{
  "id": 16564,
  "label": "primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0015811",
  "properties": {
    "xrefs": [
      "GARD:0020157",
      "MEDGEN:1388716",
      "NCIT:C45339",
      "Orphanet:178528",
      "SCTID:765136002",
      "UMLS:C4518232"
    ],
    "synonyms": [
      "Berti lymphoma",
      "primary cutaneous epidermotropic cytotoxic CD8+ T-cell lymphoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 16515,
      "label": "primary cutaneous T-cell lymphoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        16517,
        18826
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0006226",
          "MEDGEN:36336",
          "MedDRA:10011677",
          "Orphanet:171901",
          "UMLS:C0079773"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ]
      },
      "child_count": 8,
      "reference_id": "MONDO:0015758"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 16515,
      "label": "primary cutaneous T-cell lymphoma"
    }
  ]
}