{
  "id": 20921,
  "label": "childhood carcinoid tumor",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0022642",
  "properties": {
    "xrefs": [
      "GARD:0009315",
      "MEDGEN:859267",
      "NCIT:C118810",
      "UMLS:C3899673"
    ],
    "synonyms": [
      "carcinoid tumor (disease) of childhood",
      "carcinoid tumour (disease) of childhood",
      "childhood carcinoid tumor",
      "childhood carcinoid tumor (disease)",
      "childhood carcinoid tumour (disease)",
      "paediatric carcinoid tumour (disease)",
      "pediatric carcinoid tumor (disease)",
      "carcinoid tumor childhood",
      "carcinoid tumour childhood"
    ],
    "categories": [
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "A rare carcinoid tumor that occurs during childhood."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 7051,
      "label": "carcinoid tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        19314
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "EFO:0004243",
          "GARD:0024176",
          "HP:0100570",
          "ICD9:209.60",
          "ICDO:8240/3",
          "ICDO:8241/3",
          "MEDGEN:2838",
          "MESH:D002276",
          "NANDO:2200396",
          "NCIT:C2915",
          "SCTID:443492008",
          "UMLS:C0007095"
        ],
        "synonyms": [
          "NET G1",
          "carcinoid",
          "carcinoid tumor",
          "carcinoid tumor (disease)",
          "carcinoid tumour (disease)",
          "neuroendocrine neoplasm G1",
          "neuroendocrine tumor G1",
          "neuroendocrine tumour G1"
        ],
        "categories": [
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A slow growing neuroendocrine tumor, composed of uniform, round, or polygonal cells having monotonous, centrally located nuclei and small nucleoli, infrequent mitoses, and no necrosis. The tumor may show a variety of patterns, such as solid, trabecular, and acinar. Electron microscopy shows small secretory granules. Immunohistochemical studies reveal NSE, as well as chromogranin immunoreactivity. Malignant histology (cellular pleomorphism, hyperchromatic nuclei, prominent nucleoli, necrosis, and mitoses) can occasionally be seen. Such cases may have an aggressive clinical course. Gastrointestinal tract and lung are common sites of involvement."
      },
      "child_count": 7,
      "reference_id": "MONDO:0005369"
    },
    {
      "id": 20320,
      "label": "childhood neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6798
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "MEDGEN:237153",
          "NCIT:C6283",
          "UMLS:C1368871"
        ],
        "synonyms": [
          "childhood neoplasm",
          "childhood neoplasm (disease)",
          "childhood tumor",
          "childhood tumour",
          "neoplasm (disease) of childhood",
          "paediatric neoplasm",
          "paediatric neoplasm (disease)",
          "paediatric tumour",
          "pediatric neoplasm",
          "pediatric neoplasm (disease)",
          "pediatric tumor"
        ],
        "definition": "A benign or malignant neoplasm arising during childhood."
      },
      "child_count": 14,
      "reference_id": "MONDO:0021079"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 7051,
      "label": "carcinoid tumor"
    },
    {
      "id": 20320,
      "label": "childhood neoplasm"
    }
  ]
}