{
  "id": 6355,
  "label": "congenital fibrosarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004557",
  "properties": {
    "xrefs": [
      "DOID:8418",
      "GARD:0024067",
      "ICD9:171.9",
      "ICDO:8814/3",
      "MEDGEN:87246",
      "NCIT:C4244",
      "ONCOTREE:IFS",
      "SCTID:403996004",
      "UMLS:C0334459"
    ],
    "synonyms": [
      "congenital fibrosarcoma",
      "infantile fibrosarcoma",
      "infantile fibrosarcoma (congenital fibrosarcoma)",
      "infantile fibrosarcoma (morphologic abnormality)",
      "IFS"
    ],
    "categories": [
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4724,
      "label": "conventional fibrosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6886
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3517",
          "GARD:0023210",
          "MEDGEN:232393",
          "NCIT:C9429",
          "UMLS:C1333156"
        ],
        "synonyms": [
          "classic fibrosarcoma",
          "classical fibrosarcoma",
          "conventional fibrosarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A malignant mesenchymal neoplasm composed of fibroblasts, and characterized by collagen production and usually a herringbone architectural pattern."
      },
      "child_count": 2,
      "reference_id": "MONDO:0002677"
    },
    {
      "id": 4725,
      "label": "pediatric fibrosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6886,
        8005
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3520",
          "GARD:0023211",
          "MEDGEN:124685",
          "NANDO:2200060",
          "NCIT:C8088",
          "UMLS:C0279981"
        ],
        "synonyms": [
          "fibrosarcoma",
          "childhood fibrosarcoma",
          "pediatric fibrosarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "A malignant neoplasm arising from the deep soft tissues in children. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern."
      },
      "child_count": 2,
      "reference_id": "MONDO:0002678"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4724,
      "label": "conventional fibrosarcoma"
    },
    {
      "id": 4725,
      "label": "pediatric fibrosarcoma"
    }
  ]
}