{
  "id": 20360,
  "label": "hemangioendothelioma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0021121",
  "properties": {
    "xrefs": [
      "ICDO:9130/1",
      "MEDGEN:42384",
      "MESH:D006390",
      "NCIT:C3084",
      "SCTID:403980002",
      "UMLS:C0018915"
    ],
    "synonyms": [
      "angioendothelioma",
      "hemangioendothelioma"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "A vascular proliferation characterized by the presence of prominent endothelial cells and the formation of vascular channels. Hemangioendotheliomas may display borderline or low grade characteristics."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 5,
  "parents": [
    {
      "id": 20321,
      "label": "blood vessel neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7065,
        21330
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:1651181",
          "NCIT:C7387",
          "SCTID:126736007",
          "UMLS:C4722524"
        ],
        "synonyms": [
          "blood vessel neoplasm",
          "blood vessel neoplasm (disease)",
          "blood vessel tumor",
          "blood vessel tumour",
          "neoplasm of blood vessel",
          "tumor of blood vessel",
          "tumour of blood vessel"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A neoplasm arising from arteries or veins."
      },
      "child_count": 10,
      "reference_id": "MONDO:0021080"
    }
  ],
  "children": [
    {
      "id": 16338,
      "label": "epithelioid hemangioendothelioma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        4233,
        20360
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:0080190",
          "GARD:0020014",
          "ICDO:9130/3",
          "ICDO:9133/1",
          "ICDO:9133/3",
          "MEDGEN:569676",
          "MESH:D018323",
          "NCIT:C3800",
          "NORD:124536",
          "ONCOTREE:EHAE",
          "Orphanet:157791",
          "SCTID:403981003",
          "SCTID:54124005",
          "UMLS:C0334538"
        ],
        "synonyms": [
          "epithelioid angioendothelioma",
          "epithelioid angiosarcoma",
          "epithelioid hemangioendothelioma",
          "malignant epithelioid hemangioendothelioma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A low-grade malignant blood vessel neoplasm. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma."
      },
      "child_count": 0,
      "reference_id": "MONDO:0015523"
    },
    {
      "id": 16810,
      "label": "kaposiform hemangioendothelioma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        7941,
        20360
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0003077",
          "MEDGEN:234548",
          "MESH:C537007",
          "NCIT:C27510",
          "Orphanet:2122",
          "SCTID:403983000",
          "UMLS:C1367420"
        ],
        "synonyms": [
          "Kaposiform hemangioendothelioma",
          "KH",
          "KHE",
          "Kaposiform hemangio-endothelioma",
          "congenital cutaneous multifocal kaposiform hemangioendothelioma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Kaposiform hemangioendothelioma is a very rare, aggressive, vascular tumor manifesting in the neonatal period or in infancy as cutaneous vascular tumors to large infiltrative lesions."
      },
      "child_count": 0,
      "reference_id": "MONDO:0016236"
    },
    {
      "id": 18695,
      "label": "composite hemangioendothelioma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        20360
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021907",
          "MEDGEN:220987",
          "NCIT:C45475",
          "Orphanet:458758",
          "SCTID:403984006",
          "UMLS:C1304513"
        ],
        "synonyms": [
          "composite hemangioendothelioma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "An intermediate, locally aggressive and rarely metastasizing blood vessel neoplasm. It is characterized by the presence of spindle, plump, and epithelioid endothelial cells and cellular atypia."
      },
      "child_count": 0,
      "reference_id": "MONDO:0018712"
    },
    {
      "id": 18696,
      "label": "retiform hemangioendothelioma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        20360
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021908",
          "MEDGEN:266274",
          "NCIT:C27511",
          "Orphanet:458763",
          "SCTID:403982005",
          "UMLS:C1304512"
        ],
        "synonyms": [
          "hobnail hemangioendothelioma",
          "retiform hemangioendothelioma"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "An intermediate, locally aggressive and rarely metastasizing blood vessel neoplasm. It is characterized by the presence of hobnail endothelial cells and formation of arborizing vascular channels."
      },
      "child_count": 0,
      "reference_id": "MONDO:0018713"
    },
    {
      "id": 18697,
      "label": "primary intralymphatic angioendothelioma",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        20360
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0021909",
          "ICDO:9135/1",
          "MEDGEN:138037",
          "NCIT:C7526",
          "Orphanet:458768",
          "UMLS:C0346087",
          "icd11.foundation:432094068"
        ],
        "synonyms": [
          "Dabska tumor",
          "Dabska tumour",
          "PILA",
          "malignant endothelial papillary angioendothelioma",
          "papillary Endovascular angioendothelioma",
          "papillary intralymphatic angioendothelioma",
          "pila"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "An intermediate, rarely metastasizing blood vessel neoplasm. It is characterized by the presence of lymphatic-like vascular channels and papillary endothelial proliferation."
      },
      "child_count": 0,
      "reference_id": "MONDO:0018714"
    }
  ],
  "roots": [
    {
      "id": 20321,
      "label": "blood vessel neoplasm"
    }
  ]
}