{
  "id": 18677,
  "label": "acquired Creutzfeldt-Jakob disease",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0018686",
  "properties": {
    "xrefs": [
      "GARD:0017788",
      "MEDGEN:1826177",
      "MESH:C538481",
      "NANDO:1200192",
      "Orphanet:454700",
      "UMLS:C5681100"
    ],
    "synonyms": [
      "acquired CJD",
      "acquired Creutzfeldt Jacob disease",
      "sporadic CJD"
    ],
    "categories": [
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "An instance of Creutzfeldt Jacob disease that is acquired during the lifetime of the individual."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 7041,
      "label": "Creutzfeldt Jacob disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7097
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:11949",
          "EFO:0004226",
          "GARD:0024173",
          "ICD9:046.1",
          "ICD9:046.19",
          "MEDGEN:7179",
          "MESH:D007562",
          "NCIT:C26802",
          "NORD:1014",
          "SCTID:792004",
          "UMLS:C0022336"
        ],
        "synonyms": [
          "CJD",
          "CJD (Creutzfeldt Jakob disease)",
          "Creutzfeldt Jakob Disease",
          "Creutzfeldt-Jacob disease",
          "Jakob-Creutzfeldt disease",
          "classic Creutzfeldt-Jakob disease",
          "Creutzfeldt-Jakob disease"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A rare transmittable degenerative disorder of the brain caused by prions. Morphologically it is characterized by spongiform degeneration of the cerebral and cerebellar cortex. Signs and symptoms include sleep disturbances, personality changes, aphasia, ataxia, muscle atrophy and weakness, visual loss, and myoclonus. It usually leads to death within a year from the onset of the disease."
      },
      "child_count": 3,
      "reference_id": "MONDO:0005357"
    }
  ],
  "children": [
    {
      "id": 8433,
      "label": "variant Creutzfeldt-Jakob disease",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        18677
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:5435",
          "EFO:1001233",
          "GARD:0009550",
          "ICD10CM:A81.01",
          "ICD9:046.11",
          "MEDGEN:138163",
          "MedDRA:10064199",
          "NANDO:1200194",
          "NCIT:C128438",
          "Orphanet:576370",
          "SCTID:304603007",
          "UMLS:C0376329",
          "icd11.foundation:378572696"
        ],
        "synonyms": [
          "vCJD"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A form of Creutzfeldt-Jakob disease that is most commonly contracted after consuming meat from an animal suffering from bovine spongiform encephalopathy."
      },
      "child_count": 0,
      "reference_id": "MONDO:0007012"
    },
    {
      "id": 22789,
      "label": "iatrogenic Creutzfeldt-Jakob disease",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        18677,
        23227
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0022329",
          "MEDGEN:908476",
          "NANDO:1200193",
          "Orphanet:576379",
          "UMLS:C2349757",
          "icd11.foundation:437591130"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0034976"
    }
  ],
  "roots": [
    {
      "id": 7041,
      "label": "Creutzfeldt Jacob disease"
    }
  ]
}