{
  "id": 16722,
  "label": "vaginal rhabdomyosarcoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0016095",
  "properties": {
    "xrefs": [
      "GARD:0020348",
      "MEDGEN:925567",
      "NCIT:C128080",
      "Orphanet:206492",
      "SCTID:766759009",
      "UMLS:C4288035"
    ],
    "synonyms": [
      "rhabdomyosarcoma (disease) of vagina",
      "vagina rhabdomyosarcoma",
      "vagina rhabdomyosarcoma (disease)",
      "vaginal rhabdomyosarcoma",
      "vulvovaginal rhabdomyosarcoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0005039",
        "name": "reproductive system disorder"
      }
    ],
    "definition": "A malignant mesenchymal neoplasm with skeletal muscle differentiation arising from the vagina."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 4273,
      "label": "vagina sarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        3623,
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1901",
          "GARD:0023074",
          "MEDGEN:65971",
          "NCIT:C7737",
          "UMLS:C0238519"
        ],
        "synonyms": [
          "sarcoma of the vagina",
          "sarcoma of vagina",
          "vagina sarcoma",
          "vaginal sarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          }
        ],
        "definition": "A malignant mesenchymal neoplasm that arises from the vagina. Representative examples include botryoid-type embryonal rhabdomyosarcoma, leiomyosarcoma, and endometrioid stromal sarcoma."
      },
      "child_count": 6,
      "reference_id": "MONDO:0002140"
    },
    {
      "id": 6928,
      "label": "rhabdomyosarcoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        18239
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3247",
          "EFO:0002918",
          "GARD:0011951",
          "HP:0002859",
          "ICD9:171.9",
          "ICDO:8900/3",
          "MEDGEN:20561",
          "MESH:D012208",
          "MedDRA:10039022",
          "NANDO:2200056",
          "NCIT:C3359",
          "ONCOTREE:RMS",
          "Orphanet:780",
          "SCTID:302847003",
          "UMLS:C0035412"
        ],
        "synonyms": [
          "rhabdomyosarcoma",
          "rhabdomyosarcoma (disease)",
          "rhabdomyosarcoma, malignant"
        ],
        "definition": "A rare aggressive malignant mesenchymal neoplasm arising from skeletal muscle. It usually occurs in children and young adults. Only a small percentage of tumors arise in the skeletal muscle of the extremities. The majority arise in other anatomical sites."
      },
      "child_count": 20,
      "reference_id": "MONDO:0005212"
    }
  ],
  "children": [
    {
      "id": 5847,
      "label": "botryoid-type embryonal rhabdomyosarcoma of the vagina",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4639,
        16722
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:6788",
          "GARD:0023767",
          "MEDGEN:267758",
          "NCIT:C40268",
          "UMLS:C1511275"
        ],
        "synonyms": [
          "botryoid rhabdomyosarcoma of vagina",
          "botryoid-type embryonal rhabdomyosarcoma of the vagina",
          "sarcoma Botryoides of the vagina",
          "vagina botryoid rhabdomyosarcoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0005039",
            "name": "reproductive system disorder"
          }
        ],
        "definition": "A morphologic variant of embryonal rhabdomyosarcoma arising from the vagina. It is characterized by the formation of a cambium layer in the affected tissue and polypoid nodules within an abundant myxoid stroma."
      },
      "child_count": 4,
      "reference_id": "MONDO:0003994"
    }
  ],
  "roots": [
    {
      "id": 4273,
      "label": "vagina sarcoma"
    },
    {
      "id": 6928,
      "label": "rhabdomyosarcoma"
    }
  ]
}