{
  "id": 6339,
  "label": "epithelioid malignant peripheral nerve sheath tumor",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004540",
  "properties": {
    "xrefs": [
      "DOID:8353",
      "GARD:0024055",
      "MEDGEN:272104",
      "NCIT:C6561",
      "SCTID:404038007",
      "UMLS:C1321427"
    ],
    "synonyms": [
      "epithelioid MPNST",
      "epithelioid malignant peripheral nerve sheath tumor",
      "malignant epithelioid neoplasm of peripheral nerve sheath",
      "malignant epithelioid neoplasm of the peripheral nerve sheath",
      "malignant epithelioid peripheral nerve sheath neoplasm",
      "malignant epithelioid peripheral nerve sheath tumor",
      "malignant epithelioid peripheral nerve sheath tumour",
      "malignant epithelioid tumor of peripheral nerve sheath",
      "malignant epithelioid tumor of the peripheral nerve sheath",
      "malignant epithelioid tumour of peripheral nerve sheath",
      "malignant epithelioid tumour of the peripheral nerve sheath"
    ],
    "categories": [
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "A rare variant of malignant peripheral nerve sheath tumor composed predominantly or exclusively of epithelioid cells."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 18046,
      "label": "malignant peripheral nerve sheath tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4336,
        4613,
        17197,
        20329,
        24071
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5940",
          "EFO:0000760",
          "GARD:0010872",
          "ICD9:171.9",
          "ICDO:9540/3",
          "ICDO:9560/3",
          "MEDGEN:155614",
          "MedDRA:10029236",
          "NANDO:2200102",
          "NCIT:C3798",
          "ONCOTREE:MPNST",
          "Orphanet:3148",
          "SCTID:404037002",
          "UMLS:C0751690",
          "icd11.foundation:71413945"
        ],
        "synonyms": [
          "neurofibrosarcoma",
          "MPNST",
          "Malig. periph. nerve sheath tum.",
          "malignant neoplasm of peripheral nerve sheath",
          "malignant neurilemmoma",
          "malignant neurilemoma",
          "malignant neurofibroma",
          "malignant peripheral nerve sheath neoplasm",
          "malignant peripheral nerve sheath tumor",
          "malignant peripheral nerve sheath tumor (morphologic abnormality)",
          "malignant peripheral nerve sheath tumor [dup] (morphologic abnormality)",
          "malignant peripheral nerve sheath tumour (morphologic abnormality)",
          "malignant peripheral nerve sheath tumour [dup] (morphologic abnormality)",
          "malignant schwannoma",
          "malignant tumor of peripheral nerve sheath",
          "malignant tumor of the peripheral nerve sheath",
          "malignant tumour of peripheral nerve sheath",
          "malignant tumour of the peripheral nerve sheath",
          "neurofibrosarcoma, malignant",
          "neurogenic sarcoma",
          "schwannoma, malignant"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma occurring in a wide range of anatomical sites."
      },
      "child_count": 35,
      "reference_id": "MONDO:0017827"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 18046,
      "label": "malignant peripheral nerve sheath tumor"
    }
  ]
}