{
  "id": 6706,
  "label": "T-cell acute lymphoblastic leukemia",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004963",
  "properties": {
    "xrefs": [
      "CSP:2004-1600",
      "CSP:2004-1803",
      "DOID:5603",
      "EFO:0000209",
      "GARD:0024138",
      "HGNC:5056",
      "ICDO:9837/3",
      "MEDGEN:368378",
      "NANDO:2200003",
      "NCIT:C3183",
      "SCTID:277575008",
      "UMLS:C1961099"
    ],
    "synonyms": [
      "acute T cell leukaemia",
      "T acute lymphoblastic leukaemia",
      "T acute lymphoblastic leukemia",
      "T-ALL",
      "T-cell ALL",
      "T-cell acute lymphoblastic leukaemia",
      "T-cell acute lymphoblastic leukemia",
      "T-cell acute lymphocytic leukemia",
      "T-cell type acute leukaemia",
      "T-cell type acute leukemia",
      "acute T cell leukemia",
      "acute T cell lymphoblastic leukaemia",
      "acute T cell lymphoblastic leukemia",
      "acute T cell lymphocytic leukaemia",
      "acute T cell lymphocytic leukemia",
      "acute T-cell leukaemia",
      "acute T-cell leukemia",
      "acute T-cell lymphoblastic leukaemia",
      "acute T-cell lymphoblastic leukemia",
      "acute T-cell lymphocytic leukaemia",
      "acute T-cell lymphocytic leukemia",
      "precursor T lymphoblastic leukaemia",
      "precursor T-lymphoblastic leukaemia",
      "precursor T-lymphoblastic leukaemia (T-cell ALL)",
      "precursor T-lymphoblastic leukemia",
      "precursor T-lymphoblastic leukemia (T-cell ALL)"
    ],
    "categories": [
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      },
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "Acute lymphoblastic leukemia of T-cell origin. It comprises about 15% of childhood cases and 25% of adult cases. It is more common in males than females. (WHO, 2001)"
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 4,
  "parents": [
    {
      "id": 6710,
      "label": "acute lymphoblastic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5444,
        6890,
        7079,
        11789,
        18836
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:9952",
          "EFO:0000220",
          "GARD:0000522",
          "HP:0006721",
          "ICD10CM:C91.0",
          "ICD9:204",
          "ICD9:204.0",
          "ICD9:204.00",
          "ICD9:204.9",
          "ICDO:9835/3",
          "MEDGEN:7317",
          "NCIT:C3167",
          "Orphanet:513",
          "SCTID:91857003",
          "UMLS:C0023449"
        ],
        "synonyms": [
          "lymphoblastic leukaemia",
          "lymphoblastic leukemia",
          "ALL",
          "ALL - acute lymphocytic leukaemia",
          "ALL - acute lymphocytic leukemia",
          "acute lymphoblastic leukaemia (ALL)",
          "acute lymphoblastic leukaemia (disease)",
          "acute lymphoblastic leukemia",
          "acute lymphoblastic leukemia (ALL)",
          "acute lymphoblastic leukemia (disease)",
          "acute lymphoblastic leukemia/lymphoma",
          "acute lymphocytic leukaemia",
          "acute lymphocytic leukemia",
          "acute lymphocytic leukemias",
          "acute lymphogenous leukaemia",
          "acute lymphogenous leukemia",
          "acute lymphoid leukaemia",
          "acute lymphoid leukemia",
          "leukemia, lymphoblastic, malignant",
          "lymphoblastic leukemia, acute",
          "precursor Lymphoblasic leukaemia",
          "precursor Lymphoblasic leukemia",
          "precursor cell lymphoblastic leukaemia",
          "precursor cell lymphoblastic leukemia",
          "precursor lymphoblastic leukaemia",
          "precursor lymphoblastic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "Leukemia with an acute onset, characterized by the presence of lymphoblasts in the bone marrow and the peripheral blood. It includes the acute B lymphoblastic leukemia and acute T lymphoblastic leukemia."
      },
      "child_count": 60,
      "reference_id": "MONDO:0004967"
    },
    {
      "id": 7179,
      "label": "T-cell leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6569,
        7079
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:715",
          "EFO:0005592",
          "GARD:0024203",
          "MEDGEN:6064",
          "MESH:D015458",
          "UMLS:C0023492"
        ],
        "synonyms": [
          "T cell leukaemia (disease)",
          "T cell leukemia (disease)",
          "leukaemia (disease) of T cell",
          "leukemia (disease) of T cell"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A malignant disease of the T-lymphocytes in the bone marrow, thymus, and/or blood."
      },
      "child_count": 6,
      "reference_id": "MONDO:0005525"
    }
  ],
  "children": [
    {
      "id": 3161,
      "label": "T-cell childhood acute lymphocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3028,
        3160,
        6212,
        6706
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080145",
          "EFO:1001947",
          "GARD:0007346",
          "MEDGEN:75996",
          "NCIT:C7953",
          "UMLS:C0279583"
        ],
        "synonyms": [
          "T acute lymphoblastic leukaemia",
          "T acute lymphoblastic leukemia",
          "T-cell childhood ALL",
          "T-cell childhood acute lymphoblastic leukaemia",
          "T-cell childhood acute lymphoblastic leukemia",
          "T-cell childhood acute lymphocytic leukemia",
          "T-cell paediatric ALL",
          "T-cell paediatric acute lymphoblastic leukaemia",
          "T-cell paediatric acute lymphocytic leukaemia",
          "T-cell pediatric ALL",
          "T-cell pediatric acute lymphoblastic leukemia",
          "T-cell pediatric acute lymphocytic leukemia",
          "childhood T acute lymphoblastic leukaemia",
          "childhood T acute lymphoblastic leukemia",
          "childhood T-ALL",
          "childhood T-cell acute lymphoblastic leukaemia",
          "childhood T-cell acute lymphoblastic leukemia",
          "childhood precursor T-lymphoblastic leukaemia",
          "childhood precursor T-lymphoblastic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "An acute lymphoblastic leukemia of T-cell origin occurring in children."
