{
  "id": 19045,
  "label": "polyarteritis nodosa",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0019170",
  "properties": {
    "xrefs": [
      "DOID:9810",
      "GARD:0007360",
      "ICD10CM:M30.0",
      "ICD9:446.0",
      "MEDGEN:14681",
      "MESH:D010488",
      "MedDRA:10036024",
      "NANDO:1200261",
      "NANDO:2200425",
      "NCIT:C26847",
      "NORD:1588",
      "Orphanet:767",
      "SCTID:155441006",
      "UMLS:C0031036",
      "icd11.foundation:1419332129"
    ],
    "synonyms": [
      "Küssmaul-Maier disease",
      "PAN",
      "classic polyarteritis nodosa",
      "classical polyarteritis nodosa",
      "panarteritis nodosa",
      "periarteritis nodosa",
      "polyarteritis nodosa",
      "periarteritis",
      "polyarteritis"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "Polyarteritis nodosa (PAN) is a rare, clinically heterogeneous, rheumatologic disease characterized by necrotizing inflammatory lesions affecting small- and medium-sized blood vessels. PAN most commonly affects skin, joints, peripheral nerves, the gut, and the kidney."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 2,
  "parents": [
    {
      "id": 23218,
      "label": "arteritis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        2933,
        18813
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:0009011",
          "HP:0012089",
          "MEDGEN:13916",
          "MESH:D001167",
          "NCIT:C34399",
          "SCTID:52089001",
          "UMLS:C0003860"
        ],
        "synonyms": [
          "arteritis",
          "artery inflammation",
          "inflammation of artery",
          "Arteritides",
          "Inflammation, arterial",
          "arterial Inflammation"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "An inflammatory process affecting an artery."
      },
      "child_count": 14,
      "reference_id": "MONDO:0043494"
    }
  ],
  "children": [
    {
      "id": 18596,
      "label": "primary polyarteritis nodosa",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        19045
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021830",
          "MEDGEN:1842954",
          "Orphanet:439737",
          "UMLS:C5680052"
        ],
        "synonyms": [
          "primary PAN",
          "primary periarteritis nodosa"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ]
      },
      "child_count": 3,
      "reference_id": "MONDO:0018593"
    },
    {
      "id": 18597,
      "label": "secondary polyarteritis nodosa",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19045
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021831",
          "MEDGEN:1843373",
          "Orphanet:439746",
          "UMLS:C5680050"
        ],
        "synonyms": [
          "Secondary PAN",
          "secondary PAN",
          "secondary periarteritis nodosa"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV)."
      },
      "child_count": 0,
      "reference_id": "MONDO:0018594"
    }
  ],
  "roots": [
    {
      "id": 23218,
      "label": "arteritis"
    }
  ]
}