{
  "id": 13767,
  "label": "Kawasaki disease",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0012727",
  "properties": {
    "xrefs": [
      "DOID:13378",
      "EFO:0004246",
      "GARD:0006816",
      "ICD10CM:M30.3",
      "ICD9:446.1",
      "MEDGEN:10118",
      "MESH:D009080",
      "MedDRA:10023320",
      "NCIT:C34825",
      "OMIM:611775",
      "Orphanet:2331",
      "SCTID:75053002",
      "UMLS:C0026691",
      "icd11.foundation:540285662"
    ],
    "synonyms": [
      "Kawasaki syndrome",
      "acute febrile mucocutaneous lymph node syndrome",
      "acute febrile mucocutaneous lymph node syndrome [MCLS]",
      "infantile polyarteritis nodosa",
      "mucocutaneous lymph node syndrome"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      }
    ],
    "definition": "A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4199,
      "label": "lymphadenitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6675,
        20399
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1602",
          "HP:0002840",
          "ICD9:289.1",
          "ICD9:683",
          "MEDGEN:7410",
          "MESH:D008199",
          "NCIT:C26821",
          "SCTID:41174002",
          "UMLS:C0024205",
          "icd11.foundation:1483611415"
        ],
        "synonyms": [
          "adenitis",
          "lymph node inflammation",
          "lymph nodeitis",
          "lymphadenitis",
          "lymphadenitis (disease)",
          "acute adenitis",
          "acute lymphadenitis",
          "chronic adenitis",
          "chronic lymphadenitis",
          "lymph gland infection"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "Acute or chronic inflammation of one or more lymph nodes. It is usually caused by an infectious process."
      },
      "child_count": 20,
      "reference_id": "MONDO:0002052"
    },
    {
      "id": 18813,
      "label": "vasculitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7065,
        20399
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:865",
          "EFO:0006803",
          "GARD:0018844",
          "MEDGEN:12054",
          "MESH:D014657",
          "MedDRA:10036023",
          "MedDRA:10047115",
          "NCIT:C26912",
          "Orphanet:52759",
          "SCTID:31996006",
          "UMLS:C0042384",
          "Wikipedia:Vasculitis",
          "icd11.foundation:572581721"
        ],
        "synonyms": [
          "systemic vasculitis",
          "angiitis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. Behcet disease) to relatively minor skin disease."
      },
      "child_count": 36,
      "reference_id": "MONDO:0018882"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4199,
      "label": "lymphadenitis"
    },
    {
      "id": 18813,
      "label": "vasculitis"
    }
  ]
}