{
  "id": 18893,
  "label": "paraneoplastic pemphigus",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0018974",
  "properties": {
    "xrefs": [
      "DOID:0080852",
      "EFO:0008602",
      "GARD:0018858",
      "ICD10CM:L10.81",
      "MEDGEN:798302",
      "MedDRA:10057056",
      "NANDO:1200231",
      "Orphanet:63455",
      "UMLS:C1112570",
      "icd11.foundation:104197957"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0002254",
        "name": "syndromic disease"
      },
      {
        "ref": "MONDO:0005046",
        "name": "immune system disorder"
      }
    ],
    "definition": "Pemphigus is a group of chronic autoimmune skin diseases characterized by blisters formation on the outer layer of the skin and the mucous membranes. Three clinical forms have been characterized, of which paraneoplastic pemphigus is extremely rare."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 19177,
      "label": "autoimmune bullous skin disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4496,
        8092,
        8586
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8502",
          "EFO:0008598",
          "GARD:0019028",
          "ICD9:694.8",
          "ICD9:694.9",
          "MEDGEN:1842418",
          "Orphanet:79669",
          "SCTID:7231009",
          "UMLS:C5681494"
        ],
        "synonyms": [
          "bullous skin disease",
          "bullous dermatosis"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          }
        ],
        "definition": "An autoimmune disease characterized by blisters on the skin."
      },
      "child_count": 33,
      "reference_id": "MONDO:0019337"
    },
    {
      "id": 24661,
      "label": "paraneoplastic cutaneous syndrome",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4198,
        20314
      ],
      "type_id": 0,
      "properties": {
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0002254",
            "name": "syndromic disease"
          }
        ],
        "definition": "Paraneoplastic syndrome that involves the integumental system."
      },
      "child_count": 2,
      "reference_id": "MONDO:0700266"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 19177,
      "label": "autoimmune bullous skin disease"
    },
    {
      "id": 24661,
      "label": "paraneoplastic cutaneous syndrome"
    }
  ]
}