoplasm",
          "malignant great vessel of heart neoplasm",
          "malignant great vessel tumor",
          "malignant great vessel tumour",
          "malignant neoplasm of great vessel of heart"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A malignant neoplasm arising from the great vessels."
      },
      "child_count": 5,
      "reference_id": "MONDO:0040676"
    }
  ],
  "children": [
    {
      "id": 6030,
      "label": "superior vena cava leiomyosarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        5025,
        6788
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:7390",
          "GARD:0023877",
          "MEDGEN:236963",
          "NCIT:C6745",
          "UMLS:C1336531"
        ],
        "synonyms": [
          "anterior vena cava leiomyosarcoma",
          "leiomyosarcoma of Superior vena cava",
          "leiomyosarcoma of anterior vena cava",
          "leiomyosarcoma of the Superior vena cava"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "An aggressive malignant smooth muscle neoplasm, arising from the superior vena cava. It is characterized by a proliferation of neoplastic spindle cells."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004208"
    }
  ],
  "roots": [
    {
      "id": 6420,
      "label": "vein disorder"
    },
    {
      "id": 17394,
      "label": "angiosarcoma"
    },
    {
      "id": 23003,
      "label": "great vessel cancer"
    }
  ]
}