{
  "id": 9231,
  "label": "acute monocytic leukemia",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0007896",
  "properties": {
    "xrefs": [
      "CSP:2004-2820",
      "DOID:8864",
      "EFO:0000221",
      "GARD:0000525",
      "ICD10CM:C93.0",
      "ICD9:206.0",
      "ICDO:9891/3",
      "MEDGEN:7319",
      "MESH:D007948",
      "MedDRA:10000871",
      "MedDRA:10059439",
      "NANDO:2200008",
      "NANDO:2200009",
      "NCIT:C4861",
      "OMIM:151380",
      "ONCOTREE:AMOL",
      "Orphanet:514",
      "SCTID:413441006",
      "UMLS:C0023465",
      "icd11.foundation:517546180"
    ],
    "synonyms": [
      "monocytic leukaemia",
      "monocytic leukemia",
      "AML M5",
      "acute monoblastic leukaemia and acute monocytic leukaemia",
      "acute monocytic leukaemia (FAB M5B)",
      "acute monocytic leukaemia (FAB M5b)",
      "acute monocytic leukemia",
      "acute monocytic leukemia (FAB M5B)",
      "acute monocytic leukemia (FAB M5b)",
      "acute monocytic leukemia, morphology (morphologic abnormality)",
      "leukemia, monocytic, malignant",
      "monocytic leukemia, acute",
      "AML-M5",
      "acute monoblastic leukaemia",
      "acute monoblastic leukemia",
      "acute monoblastic/monocytic leukaemia",
      "acute monoblastic/monocytic leukemia",
      "acute myeloblastic leukaemia type 5",
      "acute myeloblastic leukemia type 5",
      "leukemia, acute monocytic"
    ],
    "categories": [
      {
        "ref": "MONDO:0002081",
        "name": "musculoskeletal system disorder"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      },
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "Acute monoblastic leukemia (AML-M5), is one of the most common subtypes of acute myeloid leukemia (AML) that is either comprised of more than 80% of monoblasts (AML-M5a) or 30-80% monoblasts with (pro)monocytic differentiation (AML-M5b). AML-M5 presents with asthenia, pallor, fever, and dizziness. Specific features of AML-M5 include hyperleukocytosis, propensity for extramedullary infiltrates, coagulation abnormalities including disseminated intravascular coagulation and neurological disorders. Leukemia cutis and gingival infiltration can also be seen. A characteristic translocation observed in AML-M5 is t(9;11)."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 3,
  "parents": [
    {
      "id": 6392,
      "label": "monocytic leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6789
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8527",
          "GARD:0024074",
          "ICD10CM:C93",
          "ICD9:206.8",
          "ICD9:206.80",
          "ICD9:206.81",
          "ICD9:206.90",
          "ICD9:206.91",
          "MEDGEN:109338",
          "SCTID:188744006",
          "UMLS:C0598894"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ]
      },
      "child_count": 2,
      "reference_id": "MONDO:0004600"
    },
    {
      "id": 18806,
      "label": "acute myeloid leukemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6429,
        11789
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:9119",
          "EFO:0000222",
          "GARD:0012757",
          "ICD10CM:C92.0",
          "ICD9:205.0",
          "ICD9:205.00",
          "ICDO:9861/3",
          "MEDGEN:9730",
          "MESH:D015470",
          "MedDRA:10000880",
          "NCIT:C3171",
          "NORD:1905",
          "OMIM:601626",
          "ONCOTREE:AML",
          "Orphanet:519",
          "SCTID:91861009",
          "UMLS:C0023467"
        ],
        "synonyms": [
          "AML",
          "AML - acute myeloid leukaemia",
          "AML - acute myeloid leukemia",
          "ANLL",
          "acute Nonlymphocytic leukaemia",
          "acute Nonlymphocytic leukemia",
          "acute granulocytic leukaemia",
          "acute granulocytic leukemia",
          "acute myeloblastic leukemia",
          "acute myelocytic leukaemia",
          "acute myelocytic leukemia",
          "acute myelogenous leukemia",
          "acute myelogenous leukemias",
          "acute myeloid leukaemia (AML)",
          "acute myeloid leukemia",
          "acute myeloid leukemia (AML)",
          "acute myeloid leukemia, somatic",
          "acute nonlymphocytic leukaemia",
          "acute nonlymphocytic leukemia",
          "hematopoeitic - acute Myleogenous leukaemia (AML)",
          "hematopoeitic - acute Myleogenous leukemia (AML)",
          "leukemia, acute myeloid, autosomal dominant, somatic mutation",
          "leukemia, acute myeloid, reduced survival in, somatic",
          "leukemia, acute myeloid, somatic",
          "leukemia, acute myeloid, susceptibility to, autosomal dominant, somatic mutation",
          "leukemia, myelocytic, acute",
          "myeloid leukemia, acute",
          "myeloid leukemia, acute, M4/M4Eo subtype, somatic",
          "acute non lymphoblastic leukaemia",
          "acute non lymphoblastic leukemia",
          "leukemia, acute myelogenous",
          "leukemia, acute myeloid",
          "leukemia, acute myeloid, susceptibility to"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "Acute myeloid leukemia (AML) is a group of neoplasms arising from precursor cells committed to the myeloid cell-line differentiation. All of them are characterized by clonal expansion of myeloid blasts. AML manifests by fever, pallor, anemia, hemorrhages and recurrent infections."
      },
      "child_count": 156,
      "reference_id": "MONDO:0018874"
    }
  ],
  "children": [
    {
      "id": 3165,
      "label": "adult acute monocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        9231
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080149",
          "EFO:1001933",
          "GARD:0022837",
          "MEDGEN:128856",
          "NANDO:2200008",
          "NANDO:2200009",
          "NCIT:C8263",
          "UMLS:C0280634"
        ],
        "synonyms": [
          "acute monocytic leukaemia",
          "acute monocytic leukemia",
          "M5b adult acute differentiated monocytic leukaemia",
          "M5b adult acute differentiated monocytic leukemia",
          "M5b adult acute leukaemia",
          "M5b adult acute leukemia",
          "acute monocytic leukaemia of adults",
          "acute monocytic leukemia of adults",
          "adult acute differentiated monocytic leukaemia (M5b)",
          "adult acute differentiated monocytic leukemia (M5b)",
          "adult acute monocytic leukemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "A acute monocytic leukemia that occurs in an adult."
      },
      "child_count": 0,
      "reference_id": "MONDO:0000875"
    },
    {
      "id": 5892,
      "label": "aleukemic monocytic leukemia cutis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        5609,
        9231
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:6958",
          "GARD:0023794",
          "MEDGEN:231050",
          "NCIT:C5630",
          "UMLS:C1332232"
        ],
        "synonyms": [
          "aleukemic monocytic leukemia cutis"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0004051"
    },
    {
      "id": 6430,
      "label": "subacute monocytic leukemia",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        9231
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8696",
          "GARD:0024079",
          "ICD9:206.2",
          "ICD9:206.20",
          "MEDGEN:508955",
          "SCTID:188746008",
          "UMLS:C0152275"
        ],
        "categories": [
          {
            "ref": "MONDO:0002081",
            "name": "musculoskeletal system disorder"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0004644"
    }
  ],
  "roots": [
    {
      "id": 6392,
      "label": "monocytic leukemia"
    },
    {
      "id": 18806,
      "label": "acute myeloid leukemia"
    }
  ]
}