      },
      "child_count": 0,
      "reference_id": "MONDO:0000871"
    },
    {
      "id": 19293,
      "label": "T-cell prolymphocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2906,
        3282,
        5443,
        6706
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0081042",
          "EFO:1000560",
          "GARD:0013731",
          "ICDO:9834/3",
          "MEDGEN:391707",
          "MESH:D015461",
          "MedDRA:10042985",
          "NCIT:C4752",
          "ONCOTREE:TPLL",
          "Orphanet:86871",
          "SCTID:277545003",
          "SCTID:277567002",
          "UMLS:C2363142",
          "icd11.foundation:352523899"
        ],
        "synonyms": [
          "CLL, T-cell",
          "T cell CLL",
          "T cell chronic lymphocytic leukaemia",
          "T cell chronic lymphocytic leukemia",
          "T cell prolymphocytic leukaemia",
          "T cell prolymphocytic leukemia",
          "T prolymphocytic leukaemia",
          "T prolymphocytic leukemia",
          "T-PLL",
          "T-cell CLL",
          "T-cell chronic lymphocytic leukaemia",
          "T-cell chronic lymphocytic leukemia",
          "T-cell prolymphocytic leukemia",
          "chronic T-cell leukaemia",
          "chronic T-cell leukemia",
          "chronic T-cell lymphocytic leukaemia",
          "chronic T-cell lymphocytic leukemia",
          "TPLL",
          "leukemia, T-cell, chronic"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A slow-growing type of leukemia (blood cancer) in which too many lymphocytes are found in the bone marrow and/or blood. The T-cell is specified as the defective cell line."
      },
      "child_count": 0,
      "reference_id": "MONDO:0019468"
    },
    {
      "id": 19295,
      "label": "aggressive NK-cell leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        2906,
        3274,
        5443,
        6706
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1035",
          "GARD:0010493",
          "ICDO:9948/3",
          "MEDGEN:266235",
          "MedDRA:10028811",
          "NANDO:2200012",
          "NCIT:C8647",
          "ONCOTREE:ANKL",
          "Orphanet:86873",
          "SCTID:721310007",
          "UMLS:C1292777",
          "icd11.foundation:153957345"
        ],
        "synonyms": [
          "ANKCL",
          "NK cell leukaemia",
          "NK cell leukemia",
          "NK-cell LGL leukaemia",
          "NK-cell LGL leukemia",
          "NK-cell large granular lymphocyte leukaemia",
          "NK-cell large granular lymphocyte leukemia",
          "NK-cell leukaemia",
          "NK-cell leukemia",
          "aggressive NK-cell leukaemia (morphologic abnormality)",
          "aggressive NK-cell leukemia",
          "aggressive NK-cell leukemia (morphologic abnormality)",
          "aggressive NK-cell leukemia/lymphoma",
          "aggressive NK-cell lymphoma",
          "leukaemia (disease) of natural killer cell",
          "leukemia (disease) of natural killer cell",
          "natural Killer cell leukemia",
          "natural killer cell leukaemia (disease)",
          "natural killer cell leukemia",
          "natural killer cell leukemia (disease)",
          "ANKL",
          "aggressive NK cell leukaemia",
          "aggressive NK cell leukemia",
          "aggressive natural killer cell leukaemia",
          "aggressive natural killer cell leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A rare, highly aggressive, Epstein-Barr virus-associated leukemia, also known as aggressive NK-cell leukemia/lymphoma; it may represent the leukemic counterpart of nasal type extranodal NK/T-cell lymphomas. It affects primarily teenagers and young adults. It is characterized by the systemic proliferation of NK cells in the peripheral blood, bone marrow, liver, and spleen."
      },
      "child_count": 0,
      "reference_id": "MONDO:0019470"
    },
    {
      "id": 24028,
      "label": "early T cell progenitor acute lymphoblastic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        6706
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0026127",
          "MEDGEN:1385175",
          "NCIT:C130043",
          "UMLS:C4329780"
        ],
        "synonyms": [
          "ETP ALL",
          "ETP-ALL",
          "early T acute lymphoblastic leukaemia",
          "early T acute lymphoblastic leukemia",
          "early T-cell precursor acute lymphoblastic leukaemia",
          "early T-cell precursor acute lymphoblastic leukemia",
          "early T-cell precursor lymphoblastic leukaemia",
          "early T-cell precursor lymphoblastic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "T acute lymphoblastic leukemia in which the blasts have unique immunophenotypic and genetic characteristics suggesting only limited early T-cell differentiation."
      },
      "child_count": 0,
      "reference_id": "MONDO:0100291"
    }
  ],
  "roots": [
    {
      "id": 6710,
      "label": "acute lymphoblastic leukemia"
    },
    {
      "id": 7179,
      "label": "T-cell leukemia"
    }
  ]
}