{
  "id": 6219,
  "label": "sarcomatoid penile squamous cell carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004410",
  "properties": {
    "xrefs": [
      "DOID:7958",
      "GARD:0023988",
      "MEDGEN:235580",
      "NCIT:C6984",
      "UMLS:C1335923"
    ],
    "synonyms": [
      "sarcomatoid carcinoma of the penis",
      "sarcomatoid penile carcinoma",
      "sarcomatoid penile squamous cell carcinoma",
      "sarcomatous carcinoma of the penis",
      "spindle cell carcinoma of the penis",
      "squamous cell carcinoma of penis, sarcomatoid type",
      "squamous cell carcinoma of the penis, sarcomatoid type"
    ],
    "categories": [
      {
        "ref": "MONDO:0005039",
        "name": "reproductive system disorder"
      }
    ],
    "definition": "A squamous cell carcinoma that arises from the penis and is characterized by the presence of malignant spindle-shaped cells."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 18435,
      "label": "squamous cell carcinoma of penis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6823,
        7886
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5518",
          "GARD:0021639",
          "MEDGEN:116057",
          "NCIT:C7729",
          "ONCOTREE:PSCC",
          "Orphanet:398058",
          "SCTID:403468003",
          "UMLS:C0238348",
          "icd11.foundation:186592209"
        ],
        "synonyms": [
          "epidermoid carcinoma of penis",
          "epidermoid carcinoma of the penis",
          "epidermoid cell carcinoma of penis",
          "epidermoid cell carcinoma of the penis",
          "penile epidermoid carcinoma",
          "penile epidermoid cell carcinoma",
          "penile squamous car.(epidermoid)",
          "penile squamous carcinoma (epidermoid)",
          "penile squamous cell cancer",
          "penile squamous cell carcinoma",
          "penis squamous cell carcinoma",
          "squamous cell carcinoma of penis",
          "squamous cell carcinoma of the penis",
          "PSCC"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          }
        ],
        "definition": "A squamous cell carcinoma arising from the penis. It occurs chiefly in the squamous epithelium of the glans, coronal sulcus, and foreskin. Etiologic factors include phimosis, lichen sclerosus, smoking, ultraviolet irradiation, history of warts or condylomas, and lack of circumcision. Human papilloma virus is present in a subset of penile squamous cell carcinomas. Patients may present with an exophytic or flat ulcerative mass in the glans or a large primary tumor with inguinal nodal and skin metastases. Morphologic variants include the basaloid carcinoma, warty (condylomatous) carcinoma, verrucous carcinoma, and sarcomatoid (spindle cell) carcinoma. (WHO, 2004)"
      },
      "child_count": 10,
      "reference_id": "MONDO:0018352"
    },
    {
      "id": 20715,
      "label": "sarcomatoid squamous cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6823,
        7925
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "ICD9:199.1",
          "ICDO:8074/3",
          "NCIT:C27084",
          "SCTID:403900000"
        ],
        "synonyms": [
          "epidermoid spindle cell carcinoma",
          "sarcomatoid squamous cell carcinoma",
          "spindle cell (sarcomatoid) squamous cell carcinoma",
          "squamous cell carcinoma, sarcomatoid",
          "squamous cell carcinoma, spindle cell",
          "squamous cell spindle cell carcinoma"
        ],
        "definition": "A poorly differentiated squamous cell carcinoma characterized by the presence of malignant cells with spindle cell features."
      },
      "child_count": 4,
      "reference_id": "MONDO:0021663"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 18435,
      "label": "squamous cell carcinoma of penis"
    },
    {
      "id": 20715,
      "label": "sarcomatoid squamous cell carcinoma"
    }
  ]
}