{
  "id": 5546,
  "label": "pediatric lymphoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0003659",
  "properties": {
    "xrefs": [
      "DOID:5823",
      "GARD:0023606",
      "MEDGEN:232062",
      "NANDO:2100004",
      "NCIT:C5165",
      "UMLS:C1332979"
    ],
    "synonyms": [
      "lymphoma",
      "childhood lymphoma",
      "pediatric lymphoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "A Hodgkin or non-Hodgkin lymphoma that occurs during childhood."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 3,
  "parents": [
    {
      "id": 6792,
      "label": "lymphoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6881,
        16514
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0060058",
          "EFO:0000574",
          "ICD9:200.0",
          "ICD9:200.1",
          "ICD9:202.80",
          "ICDO:9590/3",
          "MEDGEN:44223",
          "MESH:D008223",
          "MedDRA:10025310",
          "NANDO:2100004",
          "NCIT:C3208",
          "ONCOTREE:MLYM",
          "Orphanet:223735",
          "SCTID:118600007",
          "UMLS:C0024299"
        ],
        "synonyms": [
          "lymphoma",
          "lymphoma (Hodgkin and non-Hodgkin)",
          "lymphoma (Hodgkin's and non-Hodgkin's)",
          "lymphoma, malignant",
          "lymphomatous",
          "malignant lymphoma",
          "MLYM"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A malignant (clonal) proliferation of B- lymphocytes or T- lymphocytes which involves the lymph nodes, bone marrow and/or extranodal sites. This category includes Non-Hodgkin lymphomas and Hodgkin lymphomas."
      },
      "child_count": 54,
      "reference_id": "MONDO:0005062"
    },
    {
      "id": 8005,
      "label": "childhood malignant neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6733,
        20320
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:1000654",
          "MEDGEN:82962",
          "NCIT:C4005",
          "UMLS:C0278704"
        ],
        "synonyms": [
          "childhood cancer",
          "childhood malignant neoplasm",
          "childhood neoplasm, malignant",
          "malignant childhood neoplasm",
          "malignant childhood tumor",
          "malignant childhood tumour",
          "malignant paediatric neoplasm",
          "malignant paediatric tumour",
          "malignant pediatric neoplasm",
          "malignant pediatric tumor",
          "paediatric cancer",
          "pediatric cancer",
          "malignant neoplasm"
        ],
        "definition": "A malignant tumor that occurs in children. Representative examples include soft tissue and bone sarcomas (e.g. osteosarcoma) and embryonal neoplasms (e.g. hepatoblastoma and rhabdoid tumor)."
      },
      "child_count": 60,
      "reference_id": "MONDO:0006517"
    }
  ],
  "children": [
    {
      "id": 3160,
      "label": "childhood acute lymphoblastic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5546,
        6169,
        6710
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080144",
          "GARD:0009240",
          "MEDGEN:44122",
          "NCIT:C3168",
          "UMLS:C0023452"
        ],
        "synonyms": [
          "acute lymphoblastic leukaemia (ALL)",
          "acute lymphoblastic leukemia (ALL)",
          "childhood ALL",
          "childhood acute lymphoblastic leukemia",
          "childhood acute lymphocytic leukaemia",
          "childhood acute lymphocytic leukemia",
          "childhood acute lymphogenous leukaemia",
          "childhood acute lymphogenous leukemia",
          "childhood acute lymphoid leukaemia",
          "childhood acute lymphoid leukemia",
          "childhood precursor lymphoblastic leukaemia",
          "childhood precursor lymphoblastic leukemia",
          "paediatric ALL",
          "paediatric acute lymphoblastic leukaemia",
          "paediatric acute lymphocytic leukaemia",
          "paediatric acute lymphocytic leukaemia (ALL)",
          "paediatric acute lymphogenous leukaemia",
          "paediatric acute lymphoid leukaemia",
          "pediatric ALL",
          "pediatric acute lymphoblastic leukemia",
          "pediatric acute lymphocytic leukemia",
          "pediatric acute lymphocytic leukemia (ALL)",
          "pediatric acute lymphogenous leukemia",
          "pediatric acute lymphoid leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "An acute lymphoblastic leukemia occurring during childhood. The majority of cases are B-acute lymphoblastic leukemias. Approximately 15% of the cases are T-acute lymphoblastic leukemias."
      },
      "child_count": 6,
      "reference_id": "MONDO:0000870"
    },
    {
      "id": 3164,
      "label": "T-cell childhood lymphoblastic lymphoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3163,
        5546,
        6212
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080148",
          "GARD:0022836",
          "MEDGEN:232068",
          "NCIT:C7210",
          "UMLS:C1332998"
        ],
        "synonyms": [
          "T lymphoblastic lymphoma",
          "childhood T lymphoblastic lymphoma",
          "childhood precursor T-lymphoblastic lymphoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A T lymphoblastic lymphoma that occurs during childhood."
      },
      "child_count": 0,
      "reference_id": "MONDO:0000874"
    },
    {
      "id": 18353,
      "label": "systemic Epstein-Barr virus-positive T-cell lymphoproliferative disease of childhood",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2906,
        3028,
        5546,
        7744,
        17660
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0070324",
          "GARD:0021562",
          "ICDO:9724/3",
          "MEDGEN:397492",
          "NCIT:C80374",
          "Orphanet:364033",
          "SCTID:721311006",
          "UMLS:C2699747"
        ],
        "synonyms": [
          "EBV-positive T-cell lymphoproliferative disorder of childhood",
          "systemic EBV+ T-cell LPD of childhood",
          "systemic EBV-positive T-cell lymphoma of childhood",
          "systemic EBV-positive T-cell lymphoproliferative disease of childhood",
          "systemic EBV-positive T-cell lymphoproliferative disorder of childhood"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A rare and very aggressive neoplastic disease emerging after a primary acute or chronic active EBV infection. It presents with persisting fever and malaise, hepatosplenomegaly with or without lymphadenopathy, liver failure, severe pancytopenia and a rapid progression towards multi-organ failure and hemophagocytic syndrome with a fatal issue. It is characterized by clonal proliferation of EBV-infected T cells with an activated cytotoxic phenotype."
      },
      "child_count": 0,
      "reference_id": "MONDO:0018223"
    }
  ],
  "roots": [
    {
      "id": 6792,
      "label": "lymphoma"
    },
    {
      "id": 8005,
      "label": "childhood malignant neoplasm"
    }
  ]
}