{
  "id": 10007,
  "label": "adrenocortical carcinoma, hereditary",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0008734",
  "properties": {
    "xrefs": [
      "GARD:0015132",
      "MEDGEN:348508",
      "MESH:C565972",
      "OMIM:202300",
      "UMLS:C1859972"
    ],
    "synonyms": [
      "adrenocortical carcinoma, hereditary",
      "hereditary adrenal cortex carcinoma",
      "ADCC",
      "adrenocortical carcinoma, paediatric",
      "adrenocortical carcinoma, pediatric"
    ],
    "categories": [
      {
        "ref": "MONDO:0002118",
        "name": "urinary system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "An instance of adrenal cortex carcinoma that is caused by an inherited modification of the individual's genome."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 5006,
      "label": "hereditary renal cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7199,
        23932
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:4455",
          "GARD:0023326",
          "MEDGEN:392857",
          "MESH:C536851",
          "NCIT:C39789",
          "SCTID:717736007",
          "UMLS:C2608055"
        ],
        "synonyms": [
          "hereditary renal cell cancer",
          "hereditary renal cell carcinoma",
          "hereditary renal cell carcinoma (disease)",
          "familial renal carcinoma",
          "hereditary renal carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          }
        ],
        "definition": "An instance of renal cell carcinoma (disease) that is caused by an inherited modification of the individual's genome."
      },
      "child_count": 14,
      "reference_id": "MONDO:0003008"
    },
    {
      "id": 8111,
      "label": "adrenal cortex carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4233,
        4840,
        6814,
        20494
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3948",
          "DOID:3959",
          "DOID:660",
          "EFO:1000796",
          "GARD:0000558",
          "HP:0006744",
          "ICDO:8370/3",
          "MEDGEN:104917",
          "MedDRA:10001388",
          "NANDO:2200073",
          "NCIT:C9325",
          "NORD:733",
          "ONCOTREE:ACC",
          "Orphanet:1501",
          "SCTID:255035007",
          "UMLS:C0206686",
          "icd11.foundation:114092945"
        ],
        "synonyms": [
          "adrenal cortex cancer",
          "adrenal cortical tumors",
          "adrenal cortical tumours",
          "adrenocortical cancer",
          "cancer of the adrenal cortex",
          "malignant adrenocortical tumor",
          "malignant adrenocortical tumour",
          "malignant neoplasm of adrenal cortex",
          "malignant tumor of adrenal cortex",
          "malignant tumour of adrenal cortex",
          "ACC",
          "Adenoid Cystic Carcinoma",
          "adenocarcinoma, adrenocortical, malignant",
          "adrenal cortex adenocarcinoma",
          "adrenal cortex carcinoma",
          "adrenal cortical adenocarcinoma",
          "adrenal cortical carcinoma",
          "adrenal cortical carcinoma (morphologic abnormality)",
          "adrenocortical carcinoma",
          "adrenocortical carcinoma (disease)",
          "carcinoma of adrenal cortex",
          "carcinoma of the adrenal cortex",
          "carcinoma, adrenocortical, malignant",
          "cortical cell carcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival."
      },
      "child_count": 4,
      "reference_id": "MONDO:0006639"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 5006,
      "label": "hereditary renal cell carcinoma"
    },
    {
      "id": 8111,
      "label": "adrenal cortex carcinoma"
    }
  ]
}