{
  "id": 22814,
  "label": "bullous pyoderma gangrenosum",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0035237",
  "properties": {
    "xrefs": [
      "GARD:0022222",
      "MEDGEN:590609",
      "Orphanet:538869",
      "UMLS:C0406687"
    ],
    "synonyms": [
      "Phemphigoid pyoderma gangrenosum"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0002254",
        "name": "syndromic disease"
      },
      {
        "ref": "MONDO:0003900",
        "name": "connective tissue disorder"
      }
    ],
    "definition": "A rare subtype of pyoderma gangrenosum disease characterized by grouped vesicles that rapidly spread and coalesce to form large bullae, which evolve into ulcerations that have an erythematous peripheral halo and central necrosis, mainly affecting the upper limbs and face. Lymphoproliferative diseases are frequently associated, thus prognosis is often compromised."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 18765,
      "label": "pyoderma gangrenosum",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4929,
        19503
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:8553",
          "GARD:0007510",
          "ICD10CM:L88",
          "ICD10WHO:L88",
          "ICD9:686.01",
          "MEDGEN:43224",
          "MESH:D017511",
          "MedDRA:10037635",
          "NANDO:2200437",
          "NORD:1638",
          "Orphanet:48104",
          "SCTID:74578003",
          "UMLS:C0085652",
          "icd11.foundation:2120746218"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0002254",
            "name": "syndromic disease"
          },
          {
            "ref": "MONDO:0003900",
            "name": "connective tissue disorder"
          }
        ],
        "definition": "Pyoderma gangrenosum (PG) is a primarily sterile inflammatory neutrophilic dermatosis characterized by recurrent cutaneous ulcerations with a mucopurulent or hemorrhagic exudate."
      },
      "child_count": 8,
      "reference_id": "MONDO:0018824"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 18765,
      "label": "pyoderma gangrenosum"
    }
  ]
}