{
  "id": 16324,
  "label": "anti-neutrophil cytoplasmic antibody-associated vasculitis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0015492",
  "properties": {
    "xrefs": [
      "GARD:0013011",
      "MEDGEN:403453",
      "MESH:D056648",
      "Orphanet:156152",
      "UMLS:C2717865",
      "icd11.foundation:1404622826"
    ],
    "synonyms": [
      "AAV",
      "ANCA-associated vasculitis",
      "antineutrophil cytoplasmic antibody-associated vasculitis"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "Group of systemic vasculitis with a strong association with anca. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 24822,
      "label": "necrotizing vasculitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        18813
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0005106",
          "MEDGEN:230813",
          "NCIT:C70635",
          "UMLS:C1318520"
        ],
        "synonyms": [
          "systemic vasculitis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A type of vasculitis that is comprised of vasculitides that present with necrosis."
      },
      "child_count": 3,
      "reference_id": "MONDO:0800113"
    }
  ],
  "children": [
    {
      "id": 13171,
      "label": "granulomatosis with polyangiitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4542,
        6778,
        16324
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:12132",
          "EFO:0005297",
          "GARD:0007880",
          "ICD10CM:M31.3",
          "ICD9:446.4",
          "MEDGEN:811223",
          "MESH:D014890",
          "MedDRA:10047888",
          "NANDO:1200263",
          "NANDO:1201009",
          "NANDO:2200424",
          "NCIT:C123111",
          "NCIT:C3444",
          "NORD:1840",
          "OMIM:608710",
          "Orphanet:900",
          "SCTID:195353004",
          "UMLS:C3495801",
          "icd11.foundation:1020056159"
        ],
        "synonyms": [
          "ANCA-associated vasculitis",
          "Wg",
          "GPA",
          "Wegener granulomatosis",
          "Wegener's granulomatosis",
          "Wegener's syndrome",
          "granulomatosis - Wegener's",
          "granulomatosis with polyangiitis",
          "necrotizing respiratory granulomatosis",
          "pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis",
          "Midline granulomatosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "A small-vessel necrotizing vasculitis characterized by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis."
      },
      "child_count": 3,
      "reference_id": "MONDO:0012105"
    },
    {
      "id": 19005,
      "label": "microscopic polyangiitis",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        16324,
        23218
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:1000784",
          "GARD:0003652",
          "ICD10CM:M31.7",
          "MEDGEN:389393",
          "MESH:D055953",
          "MedDRA:10063344",
          "NANDO:1200262",
          "NANDO:2200426",
          "NCIT:C70549",
          "Orphanet:727",
          "SCTID:239928004",
          "UMLS:C2347126",
          "icd11.foundation:999231798"
        ],
        "synonyms": [
          "MPA",
          "Micropolyangiitis",
          "microscopic polyarteritis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Microscopic polyangiitis (MPA) is an inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs."
      },
      "child_count": 0,
      "reference_id": "MONDO:0019124"
    }
  ],
  "roots": [
    {
      "id": 24822,
      "label": "necrotizing vasculitis"
    }
  ]
}