{
  "id": 16228,
  "label": "primary central nervous system vasculitis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0015374",
  "properties": {
    "xrefs": [
      "GARD:0008703",
      "MEDGEN:419271",
      "MESH:C537295",
      "Orphanet:140989",
      "UMLS:C2930862",
      "icd11.foundation:2130738127"
    ],
    "synonyms": [
      "PACNS",
      "PCNSV",
      "isolated angiitis of the central nervous system",
      "primary angiitis of the central nervous system",
      "primary central nervous system vasculitis",
      "primary vasculitis of the central nervous system",
      "granulomatous angiitis of the central nervous system",
      "primary CNS vasculitis"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ]
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 5281,
      "label": "central nervous system vasculitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4657,
        18813,
        23165
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:525",
          "GARD:0023462",
          "MEDGEN:148408",
          "MESH:D020293",
          "NCIT:C84622",
          "UMLS:C0751878"
        ],
        "synonyms": [
          "central nervous system vasculitis",
          "vasculitis of central nervous system"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "Vasculitis affecting the blood vessels of the brain and/or spinal cord."
      },
      "child_count": 15,
      "reference_id": "MONDO:0003346"
    }
  ],
  "children": [
    {
      "id": 23986,
      "label": "rapidly progressive primary central nervous system vasculitis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        16228
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0026097"
        ],
        "synonyms": [
          "rapidly progressive PCNSV"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A subset of primary central nervous system vasculitis where disease is rapidly progressive after onset that is characterized by bilateral, multiple, large cerebral vessel lesions and multiple CNS infarctions."
      },
      "child_count": 0,
      "reference_id": "MONDO:0100248"
    }
  ],
  "roots": [
    {
      "id": 5281,
      "label": "central nervous system vasculitis"
    }
  ]
}