{
  "id": 16943,
  "label": "Marburg acute multiple sclerosis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0016429",
  "properties": {
    "xrefs": [
      "GARD:0020572",
      "MEDGEN:1641985",
      "Orphanet:228157",
      "SCTID:766246000",
      "UMLS:C4707723",
      "icd11.foundation:113448281"
    ],
    "synonyms": [
      "acute multiple sclerosis, Marburg type",
      "acute multiple sclerosis, Marburg variant"
    ],
    "categories": [
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      },
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "Marburg acute multiple sclerosis is a rare variant of multiple sclerosis characterized by a rapidly progressive, aggressive form of multiple sclerosis with numerous large multifocal demyelinating lesions in deep white matter on cerebral MRI that usually leads to severe disability or death within weeks to months without remission. A relapsing form of multiple sclerosis is observed in surviving patients."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 6995,
      "label": "multiple sclerosis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2996,
        7209,
        8166,
        20199
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:2377",
          "ICD10CM:G35",
          "ICD10WHO:G35",
          "ICD9:340",
          "MEDGEN:10123",
          "MESH:D009103",
          "NANDO:1200023",
          "NANDO:2100250",
          "NANDO:2200904",
          "NCIT:C3243",
          "Orphanet:802",
          "SCTID:24700007",
          "UMLS:C0026769",
          "icd11.foundation:1298865187"
        ],
        "synonyms": [
          "generalised multiple sclerosis",
          "generalized multiple sclerosis",
          "insular sclerosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A progressive autoimmune disorder affecting the central nervous system resulting in demyelination. Patients develop physical and cognitive impairments that correspond with the affected nerve fibers."
      },
      "child_count": 16,
      "reference_id": "MONDO:0005301"
    },
    {
      "id": 20092,
      "label": "acute disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        24492
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "ICD9:799.89",
          "MEDGEN:1738",
          "MESH:D000208",
          "SCTID:2704003",
          "UMLS:C0001314"
        ],
        "synonyms": [
          "acute disease",
          "acute diseases",
          "disease, acute"
        ],
        "definition": "Disease having a short and relatively severe course."
      },
      "child_count": 119,
      "reference_id": "MONDO:0020683"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 6995,
      "label": "multiple sclerosis"
    },
    {
      "id": 20092,
      "label": "acute disease"
    }
  ]
}