{
  "id": 18597,
  "label": "secondary polyarteritis nodosa",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0018594",
  "properties": {
    "xrefs": [
      "GARD:0021831",
      "MEDGEN:1843373",
      "Orphanet:439746",
      "UMLS:C5680050"
    ],
    "synonyms": [
      "Secondary PAN",
      "secondary PAN",
      "secondary periarteritis nodosa"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV)."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 19045,
      "label": "polyarteritis nodosa",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        23218
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:9810",
          "GARD:0007360",
          "ICD10CM:M30.0",
          "ICD9:446.0",
          "MEDGEN:14681",
          "MESH:D010488",
          "MedDRA:10036024",
          "NANDO:1200261",
          "NANDO:2200425",
          "NCIT:C26847",
          "NORD:1588",
          "Orphanet:767",
          "SCTID:155441006",
          "UMLS:C0031036",
          "icd11.foundation:1419332129"
        ],
        "synonyms": [
          "Küssmaul-Maier disease",
          "PAN",
          "classic polyarteritis nodosa",
          "classical polyarteritis nodosa",
          "panarteritis nodosa",
          "periarteritis nodosa",
          "polyarteritis nodosa",
          "periarteritis",
          "polyarteritis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Polyarteritis nodosa (PAN) is a rare, clinically heterogeneous, rheumatologic disease characterized by necrotizing inflammatory lesions affecting small- and medium-sized blood vessels. PAN most commonly affects skin, joints, peripheral nerves, the gut, and the kidney."
      },
      "child_count": 2,
      "reference_id": "MONDO:0019170"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 19045,
      "label": "polyarteritis nodosa"
    }
  ]
}