{
  "id": 18823,
  "label": "Plummer-Vinson syndrome",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0018895",
  "properties": {
    "xrefs": [
      "GARD:0008259",
      "ICD10CM:D50.1",
      "ICD9:280.8",
      "MEDGEN:45967",
      "MESH:D011004",
      "MedDRA:10040664",
      "NCIT:C85016",
      "Orphanet:54028",
      "SCTID:80126007",
      "UMLS:C0032249",
      "icd11.foundation:1568337509"
    ],
    "synonyms": [
      "Kelly-Paterson syndrome",
      "Sideropenic dysphagia",
      "Kelly's syndrome",
      "Paterson's syndrome",
      "Paterson-Brown-Kelly syndrome",
      "Paterson-Kelly syndrome",
      "Paterson’s syndrome",
      "Plummer Vinson syndrome",
      "dysphagia sideropenica"
    ],
    "categories": [
      {
        "ref": "MONDO:0002254",
        "name": "syndromic disease"
      },
      {
        "ref": "MONDO:0005570",
        "name": "hematologic disorder"
      }
    ],
    "definition": "Plummer-Vinson or Paterson-Kelly syndrome presents as a classical triad of dysphagia, iron-deficiency anemia and esophageal webs."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4370,
      "label": "syndromic disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        29379
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:225",
          "MEDGEN:11688",
          "MESH:D013577",
          "NCIT:C28193",
          "OGMS:0000086",
          "UMLS:C0039082"
        ],
        "synonyms": [
          "cluster, symptom",
          "clusters, symptom",
          "symptom cluster",
          "symptom clusters",
          "syndrome",
          "syndrome associated with disease or disorder",
          "syndromes",
          "syndromic disease",
          "syndromic disease or disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0002254",
            "name": "syndromic disease"
          }
        ],
        "definition": "A group of signs, symptoms, and clinicopathological characteristics that may or may not have a genetic basis and collectively define an abnormal condition."
      },
      "child_count": 1182,
      "reference_id": "MONDO:0002254"
    },
    {
      "id": 17108,
      "label": "acquired deficiency anemia",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        3835
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:1842907",
          "Orphanet:248302",
          "UMLS:C5680693"
        ],
        "synonyms": [
          "rare acquired deficiency anaemia",
          "rare acquired deficiency anemia"
        ],
        "categories": [
          {
            "ref": "MONDO:0005570",
            "name": "hematologic disorder"
          }
        ],
        "definition": "An instance of deficiency anemia that is acquired during the lifetime of the individual."
      },
      "child_count": 1,
      "reference_id": "MONDO:0016625"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4370,
      "label": "syndromic disease"
    },
    {
      "id": 17108,
      "label": "acquired deficiency anemia"
    }
  ]
}