{
  "id": 6708,
  "label": "acinar cell carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0004965",
  "properties": {
    "xrefs": [
      "DOID:3025",
      "EFO:0000216",
      "GARD:0008568",
      "ICDO:8550/3",
      "MEDGEN:61660",
      "MESH:D018267",
      "NCIT:C3768",
      "ONCOTREE:ACCC",
      "UMLS:C0206685",
      "icd11.foundation:1322159869"
    ],
    "synonyms": [
      "acinar adenocarcinoma",
      "acinar carcinoma",
      "acinar cell adenocarcinoma",
      "acinar cell carcinoma",
      "acinar cell carcinoma (morphologic abnormality)",
      "acinic cell adenocarcinoma",
      "acinic cell carcinoma",
      "carcinoma of acinar cell",
      "carcinoma, acinar cell, malignant",
      "ACCC",
      "acinic cell tumor",
      "acinic cell tumour"
    ],
    "definition": "A carcinoma that arises from epithelial cells of the acinar cell"
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 5,
  "parents": [
    {
      "id": 6712,
      "label": "adenocarcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6734,
        21312
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "CSP:2000-0386",
          "DOID:299",
          "EFO:0000228",
          "ICDO:8140/3",
          "MEDGEN:122",
          "MESH:D000230",
          "NCIT:C2852",
          "ONCOTREE:ADNOS",
          "SCTID:443961001",
          "UMLS:C0001418"
        ],
        "synonyms": [
          "adenocarcinoma",
          "adenocarcinoma NOS (morphologic abnormality)",
          "adenocarcinoma, malignant",
          "adenocarcinoma, no subtype (morphologic abnormality)",
          "adenocarcinomas",
          "ADNOS"
        ],
        "definition": "A common cancer characterized by the presence of malignant glandular cells. Morphologically, adenocarcinomas are classified according to the growth pattern (e.g., papillary, alveolar) or according to the secreting product (e.g., mucinous, serous). Representative examples of adenocarcinoma are ductal and lobular breast carcinoma, lung adenocarcinoma, renal cell carcinoma, hepatocellular carcinoma (hepatoma), colon adenocarcinoma, and prostate adenocarcinoma."
      },
      "child_count": 128,
      "reference_id": "MONDO:0004970"
    }
  ],
  "children": [
    {
      "id": 4572,
      "label": "prostatic acinar adenocarcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6708,
        6810
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3024",
          "GARD:0027608",
          "MEDGEN:231350",
          "NCIT:C5596",
          "UMLS:C1332139"
        ],
        "synonyms": [
          "acinar adenocarcinoma of prostate",
          "acinar adenocarcinoma of the prostate",
          "acinar prostate adenocarcinoma",
          "prostate acinar adenocarcinoma",
          "prostatic acinar adenocarcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          }
        ],
        "definition": "An invasive adenocarcinoma of the prostate gland composed of secretory cells. It is the most common histologic type of prostate adenocarcinoma. Several morphologic variants exist, including atrophic, pseudohyperplastic, foamy gland, and oncocytic variants."
      },
      "child_count": 8,
      "reference_id": "MONDO:0002493"
    },
    {
      "id": 5515,
      "label": "acinic cell breast carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        6698,
        6708
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5743",
          "GARD:0027643",
          "MEDGEN:272988",
          "NCIT:C40367",
          "UMLS:C1515868"
        ],
        "synonyms": [
          "acinar cell breast carcinoma",
          "acinic cell breast carcinoma",
          "breast carcinoma of acinar cell"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0002657",
            "name": "breast disorder"
          }
        ],
        "definition": "A breast adenocarcinoma characterized by the presence of serous (acinic cell) differentiation."
      },
      "child_count": 0,
      "reference_id": "MONDO:0003624"
    },
    {
      "id": 7872,
      "label": "pancreatic acinar cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6708,
        7633
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5742",
          "EFO:1000439",
          "GARD:0021777",
          "MEDGEN:83540",
          "NCIT:C7977",
          "ONCOTREE:PAAC",
          "Orphanet:424046",
          "UMLS:C0279661",
          "icd11.foundation:449785448"
        ],
        "synonyms": [
          "Pancreatic acinar cell cancer",
          "acinar cell adenocarcinoma of pancreas",
          "acinar cell adenocarcinoma of the pancreas",
          "acinar cell carcinoma of pancreas",
          "acinar cell carcinoma of the pancreas",
          "carcinoma of pancreatic acinar cell",
          "pancreas acinar cell adenocarcinoma",
          "pancreatic acinar cell adenocarcinoma",
          "pancreatic acinar cell carcinoma",
          "PAAC"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "An adenocarcinoma arising from the pancreas. It is characterized by the presence of relatively uniform malignant cells which form acinar patterns. It usually occurs during adulthood. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It may metastasize to regional lymph nodes and the liver. A minority of patients develop lipase hypersecretion syndrome. This syndrome may be seen in patients with liver metastases and it is characterized by excessive secretion of lipase in the serum, polyarthralgia, and subcutaneous fat necrosis."
      },
      "child_count": 2,
      "reference_id": "MONDO:0006346"
    },
    {
      "id": 7881,
      "label": "parotid gland acinic cell carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        6708,
        20508
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:1000458",
          "GARD:0027749",
          "MEDGEN:277501",
          "NCIT:C5933",
          "UMLS:C1335353"
        ],
        "synonyms": [
          "parotid gland acinar cell carcinoma",
          "parotid gland acinic cell carcinoma",
          "acinic cell carcinoma of parotid",
          "acinic cell carcinoma of parotid gland",
          "acinic cell carcinoma of the parotid",
          "acinic cell carcinoma of the parotid gland",
          "parotid acinic cell carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0006858",
            "name": "mouth disorder"
          }
        ],
        "definition": "An adenocarcinoma with serous acinar cell differentiation that arises from the parotid gland. Patients usually present with a slow growing mass in the parotid area."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006355"
    },
    {
      "id": 7919,
      "label": "salivary gland acinic cell carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        6708
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:1000513",
          "GARD:0027751",
          "MEDGEN:79030",
          "NCIT:C8013",
          "UMLS:C0279738"
        ],
        "synonyms": [
          "acinic cell carcinoma of salivary gland",
          "acinic cell carcinoma of the salivary gland",
          "acinic cell neoplasm of salivary gland",
          "acinic cell neoplasm of the salivary gland",
          "acinic cell tumor of salivary gland",
          "acinic cell tumor of the salivary gland",
          "acinic cell tumour of salivary gland",
          "acinic cell tumour of the salivary gland",
          "salivary gland acinic cell cancer",
          "salivary gland acinic cell neoplasm",
          "salivary gland acinic cell tumor",
          "salivary gland acinic cell tumour"
        ],
        "definition": "A carcinoma of the salivary gland characterized by serous acinar cell differentiation. The vast majority of cases occur in the parotid gland. It usually presents as a slowly enlarging mass. A minority of patients experience pain. It may recur or metastasize. Multiple recurrences and metastasis to cervical lymph nodes are usually associated with a poor prognosis."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006400"
    }
  ],
  "roots": [
    {
      "id": 6712,
      "label": "adenocarcinoma"
    }
  ]
}