{
  "id": 13171,
  "label": "granulomatosis with polyangiitis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0012105",
  "properties": {
    "xrefs": [
      "DOID:12132",
      "EFO:0005297",
      "GARD:0007880",
      "ICD10CM:M31.3",
      "ICD9:446.4",
      "MEDGEN:811223",
      "MESH:D014890",
      "MedDRA:10047888",
      "NANDO:1200263",
      "NANDO:1201009",
      "NANDO:2200424",
      "NCIT:C123111",
      "NCIT:C3444",
      "NORD:1840",
      "OMIM:608710",
      "Orphanet:900",
      "SCTID:195353004",
      "UMLS:C3495801",
      "icd11.foundation:1020056159"
    ],
    "synonyms": [
      "ANCA-associated vasculitis",
      "Wg",
      "GPA",
      "Wegener granulomatosis",
      "Wegener's granulomatosis",
      "Wegener's syndrome",
      "granulomatosis - Wegener's",
      "granulomatosis with polyangiitis",
      "necrotizing respiratory granulomatosis",
      "pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis",
      "Midline granulomatosis"
    ],
    "categories": [
      {
        "ref": "MONDO:0002118",
        "name": "urinary system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      }
    ],
    "definition": "A small-vessel necrotizing vasculitis characterized by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 4542,
      "label": "glomerulonephritis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        3410,
        19482
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2921",
          "GARD:0006516",
          "HP:0000099",
          "ICD9:583.9",
          "MEDGEN:6616",
          "MESH:D005921",
          "NCIT:C26784",
          "SCTID:36171008",
          "UMLS:C0017658"
        ],
        "synonyms": [
          "glomerular nephritis",
          "glomerulonephritis",
          "glomerulonephritis (disease)",
          "nephritis of renal glomerulus",
          "renal glomerulus nephritis",
          "bright's disease"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          }
        ],
        "definition": "A renal disorder characterized by damage in the glomeruli. It may be acute or chronic, focal or diffuse, and it may lead to renal failure. Causes include autoimmune disorders, infections, diabetes, and malignancies."
      },
      "child_count": 40,
      "reference_id": "MONDO:0002462"
    },
    {
      "id": 6778,
      "label": "immune system disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        29379
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2914",
          "EFO:0000540",
          "ICD9:279",
          "ICD9:279.1",
          "ICD9:279.10",
          "ICD9:279.19",
          "ICD9:279.4",
          "ICD9:279.49",
          "ICD9:279.8",
          "ICD9:279.9",
          "MEDGEN:5759",
          "MESH:D007154",
          "NANDO:1100004",
          "NANDO:2100202",
          "NCIT:C3507",
          "SCTID:414029004",
          "UMLS:C0021053"
        ],
        "synonyms": [
          "disease of immune system",
          "disease or disorder of immune system",
          "disorder of immune system",
          "immune disease",
          "immune disorder",
          "immune dysfunction",
          "immune system disease or disorder",
          "immune system disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "A disorder resulting from an abnormality in the immune system."
      },
      "child_count": 47,
      "reference_id": "MONDO:0005046"
    },
    {
      "id": 16324,
      "label": "anti-neutrophil cytoplasmic antibody-associated vasculitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        24822
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0013011",
          "MEDGEN:403453",
          "MESH:D056648",
          "Orphanet:156152",
          "UMLS:C2717865",
          "icd11.foundation:1404622826"
        ],
        "synonyms": [
          "AAV",
          "ANCA-associated vasculitis",
          "antineutrophil cytoplasmic antibody-associated vasculitis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Group of systemic vasculitis with a strong association with anca. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls."
      },
      "child_count": 2,
      "reference_id": "MONDO:0015492"
    }
  ],
  "children": [
    {
      "id": 16622,
      "label": "eosinophilic granulomatosis with polyangiitis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4370,
        13171
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3049",
          "EFO:0007208",
          "GARD:0006111",
          "ICD10CM:M30.1",
          "MEDGEN:3088",
          "MESH:D015267",
          "MedDRA:10048594",
          "NANDO:1200264",
          "NANDO:2200427",
          "NCIT:C34481",
          "NORD:973",
          "Orphanet:183",
          "SCTID:82275008",
          "UMLS:C0008728",
          "icd11.foundation:835880885"
        ],
        "synonyms": [
          "CSS",
          "Churg Strauss Syndrome",
          "Churg Strauss syndrome",
          "Churg-Strauss syndrome",
          "Churg-Strauss vasculitis",
          "EGPA",
          "allergic angiitides",
          "allergic angiitides, granulomatous",
          "allergic angiitis",
          "allergic angiitis and granulomatosis",
          "allergic angiitis, granulomatous",
          "allergic granulomatoses",
          "allergic granulomatosis",
          "allergic granulomatous Angiitides",
          "allergic granulomatous and angiitis",
          "allergic granulomatous angiitis",
          "angiitides, allergic",
          "angiitides, allergic granulomatous",
          "angiitides, granulomatous allergic",
          "angiitis, allergic",
          "angiitis, allergic granulomatous",
          "angiitis, granulomatous allergic",
          "eosinophilic granulomatous Vasculitides",
          "eosinophilic granulomatous vasculitis",
          "granulomatoses, allergic",
          "granulomatosis, allergic",
          "granulomatous allergic Angiitides",
          "granulomatous allergic angiitis",
          "granulomatous angiitides, allergic",
          "granulomatous angiitis, allergic",
          "granulomatous vasculitides, eosinophilic",
          "granulomatous vasculitis, eosinophilic",
          "syndrome, Churg-Strauss",
          "vasculitides, eosinophilic granulomatous",
          "vasculitis, Churg Strauss",
          "vasculitis, Churg-Strauss",
          "vasculitis, eosinophilic granulomatous"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          },
          {
            "ref": "MONDO:0002254",
            "name": "syndromic disease"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia."
      },
      "child_count": 0,
      "reference_id": "MONDO:0015943"
    }
  ],
  "roots": [
    {
      "id": 4542,
      "label": "glomerulonephritis"
    },
    {
      "id": 6778,
      "label": "immune system disorder"
    },
    {
      "id": 16324,
      "label": "anti-neutrophil cytoplasmic antibody-associated vasculitis"
    }
  ]
}