{
  "id": 5332,
  "label": "childhood endodermal sinus tumor",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0003400",
  "properties": {
    "xrefs": [
      "DOID:5342",
      "GARD:0023500",
      "MEDGEN:234139",
      "NCIT:C27364",
      "UMLS:C1333016"
    ],
    "synonyms": [
      "childhood endodermal sinus neoplasm",
      "childhood endodermal sinus tumor",
      "pediatric yolk Sac tumor",
      "childhood yolk Sac neoplasm",
      "childhood yolk Sac tumor",
      "childhood yolk Sac tumour",
      "paediatric endodermal sinus neoplasm",
      "paediatric yolk Sac neoplasm",
      "pediatric endodermal sinus neoplasm",
      "pediatric yolk Sac neoplasm"
    ],
    "definition": "A yolk sac tumor that occurs during childhood."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 6283,
      "label": "malignant childhood germ cell neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5631,
        7832,
        8005
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8149",
          "GARD:0024027",
          "MEDGEN:233150",
          "NCIT:C6541",
          "UMLS:C1334574"
        ],
        "synonyms": [
          "malignant childhood germ cell neoplasm",
          "malignant paediatric germ cell tumour",
          "malignant pediatric germ cell tumor",
          "malignant childhood germ cell tumor",
          "malignant childhood germ cell tumour",
          "malignant paediatric germ cell neoplasm",
          "malignant pediatric germ cell neoplasm"
        ],
        "definition": "A malignant germ cell tumor that occurs during childhood."
      },
      "child_count": 36,
      "reference_id": "MONDO:0004479"
    },
    {
      "id": 7365,
      "label": "yolk sac tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5475
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1911",
          "EFO:0007252",
          "GARD:0000348",
          "ICDO:9071/3",
          "MEDGEN:41782",
          "MedDRA:10048251",
          "NANDO:2200069",
          "NCIT:C3011",
          "ONCOTREE:BYST",
          "Orphanet:876",
          "SCTID:404081005",
          "UMLS:C0014145"
        ],
        "synonyms": [
          "endodermal sinus neoplasm",
          "endodermal sinus tumor",
          "hepatoid yolk sac tumor",
          "yolk SAC tumor, malignant",
          "yolk Sac neoplasm",
          "yolk Sac tumor",
          "yolk Sac tumor site unspecified",
          "yolk Sac tumour site unspecified",
          "yolk sac tumor",
          "infantile embryonal carcinoma"
        ],
        "definition": "A non-seminomatous malignant germ cell tumor composed of primitive germ cells. It is the most common malignant germ cell tumor in the pediatric population. It occurs in the infant testis, ovary, sacrococcygeal region, vagina, uterus, prostate, abdomen, liver, retroperitoneum, thorax, and pineal/third ventricle. The tumor mimics the yolk sac of the embryo and produces alpha-fetoprotein (AFP). Treatment includes: surgical resection, radiation, and chemotherapy. This tumor is very responsive to chemotherapy regimens that include cisplatinum."
      },
      "child_count": 7,
      "reference_id": "MONDO:0005744"
    }
  ],
  "children": [
    {
      "id": 5333,
      "label": "central nervous system endodermal sinus tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4753,
        5332,
        5630,
        17189,
        20012
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5343",
          "GARD:0023501",
          "MEDGEN:234604",
          "NCIT:C6209",
          "UMLS:C1377613"
        ],
        "synonyms": [
          "central nervous system yolk Sac tumor",
          "central nervous system yolk Sac tumour",
          "central nervous system yolk sac tumor",
          "central nervous system yolk sac tumour",
          "childhood central nervous system yolk Sac neoplasm",
          "childhood central nervous system yolk Sac tumor",
          "childhood central nervous system yolk Sac tumour",
          "paediatric central nervous system yolk Sac neoplasm",
          "paediatric central nervous system yolk Sac tumour",
          "pediatric central nervous system yolk Sac neoplasm",
          "pediatric central nervous system yolk Sac tumor",
          "yolk Sac tumor of the CNS",
          "yolk Sac tumour of the CNS",
          "central nervous system endodermal sinus tumor",
          "childhood central nervous system endodermal sinus neoplasm",
          "childhood central nervous system endodermal sinus tumor",
          "childhood central nervous system endodermal sinus tumour",
          "paediatric central nervous system endodermal sinus neoplasm",
          "pediatric central nervous system endodermal sinus neoplasm"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A yolk sac tumor that arises from the central nervous system and occurs during childhood."
      },
      "child_count": 5,
      "reference_id": "MONDO:0003401"
    },
    {
      "id": 5639,
      "label": "childhood ovarian yolk sac tumor",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        5332,
        5640,
        7870,
        20015
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:6083",
          "GARD:0023654",
          "MEDGEN:234136",
          "NANDO:2200069",
          "NCIT:C6551",
          "UMLS:C1332993"
        ],
        "synonyms": [
          "childhood ovarian endodermal sinus neoplasm",
          "childhood ovarian yolk sac tumor",
          "ovary childhood endodermal sinus tumor",
          "ovary childhood endodermal sinus tumour",
          "pediatric ovarian yolk Sac tumor",
          "childhood ovarian endodermal sinus tumor",
          "childhood ovarian endodermal sinus tumour",
          "childhood ovarian yolk Sac neoplasm",
          "paediatric ovarian endodermal sinus neoplasm",
          "paediatric ovarian endodermal sinus tumour",
          "paediatric ovarian yolk Sac neoplasm",
          "pediatric ovarian endodermal sinus neoplasm",
          "pediatric ovarian endodermal sinus tumor",
          "pediatric ovarian yolk Sac neoplasm"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A yolk sac tumor that arises from the ovary and occurs in children."
      },
      "child_count": 0,
      "reference_id": "MONDO:0003759"
    }
  ],
  "roots": [
    {
      "id": 6283,
      "label": "malignant childhood germ cell neoplasm"
    },
    {
      "id": 7365,
      "label": "yolk sac tumor"
    }
  ]
}