{
  "id": 17063,
  "label": "primary pulmonary lymphoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0016570",
  "properties": {
    "xrefs": [
      "GARD:0018770",
      "MEDGEN:903876",
      "MedDRA:10037418",
      "Orphanet:2420",
      "SCTID:718200007",
      "UMLS:C4273669",
      "icd11.foundation:1042489672"
    ],
    "categories": [
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "Primary pulmonary lymphoma (PPL) is a rare lymphoma of the lung, defined as a clonal lymphoid proliferation affecting one or both lungs (parenchyma and/or bronchi) in a patient with no detectable extrapulmonary involvement at diagnosis or during the subsequent 3 months. PPL comprises low grade/indolent B cell PPL forms, the most frequent form represented by the marginal B-cell lymphoma of mucosa associated lymphoid tissue (MALT lymphoma) and other non-MALT low grade lymphomas; and more rarely high-grade B-cell PPL (including diffuse large B cell lymphoma) and lymphomatoid granulomatosis (LYG)."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 17548,
      "label": "primary organ-specific lymphoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6792
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021064",
          "MEDGEN:1826175",
          "NCIT:C7185",
          "Orphanet:279911",
          "UMLS:C5680788"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ]
      },
      "child_count": 8,
      "reference_id": "MONDO:0017207"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 17548,
      "label": "primary organ-specific lymphoma"
    }
  ]
}