{
  "id": 20286,
  "label": "pleural solitary fibrous tumor",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0021041",
  "properties": {
    "xrefs": [
      "GARD:0025278",
      "NCIT:C4457",
      "SCTID:254646001"
    ],
    "synonyms": [
      "fibroma of pleura",
      "fibroma of the pleura",
      "localised fibrous mesothelioma of pleura",
      "localised fibrous mesothelioma of the pleura",
      "localized fibrous mesothelioma of pleura",
      "localized fibrous mesothelioma of the pleura",
      "pleura solitary fibrous tumor",
      "pleura solitary fibrous tumour",
      "pleural Submesothelial fibroma",
      "pleural cavity solitary fibrous tumor",
      "pleural cavity solitary fibrous tumour",
      "pleural fibroma",
      "pleural solitary fibrous tumor",
      "solitary fibrous tumor of pleura",
      "solitary fibrous tumor of the pleura",
      "solitary fibrous tumour of pleura",
      "solitary fibrous tumour of the pleura"
    ],
    "categories": [
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      },
      {
        "ref": "MONDO:0005087",
        "name": "respiratory system disorder"
      }
    ],
    "definition": "A localized neoplasm of probable fibroblastic derivation, that arises from the pleura. It is characterized by the presence of round to spindle-shaped cells, hylanized stroma formation, thin-walled branching blood vessels, and thin bands of collagen."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 16812,
      "label": "solitary fibrous tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7762
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0015014",
          "ICD9:238.1",
          "ICDO:8815/0",
          "ICDO:8815/1",
          "ICDO:9051/0",
          "MEDGEN:224764",
          "MESH:D054364",
          "MedDRA:10018825",
          "NCIT:C7634",
          "ONCOTREE:SFT",
          "Orphanet:2126",
          "UMLS:C1266119"
        ],
        "synonyms": [
          "SFT",
          "localised fibrous mesothelioma",
          "localised fibrous tumour",
          "localized fibrous mesothelioma",
          "localized fibrous tumor",
          "solitary fibrous tumor",
          "submesothelial fibroma",
          "hemangiopericytoma",
          "solitary fibrous tumor/hemangiopericytoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "Solitary fibrous tumor (SFT) represents a diverse group of ubiquitous rare spindle cell neoplasms that may be benign or malignant and that most frequently arises from the pleura and peritoneum and rarely from other sites such as head and neck, liver and skeletal muscle. SFT may be clinically asymptomatic or may present with enlarging mass, compressive effects depending on the site involved and rarely with paraneoplastic manifestations (osteoarthropathy or hypoglycemia)."
      },
      "child_count": 5,
      "reference_id": "MONDO:0016238"
    },
    {
      "id": 20306,
      "label": "pleural neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4184,
        20056
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:18523",
          "MESH:D010997",
          "NCIT:C3332",
          "ONCOTREE:PLEURA",
          "SCTID:126719004",
          "UMLS:C0032229"
        ],
        "synonyms": [
          "neoplasm of pleura",
          "neoplasm of pleural cavity",
          "neoplasm of the pleura",
          "pleura neoplasm",
          "pleura neoplasm (disease)",
          "pleura tumor",
          "pleura tumour",
          "pleural cavity neoplasm (disease)",
          "pleural cavity tumor",
          "pleural cavity tumour",
          "pleural neoplasm",
          "pleural tumor",
          "pleural tumour",
          "tumor of pleura",
          "tumor of the pleura",
          "tumour of pleura",
          "tumour of the pleura"
        ],
        "categories": [
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          }
        ],
        "definition": "A benign or malignant neoplasm that involves the serous membrane that lines the lungs and thoracic cavity. Most pleural neoplasms are metastatic. Diffuse malignant mesothelioma is the most common primary malignant neoplasm of the pleura."
      },
      "child_count": 10,
      "reference_id": "MONDO:0021065"
    }
  ],
  "children": [
    {
      "id": 2896,
      "label": "malignant pleural solitary fibrous tumor",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        7835,
        20286
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0050695",
          "GARD:0022766",
          "MEDGEN:1876517",
          "UMLS:C5985025"
        ],
        "synonyms": [
          "pleural solitary fibrous tumor, malignant"
        ],
        "categories": [
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          },
          {
            "ref": "MONDO:0005087",
            "name": "respiratory system disorder"
          }
        ],
        "definition": "A malignant form of pleural solitary fibrous tumor."
      },
      "child_count": 0,
      "reference_id": "MONDO:0000407"
    }
  ],
  "roots": [
    {
      "id": 16812,
      "label": "solitary fibrous tumor"
    },
    {
      "id": 20306,
      "label": "pleural neoplasm"
    }
  ]
}