{
  "id": 7878,
  "label": "paranasal sinus adenoid cystic carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0006352",
  "properties": {
    "xrefs": [
      "GARD:0024379",
      "MEDGEN:233840",
      "NCIT:C6019",
      "UMLS:C1335337"
    ],
    "synonyms": [
      "accessory sinus adenoid cystic carcinoma",
      "adenoid cystic carcinoma of accessory sinus",
      "adenoid cystic carcinoma of paranasal sinus",
      "adenoid cystic carcinoma of the accessory sinus",
      "adenoid cystic carcinoma of the paranasal sinus",
      "paranasal sinus adenoid cystic carcinoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      },
      {
        "ref": "MONDO:0005087",
        "name": "respiratory system disorder"
      },
      {
        "ref": "MONDO:0024623",
        "name": "otorhinolaryngologic disease"
      }
    ],
    "definition": "A rare adenoid cystic carcinoma that arises from the paranasal sinuses. It usually has an aggressive clinical course characterized by high recurrence rates and distant metastases."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 2879,
      "label": "paranasal sinus carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4505,
        20081,
        23674
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0050619",
          "GARD:0009354",
          "MEDGEN:167751",
          "NCIT:C6014",
          "UMLS:C0854995"
        ],
        "synonyms": [
          "malignant neoplasm of paranasal sinus",
          "malignant paranasal sinus neoplasm",
          "paranasal sinus cancer",
          "accessory sinus cancer",
          "accessory sinus carcinoma",
          "cancer of paranasal sinus",
          "carcinoma of accessory sinus",
          "carcinoma of paranasal sinus",
          "carcinoma of the accessory sinus",
          "carcinoma of the paranasal sinus",
          "paranasal sinus carcinoma",
          "adenoid cystic carcinoma of accessory sinus",
          "epidermoid carcinoma of the paranasal sinus",
          "mucoepidermoid carcinoma of accessory sinus",
          "paranasal sinus adenocarcinoma",
          "paranasal sinus adenoid cystic carcinoma",
          "paranasal sinus mucoepidermoid carcinoma",
          "paranasal sinus squamous cell carcinoma",
          "squamous cell carcinoma of paranasal sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "A malignant epithelial neoplasm arising in the paranasal sinus."
      },
      "child_count": 24,
      "reference_id": "MONDO:0000380"
    },
    {
      "id": 6713,
      "label": "adenoid cystic carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6712
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080202",
          "EFO:0000231",
          "GARD:0005743",
          "ICDO:8200/3",
          "MEDGEN:41382",
          "MESH:D003528",
          "NCIT:C2970",
          "ONCOTREE:ACYC",
          "UMLS:C0010606",
          "icd11.foundation:2127202862"
        ],
        "synonyms": [
          "adenocystic carcinoma",
          "adenoid cystic cancer",
          "adenoid cystic carcinoma",
          "cylindroid adenocarcinoma",
          "cribriform carcinoma",
          "cylindroma"
        ],
        "definition": "A malignant tumor arising from the epithelial cells. Microscopically, the neoplastic epithelial cells form cylindrical spatial configurations (cribriform or classic type of adenoid cystic carcinoma), cordlike structures (tubular type of adenoid cystic carcinoma), or solid structures (basaloid variant of adenoid cystic carcinoma). Adenoid cystic carcinomas mostly occur in the salivary glands. Other primary sites of involvement include the lacrimal gland, the larynx, and the lungs. Adenoid cystic carcinomas spread along nerve sheaths, resulting in severe pain, and they tend to recur. Lymph node metastases are unusual; hematogenous tumor spread is characteristic."
      },
      "child_count": 17,
      "reference_id": "MONDO:0004971"
    }
  ],
  "children": [
    {
      "id": 7756,
      "label": "ethmoid sinus adenoid cystic carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3947,
        7878
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2764",
          "EFO:1000246",
          "GARD:0024326",
          "MEDGEN:232471",
          "NCIT:C6238",
          "UMLS:C1333473"
        ],
        "synonyms": [
          "adenoid cystic carcinoma of the ethmoid sinus"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "An adenoid cystic carcinoma that affects the ethmoid sinus."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006201"
    },
    {
      "id": 7837,
      "label": "maxillary sinus adenoid cystic carcinoma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        3934,
        7878
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:7198",
          "EFO:1000365",
          "GARD:0024364",
          "MEDGEN:233168",
          "NCIT:C6239",
          "UMLS:C1334643"
        ],
        "synonyms": [
          "adenoid cystic carcinoma of the maxillary sinus",
          "maxillary sinus adenoid cystic carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          },
          {
            "ref": "MONDO:0006858",
            "name": "mouth disorder"
          },
          {
            "ref": "MONDO:0024623",
            "name": "otorhinolaryngologic disease"
          }
        ],
        "definition": "An adenoid cystic carcinoma that arises from the maxillary sinus. It usually has an aggressive clinical course."
      },
      "child_count": 0,
      "reference_id": "MONDO:0006297"
    }
  ],
  "roots": [
    {
      "id": 2879,
      "label": "paranasal sinus carcinoma"
    },
    {
      "id": 6713,
      "label": "adenoid cystic carcinoma"
    }
  ]
}