{
  "id": 21300,
  "label": "acute lichenoid pityriasis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0024250",
  "properties": {
    "xrefs": [
      "GARD:0009768",
      "ICD9:696.5",
      "MEDGEN:57997",
      "SCTID:86487001",
      "UMLS:C0162852"
    ],
    "synonyms": [
      "Habermann disease",
      "Habermann's disease",
      "Habermanns disease",
      "Mucha Habermann disease",
      "Mucha-Habermann disease",
      "PLEVA",
      "disease, Habermann",
      "disease, Habermann's",
      "disease, Mucha-Habermann",
      "mucha habermann disease",
      "mucha-habermann disease",
      "mucha-habermann syndrome",
      "parapsoriasis lichenoides et varioliformis acuta",
      "parapsoriasis varioliformis acuta"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ]
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 20092,
      "label": "acute disease",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        24492
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "ICD9:799.89",
          "MEDGEN:1738",
          "MESH:D000208",
          "SCTID:2704003",
          "UMLS:C0001314"
        ],
        "synonyms": [
          "acute disease",
          "acute diseases",
          "disease, acute"
        ],
        "definition": "Disease having a short and relatively severe course."
      },
      "child_count": 119,
      "reference_id": "MONDO:0020683"
    },
    {
      "id": 21299,
      "label": "pityriasis lichenoides",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        8030,
        8068,
        19142
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0010265",
          "MEDGEN:102482",
          "MESH:D017514",
          "NCIT:C85013",
          "SCTID:200983001",
          "UMLS:C0162853",
          "icd11.foundation:266281219"
        ],
        "synonyms": [
          "Pityriasis Lichenoides",
          "pityriasis lichenoides",
          "acute Pityriasis Lichenoides",
          "chronic Pityriasis Lichenoides",
          "Pityriasis Lichenoides chronica",
          "Pityriasis Lichenoides et Varioliformis Acuta",
          "Pityriasis Lichenoides, acute",
          "Pityriasis Lichenoides, chronic"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A rare cutaneous disorder of unknown etiology that can present either as an acute condition, with multiple papular lesions which become vesicular and necrotic (pityriasis lichenoides et varioliformis acuta) or chronic, with small, scaling papules (pityriasis lichenoides chronica)."
      },
      "child_count": 3,
      "reference_id": "MONDO:0024249"
    }
  ],
  "children": [
    {
      "id": 21146,
      "label": "febrile ulceronecrotic Mucha-Habermann disease",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        21300
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0009516",
          "MEDGEN:266145",
          "MESH:C537077",
          "SCTID:402860008",
          "UMLS:C1274297",
          "icd11.foundation:1408299147"
        ],
        "synonyms": [
          "febrile ulceronecrotic Mucha-Habermann disease",
          "febrile ulceronecrotic pityriasis lichenoides acuta",
          "A severe variant of pityriasis lichenoides et varioliformis acuta (PLEVA)",
          "FUMHD",
          "ulceronecrotic Mucha-Habermann disease",
          "variant of Mucha-Habermann disease"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe form of pityriasis lichenoides et varioliformis acuta (PLEVA). PLEVA is characterized by skin lesions that ulcerate, breakdown, form open sores, then form a red-brown crust. FUMHD often begins as PLEVA, but then rapidly and suddenly progresses to large, destructive ulcers. There may be fever and extensive, painful loss of skin tissue as well as secondary infection of the ulcers. Diagnosis of FUMHD is confirmed by biopsy of skin lesions. FUMHD occurs more frequently in children, peaking at age 5 to 10. Males tend to be affected more often than females. While some cases of FUMHD have resolved without therapy, others have resulted in death. Early diagnosis and prompt treatment may help to reduce morbidity and death."
      },
      "child_count": 0,
      "reference_id": "MONDO:0023134"
    }
  ],
  "roots": [
    {
      "id": 20092,
      "label": "acute disease"
    },
    {
      "id": 21299,
      "label": "pityriasis lichenoides"
    }
  ]
}