{
  "id": 10561,
  "label": "pulmonary venoocclusive disease 2",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0009329",
  "properties": {
    "xrefs": [
      "DOID:0081269",
      "GARD:0015027",
      "ICD9:416.8",
      "MEDGEN:90956",
      "MESH:C535861",
      "OMIM:234810",
      "Orphanet:199241",
      "SCTID:233949008",
      "UMLS:C0340848"
    ],
    "synonyms": [
      "pulmonary capillary hemangiomatosis",
      "PVOD2",
      "familial pulmonary capillary hemangiomatosis",
      "hemangiomatosis, familial pulmonary capillary",
      "pulmonary venoocclusive disease 2, autosomal recessive"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005087",
        "name": "respiratory system disorder"
      }
    ],
    "definition": "A rare form of pulmonary arterial hypertension (PAH) characterized by a capillary infiltration of the pulmonary interstitium, bronchioles and pleura leading to elevated pulmonary arterial resistance and right heart failure. PCH is potentially fatal."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 11139,
      "label": "pulmonary venoocclusive disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5714,
        6971,
        7065
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5453",
          "GARD:0010153",
          "ICD9:416.8",
          "MEDGEN:18769",
          "MESH:D011668",
          "MedDRA:10037458",
          "NANDO:1200427",
          "NCIT:C85039",
          "OMIMPS:265450",
          "Orphanet:31837",
          "SCTID:89420002",
          "UMLS:C0034091",
          "icd11.foundation:1368993024"
        ],
        "synonyms": [
          "PVOD",
          "pulmonary capillary hemangiomatosis",
          "pulmonary veno-occlusive disease",
          "obstructive disease of the pulmonary veins"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          }
        ],
        "definition": "A disorder characterized by pulmonary venous constriction or occlusion, resulting in pulmonary hypertension."
      },
      "child_count": 6,
      "reference_id": "MONDO:0009937"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 11139,
      "label": "pulmonary venoocclusive disease"
    }
  ]
}