{
  "id": 16622,
  "label": "eosinophilic granulomatosis with polyangiitis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0015943",
  "properties": {
    "xrefs": [
      "DOID:3049",
      "EFO:0007208",
      "GARD:0006111",
      "ICD10CM:M30.1",
      "MEDGEN:3088",
      "MESH:D015267",
      "MedDRA:10048594",
      "NANDO:1200264",
      "NANDO:2200427",
      "NCIT:C34481",
      "NORD:973",
      "Orphanet:183",
      "SCTID:82275008",
      "UMLS:C0008728",
      "icd11.foundation:835880885"
    ],
    "synonyms": [
      "CSS",
      "Churg Strauss Syndrome",
      "Churg Strauss syndrome",
      "Churg-Strauss syndrome",
      "Churg-Strauss vasculitis",
      "EGPA",
      "allergic angiitides",
      "allergic angiitides, granulomatous",
      "allergic angiitis",
      "allergic angiitis and granulomatosis",
      "allergic angiitis, granulomatous",
      "allergic granulomatoses",
      "allergic granulomatosis",
      "allergic granulomatous Angiitides",
      "allergic granulomatous and angiitis",
      "allergic granulomatous angiitis",
      "angiitides, allergic",
      "angiitides, allergic granulomatous",
      "angiitides, granulomatous allergic",
      "angiitis, allergic",
      "angiitis, allergic granulomatous",
      "angiitis, granulomatous allergic",
      "eosinophilic granulomatous Vasculitides",
      "eosinophilic granulomatous vasculitis",
      "granulomatoses, allergic",
      "granulomatosis, allergic",
      "granulomatous allergic Angiitides",
      "granulomatous allergic angiitis",
      "granulomatous angiitides, allergic",
      "granulomatous angiitis, allergic",
      "granulomatous vasculitides, eosinophilic",
      "granulomatous vasculitis, eosinophilic",
      "syndrome, Churg-Strauss",
      "vasculitides, eosinophilic granulomatous",
      "vasculitis, Churg Strauss",
      "vasculitis, Churg-Strauss",
      "vasculitis, eosinophilic granulomatous"
    ],
    "categories": [
      {
        "ref": "MONDO:0002118",
        "name": "urinary system disorder"
      },
      {
        "ref": "MONDO:0002254",
        "name": "syndromic disease"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      }
    ],
    "definition": "Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4370,
      "label": "syndromic disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        29379
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:225",
          "MEDGEN:11688",
          "MESH:D013577",
          "NCIT:C28193",
          "OGMS:0000086",
          "UMLS:C0039082"
        ],
        "synonyms": [
          "cluster, symptom",
          "clusters, symptom",
          "symptom cluster",
          "symptom clusters",
          "syndrome",
          "syndrome associated with disease or disorder",
          "syndromes",
          "syndromic disease",
          "syndromic disease or disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0002254",
            "name": "syndromic disease"
          }
        ],
        "definition": "A group of signs, symptoms, and clinicopathological characteristics that may or may not have a genetic basis and collectively define an abnormal condition."
      },
      "child_count": 1182,
      "reference_id": "MONDO:0002254"
    },
    {
      "id": 13171,
      "label": "granulomatosis with polyangiitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4542,
        6778,
        16324
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:12132",
          "EFO:0005297",
          "GARD:0007880",
          "ICD10CM:M31.3",
          "ICD9:446.4",
          "MEDGEN:811223",
          "MESH:D014890",
          "MedDRA:10047888",
          "NANDO:1200263",
          "NANDO:1201009",
          "NANDO:2200424",
          "NCIT:C123111",
          "NCIT:C3444",
          "NORD:1840",
          "OMIM:608710",
          "Orphanet:900",
          "SCTID:195353004",
          "UMLS:C3495801",
          "icd11.foundation:1020056159"
        ],
        "synonyms": [
          "ANCA-associated vasculitis",
          "Wg",
          "GPA",
          "Wegener granulomatosis",
          "Wegener's granulomatosis",
          "Wegener's syndrome",
          "granulomatosis - Wegener's",
          "granulomatosis with polyangiitis",
          "necrotizing respiratory granulomatosis",
          "pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis",
          "Midline granulomatosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "A small-vessel necrotizing vasculitis characterized by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis."
      },
      "child_count": 3,
      "reference_id": "MONDO:0012105"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4370,
      "label": "syndromic disease"
    },
    {
      "id": 13171,
      "label": "granulomatosis with polyangiitis"
    }
  ]
}