{
  "id": 7977,
  "label": "undifferentiated pleomorphic sarcoma, inflammatory variant",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0006480",
  "properties": {
    "xrefs": [
      "DOID:6192",
      "EFO:1000608",
      "GARD:0024429",
      "MEDGEN:235211",
      "NCIT:C6497",
      "UMLS:C1334180"
    ],
    "synonyms": [
      "inflammatory MFH",
      "inflammatory malignant fibrous histiocytoma",
      "malignant xanthogranuloma",
      "undifferentiated pleomorphic sarcoma, inflammatory variant"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "An undifferentiated pleomorphic sarcoma characterized by the presence of numerous inflammatory cells."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4275,
      "label": "undifferentiated pleomorphic sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7165,
        18239,
        20297
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1907",
          "EFO:1001972",
          "GARD:0006963",
          "HGNC:16982",
          "ICD9:171.9",
          "ICDO:8830/3",
          "MEDGEN:87248",
          "MESH:D051677",
          "MedDRA:10025552",
          "NCIT:C114541",
          "NCIT:C4247",
          "ONCOTREE:MFH",
          "Orphanet:2023",
          "SCTID:443439001",
          "UMLS:C0334463"
        ],
        "synonyms": [
          "MFH",
          "Storiform-pleomorphic MFH",
          "Storiform-pleomorphic fibrous histiocytoma",
          "Storiform-pleomorphic malignant fibrous histiocytoma",
          "UPS",
          "Unclassified Pleomorphic sarcoma (formerly \"MFH\")",
          "Unclassified Pleomorphic sarcoma (formerly \"malignant fibrous histiocytoma\")",
          "adult malignant fibrous histiocytoma",
          "adult unclassified pleomorphic sarcoma",
          "adult undifferentiated pleomorphic sarcoma",
          "fibrous histiocytoma, malignant",
          "fibrous histiocytoma, malignant (morphologic abnormality)",
          "fibroxanthosarcoma",
          "fibroxanthosarcoma (morphologic abnormality)",
          "histiocytoma, fibrous, malignant",
          "malignant fibrous cytoma",
          "malignant fibrous histiocytoma",
          "malignant fibrous histiocytoma of soft tissue and bone",
          "malignant fibrous histiocytoma of the soft tissue and bone",
          "malignant fibroxanthoma",
          "unclassified pleomorphic sarcoma",
          "undifferentiated pleomorphic sarcoma",
          "undifferentiated pleomorphic soft tissue sarcoma",
          "malignant fibrohistiocytic tumors",
          "malignant fibrohistiocytic tumours",
          "undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma."
      },
      "child_count": 9,
      "reference_id": "MONDO:0002142"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4275,
      "label": "undifferentiated pleomorphic sarcoma"
    }
  ]
}