{
  "id": 5590,
  "label": "extrahepatic bile duct small cell adenocarcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0003708",
  "properties": {
    "xrefs": [
      "DOID:5926",
      "GARD:0023628",
      "MEDGEN:277648",
      "NCIT:C5845",
      "UMLS:C1335979"
    ],
    "synonyms": [
      "Oat cell carcinoma of extrahepatic bile duct",
      "Oat cell carcinoma of the extrahepatic bile duct",
      "Oat cell extrahepatic bile duct carcinoma",
      "extrahepatic bile duct small cell NEC",
      "extrahepatic bile duct small cell neuroendocrine carcinoma",
      "small cell adenocarcinoma of extrahepatic bile duct",
      "small cell adenocarcinoma of the extrahepatic bile duct",
      "small cell extrahepatic bile duct carcinoma",
      "small cell extrahepatic bile duct neuroendocrine carcinoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the extrahepatic bile ducts. It is characterized by the presence of malignant small cells."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 2894,
      "label": "small cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4255
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0050685",
          "EFO:0008524",
          "GARD:0022765",
          "ICDO:8041/3",
          "ICDO:8042/3",
          "MEDGEN:90748",
          "MESH:D018288",
          "NCIT:C3915",
          "NCIT:C4099",
          "SCTID:11010461000119101",
          "UMLS:C0334239"
        ],
        "synonyms": [
          "oat cell cancer",
          "oat cell carcinoma",
          "small cell NEC",
          "small cell cancer",
          "small cell car. (extrapulmonary)",
          "small cell carcinoma",
          "small cell carcinoma (extrapulmonary)",
          "small cell neuroendocrine carcinoma",
          "intermediate cell small cell carcinoma",
          "small cell carcinoma - intermediate cell",
          "small cell carcinoma, intermediate cell",
          "small cell carcinoma, intermediate cell (morphologic abnormality)"
        ],
        "categories": [
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A neuroendocrine carcinoma composed of small malignant cells which are often said to resemble \"oat cells\" under the microscope. Small cell carcinoma most often affects the lungs. Clinically, this is often a rapidly growing cancer that spreads to distant sites early."
      },
      "child_count": 18,
      "reference_id": "MONDO:0000402"
    },
    {
      "id": 4714,
      "label": "extrahepatic bile duct adenocarcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5076,
        5152
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3495",
          "GARD:0023205",
          "MEDGEN:124642",
          "NCIT:C7975",
          "UMLS:C0279659"
        ],
        "synonyms": [
          "adenocarcinoma of extrahepatic bile duct",
          "adenocarcinoma of the extrahepatic bile duct",
          "extrahepatic bile duct adenocarcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A carcinoma that arises from glandular epithelial cells of the extrahepatic bile duct"
      },
      "child_count": 14,
      "reference_id": "MONDO:0002665"
    },
    {
      "id": 16046,
      "label": "liver neuroendocrine carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4255,
        18551,
        21456
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0019760",
          "MEDGEN:474664",
          "NCIT:C96787",
          "Orphanet:100085",
          "SCTID:716652006",
          "UMLS:C3273031"
        ],
        "synonyms": [
          "HNEC",
          "PHNEC",
          "hepatic neuroendocrine carcinoma",
          "liver neuroendocrine cancer",
          "liver neuroendocrine carcinoma",
          "neuroendocrine carcinoma of liver",
          "primary hepatic neuroendocrine carcinoma",
          "primary liver neuroendocrine carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "An extremely rare, aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the liver."
      },
      "child_count": 6,
      "reference_id": "MONDO:0015072"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 2894,
      "label": "small cell carcinoma"
    },
    {
      "id": 4714,
      "label": "extrahepatic bile duct adenocarcinoma"
    },
    {
      "id": 16046,
      "label": "liver neuroendocrine carcinoma"
    }
  ]
}