{
  "id": 19328,
  "label": "hepatic veno-occlusive disease",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0019514",
  "properties": {
    "xrefs": [
      "DOID:0080177",
      "GARD:0013004",
      "ICD10CM:K76.5",
      "ICD9:453.89",
      "MEDGEN:5514",
      "MESH:D006504",
      "MedDRA:10047216",
      "NCIT:C26793",
      "NORD:879",
      "Orphanet:890",
      "SCTID:65617004",
      "UMLS:C0019156",
      "icd11.foundation:762044088",
      "icd11.foundation:901464792"
    ],
    "synonyms": [
      "Budd Chiari Syndrome",
      "hepatic Vod",
      "liver veno-occlusive disease",
      "sinusoidal obstruction syndrome",
      "veno-occlusive disease"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "Hepatic veno-occlusive disease (hepatic VOD) is a condition resulting from toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 4495,
      "label": "hepatic vascular disorder",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6878,
        7065
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:272",
          "ICD9:573.8",
          "MEDGEN:140779",
          "NCIT:C35442",
          "SCTID:235878005",
          "UMLS:C0400923"
        ],
        "synonyms": [
          "hepatic vascular disorder",
          "liver vascular disorder"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A non-neoplastic or neoplastic vascular disorder that affects the liver. Representative examples include veno-occlusive disease, hemangioma, lymphangioma, and angiosarcoma."
      },
      "child_count": 22,
      "reference_id": "MONDO:0002405"
    }
  ],
  "children": [
    {
      "id": 10570,
      "label": "hepatic veno-occlusive disease-immunodeficiency syndrome",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        5658,
        5714,
        19328
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0112254",
          "GARD:0010083",
          "MEDGEN:344659",
          "MESH:C537257",
          "NANDO:1200341",
          "NANDO:2200714",
          "OMIM:235550",
          "Orphanet:79124",
          "SCTID:724361001",
          "UMLS:C1856128",
          "icd11.foundation:712514250"
        ],
        "synonyms": [
          "VODI syndrome",
          "VODI",
          "familial veno-occlusive disease with immunodeficiency",
          "hepatic veno-occlusive disease with immunodeficiency",
          "hepatic venoocclusive disease with immunodeficiency",
          "veno-occlusive disease and immunodeficiency syndrome"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005046",
            "name": "immune system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "Hepatic veno-occlusive disease-immunodeficiency syndrome is characterized by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centers, absent tissue plasma cells and hepatic veno-occlusive disease."
      },
      "child_count": 0,
      "reference_id": "MONDO:0009338"
    }
  ],
  "roots": [
    {
      "id": 4495,
      "label": "hepatic vascular disorder"
    }
  ]
}