{
  "id": 23440,
  "label": "solid pseudopapillary neoplasm of the pancreas",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0044786",
  "properties": {
    "xrefs": [
      "GARD:0027975",
      "MEDGEN:234800",
      "NCIT:C37212",
      "ONCOTREE:SPN",
      "UMLS:C1336030"
    ],
    "synonyms": [
      "Frantz tumor",
      "Frantz tumour",
      "solid pseudopapillary neoplasm of the pancreas",
      "solid pseudopapillary tumor of the pancreas",
      "solid pseudopapillary tumour of the pancreas"
    ],
    "categories": [
      {
        "ref": "MONDO:0004335",
        "name": "digestive system disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "A low-grade malignant neoplasm that arises from the exocrine pancreas. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. Perineural invasion, vascular invasion, and invasion into surrounding tissues may be present. It usually presents as an encapsulated, solitary, and lobulated pancreatic mass. It is usually found incidentally during physical examination or it may present with abdominal discomfort and pain. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 4251,
      "label": "malignant exocrine pancreas neoplasm",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        11035,
        20317
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:1795",
          "GARD:0027598",
          "MEDGEN:91108",
          "NCIT:C7430",
          "SCTID:255088001",
          "UMLS:C0346648"
        ],
        "synonyms": [
          "pancreatic exocrine tumor",
          "pancreatic exocrine tumour",
          "cancer of exocrine pancreas",
          "exocrine pancreas cancer",
          "malignant exocrine pancreas neoplasm",
          "malignant exocrine pancreas tumor",
          "malignant exocrine pancreas tumour",
          "malignant neoplasm of exocrine pancreas",
          "malignant neoplasm of the exocrine pancreas",
          "malignant tumor of exocrine pancreas",
          "malignant tumor of the exocrine pancreas",
          "malignant tumour of the exocrine pancreas",
          "tumor of exocrine pancreas",
          "tumour of exocrine pancreas"
        ],
        "categories": [
          {
            "ref": "MONDO:0004335",
            "name": "digestive system disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A malignant neoplasm that arises from the epithelial cells of the exocrine pancreatic tissue."
      },
      "child_count": 8,
      "reference_id": "MONDO:0002116"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 4251,
      "label": "malignant exocrine pancreas neoplasm"
    }
  ]
}