{
  "id": 5514,
  "label": "pancreatic vasoactive intestinal peptide producing tumor",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0003622",
  "properties": {
    "xrefs": [
      "DOID:5741",
      "GARD:0023591",
      "MEDGEN:453212",
      "NCIT:C27454",
      "UMLS:C2033037"
    ],
    "synonyms": [
      "pancreatic VIP producing NET",
      "pancreatic VIP producing neoplasm",
      "pancreatic VIP producing tumor",
      "pancreatic VIP-producing neuroendocrine tumor",
      "pancreatic VIP-producing neuroendocrine tumour",
      "pancreatic vasoactive intestinal peptide producing neoplasm",
      "pancreatic vasoactive intestinal peptide producing tumor"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "A usually malignant pancreatic neuroendocrine tumor producing vasoactive intestinal peptide (VIP). It may or may not be associated with inappropriate secretion of VIP and an associated clinical syndrome."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 19676,
      "label": "VIPoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        19671
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5574",
          "GARD:0003787",
          "ICD9:239.7",
          "ICDO:8155/1",
          "MEDGEN:41532",
          "MESH:D003969",
          "MedDRA:10047430",
          "NANDO:2200394",
          "NCIT:C26749",
          "Orphanet:97282",
          "SCTID:253005002",
          "UMLS:C0011993",
          "icd11.foundation:20634476"
        ],
        "synonyms": [
          "Diarrheogenic islet cell tumor",
          "Diarrheogenic islet cell tumour",
          "VIP producing neoplasm",
          "VIP- secreting neoplasm",
          "VIP- secreting tumor",
          "VIP- secreting tumour",
          "VIP-producing NET",
          "VIP-producing neuroendocrine tumor",
          "VIP-producing neuroendocrine tumour",
          "VIP-secreting tumor",
          "VIP-secreting tumour",
          "VIPoma",
          "Verner-Morrison syndrome",
          "malignant vasoactive intestinal peptide-secreting tumour",
          "vasoactive intestinal peptide producing neoplasm",
          "vasoactive intestinal peptide producing tumor",
          "vasoactive intestinal peptide producing tumour",
          "vasoactive intestinal peptide secreting neoplasm",
          "vasoactive intestinal peptide-secreting tumour",
          "WDHA syndrome",
          "pancreatic cholera",
          "pancreatic vipoma",
          "vasoactive intestinal peptide (VIP) tumor",
          "vasoactive intestinal peptide (VIP) tumour",
          "vasoactive intestinal peptide-producing tumor",
          "vasoactive intestinal peptide-producing tumour",
          "watery diarrhea, hypokalemia, and achlorhydria syndrome",
          "watery diarrhea-hypokalemia-achlorhydria syndrome"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "VIPoma is an extremely rare type of pancreatic neuroendocrine tumor that secretes vasoactive intestinal polypeptide (VIP) leading to the manifestations of watery diarrhea, hypokalemia and achlorhydia or hypochhlorhydia (known as WDHA syndrome)."
      },
      "child_count": 2,
      "reference_id": "MONDO:0019960"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 19676,
      "label": "VIPoma"
    }
  ]
}