{
  "id": 6065,
  "label": "proximal-type epithelioid sarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004244",
  "properties": {
    "xrefs": [
      "DOID:7492",
      "GARD:0023896",
      "MEDGEN:235511",
      "NCIT:C27472",
      "ONCOTREE:PTES",
      "UMLS:C1335563"
    ],
    "synonyms": [
      "central epithelioid sarcoma",
      "proximal-type epithelioid sarcoma",
      "PTES"
    ],
    "definition": "An epithelioid sarcoma predominantly involving the pelvis, perineum, and genital organs. It tends to have a more aggressive clinical course as compared to the more frequently seen distal-type epithelioid sarcoma."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 17696,
      "label": "epithelioid sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:6193",
          "GARD:0010181",
          "ICDO:8804/3",
          "MEDGEN:104753",
          "MedDRA:10015099",
          "NCIT:C3714",
          "ONCOTREE:EPIS",
          "Orphanet:293202",
          "UMLS:C0205944"
        ],
        "synonyms": [
          "ES",
          "epithelioid cell sarcoma",
          "epithelioid sarcoma"
        ],
        "definition": "An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma)."
      },
      "child_count": 4,
      "reference_id": "MONDO:0017387"
    }
  ],
  "children": [
    {
      "id": 6064,
      "label": "vulvar proximal-type epithelioid sarcoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        6065,
        6930
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:7491",
          "GARD:0023895",
          "MEDGEN:276995",
          "NCIT:C40319",
          "UMLS:C1520093"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          }
        ],
        "definition": "An epithelioid sarcoma of the proximal type involving the vulva."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004243"
    }
  ],
  "roots": [
    {
      "id": 17696,
      "label": "epithelioid sarcoma"
    }
  ]
}