{
  "id": 7872,
  "label": "pancreatic acinar cell carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0006346",
  "properties": {
    "xrefs": [
      "DOID:5742",
      "EFO:1000439",
      "GARD:0021777",
      "MEDGEN:83540",
      "NCIT:C7977",
      "ONCOTREE:PAAC",
      "Orphanet:424046",
      "UMLS:C0279661",
      "icd11.foundation:449785448"
    ],
    "synonyms": [
      "Pancreatic acinar cell cancer",
      "acinar cell adenocarcinoma of pancreas",
      "acinar cell adenocarcinoma of the pancreas",
      "acinar cell carcinoma of pancreas",
      "acinar cell carcinoma of the pancreas",
      "carcinoma of pancreatic acinar cell",
      "pancreas acinar cell adenocarcinoma",
      "pancreatic acinar cell adenocarcinoma",
      "pancreatic acinar cell carcinoma",
      "PAAC"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "An adenocarcinoma arising from the pancreas. It is characterized by the presence of relatively uniform malignant cells which form acinar patterns. It usually occurs during adulthood. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It may metastasize to regional lymph nodes and the liver. A minority of patients develop lipase hypersecretion syndrome. This syndrome may be seen in patients with liver metastases and it is characterized by excessive secretion of lipase in the serum, polyarthralgia, and subcutaneous fat necrosis."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 6708,
      "label": "acinar cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6712
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3025",
          "EFO:0000216",
          "GARD:0008568",
          "ICDO:8550/3",
          "MEDGEN:61660",
          "MESH:D018267",
          "NCIT:C3768",
          "ONCOTREE:ACCC",
          "UMLS:C0206685",
          "icd11.foundation:1322159869"
        ],
        "synonyms": [
          "acinar adenocarcinoma",
          "acinar carcinoma",
          "acinar cell adenocarcinoma",
          "acinar cell carcinoma",
          "acinar cell carcinoma (morphologic abnormality)",
          "acinic cell adenocarcinoma",
          "acinic cell carcinoma",
          "carcinoma of acinar cell",
          "carcinoma, acinar cell, malignant",
          "ACCC",
          "acinic cell tumor",
          "acinic cell tumour"
        ],
        "definition": "A carcinoma that arises from epithelial cells of the acinar cell"
      },
      "child_count": 5,
      "reference_id": "MONDO:0004965"
    },
    {
      "id": 7633,
      "label": "pancreatic adenocarcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6712,
        6912
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:4074",
          "EFO:1000044",
          "GARD:0027736",
          "MEDGEN:83800",
          "NCIT:C8294",
          "ONCOTREE:PAAD",
          "SCTID:700423003",
          "UMLS:C0281361",
          "icd11.foundation:1663659989"
        ],
        "synonyms": [
          "adenocarcinoma - pancreas",
          "adenocarcinoma of pancreas",
          "adenocarcinoma of the pancreas",
          "pancreas adenocarcinoma",
          "pancreatic adenocarcinoma",
          "PAAD"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A carcinoma that arises from glandular epithelial cells of the pancreas"
      },
      "child_count": 10,
      "reference_id": "MONDO:0006047"
    }
  ],
  "children": [
    {
      "id": 6158,
      "label": "pancreatic acinar cell cystadenocarcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4881,
        7872
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:7729",
          "GARD:0023946",
          "ICDO:8551/3",
          "MEDGEN:224757",
          "NCIT:C5727",
          "UMLS:C1266087"
        ],
        "synonyms": [
          "acinar cell cystadenocarcinoma",
          "acinar cell cystadenocarcinoma (morphologic abnormality)",
          "acinar cell cystadenocarcinoma of pancreas",
          "acinar cell cystadenocarcinoma of the pancreas",
          "pancreatic acinar cell cystadenocarcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A cystic adenocarcinoma characterized by the presence of relatively uniform neoplastic cells which produce pancreatic enzymes and are arranged in acinar patterns. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It usually has an aggressive clinical course."
      },
      "child_count": 0,
      "reference_id": "MONDO:0004343"
    }
  ],
  "roots": [
    {
      "id": 6708,
      "label": "acinar cell carcinoma"
    },
    {
      "id": 7633,
      "label": "pancreatic adenocarcinoma"
    }
  ]
}