{
  "id": 17706,
  "label": "frontotemporal dementia, right temporal atrophy variant",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0017399",
  "properties": {
    "xrefs": [
      "GARD:0025093",
      "Orphanet:293848",
      "SCTID:716667005"
    ],
    "synonyms": [
      "RTLA",
      "rvFTD"
    ],
    "categories": [
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "Right temporal lobar atrophy (RTLA) is an anatomic variant of frontotemporal dementia (FTD), characterized by behavioral dysfunction, personality changes, episodic memory loss, and prosopagnosia; attributable to an asymmetrical predominantly right-sided, frontotemporal atrophy."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 11992,
      "label": "semantic dementia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        16033,
        17505
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0051060",
          "DOID:0081391",
          "GARD:0010792",
          "MEDGEN:83268",
          "NANDO:1200550",
          "OMIM:600274",
          "Orphanet:100069",
          "UMLS:C0338462"
        ],
        "synonyms": [
          "dementia, frontotemporal",
          "dementia, frontotemporal, with or without parkinsonism",
          "semantic primary progressive aphasia",
          "semantic variant PPA",
          "FTD",
          "Ftdp17",
          "Ftld with Tau inclusions",
          "Pallidopontonigral Degeneration",
          "Pick Complex",
          "Wilhelmsen-Lynch disease",
          "dementia, frontotemporal, with Parkinsonism",
          "disinhibition-dementia-Parkinsonism-amyotrophy Complex",
          "frontotemporal dementia",
          "frontotemporal dementia with Parkinsonism",
          "frontotemporal lobar Degeneration with Tau inclusions",
          "frontotemporal lobe dementia",
          "multiple system tauopathy with presenile dementia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "Semantic dementia (SD) is a form of frontotemporal dementia (FTD), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes."
      },
      "child_count": 2,
      "reference_id": "MONDO:0010857"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 11992,
      "label": "semantic dementia"
    }
  ]
}