{
  "id": 23986,
  "label": "rapidly progressive primary central nervous system vasculitis",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0100248",
  "properties": {
    "xrefs": [
      "GARD:0026097"
    ],
    "synonyms": [
      "rapidly progressive PCNSV"
    ],
    "categories": [
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "A subset of primary central nervous system vasculitis where disease is rapidly progressive after onset that is characterized by bilateral, multiple, large cerebral vessel lesions and multiple CNS infarctions."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 16228,
      "label": "primary central nervous system vasculitis",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        5281
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0008703",
          "MEDGEN:419271",
          "MESH:C537295",
          "Orphanet:140989",
          "UMLS:C2930862",
          "icd11.foundation:2130738127"
        ],
        "synonyms": [
          "PACNS",
          "PCNSV",
          "isolated angiitis of the central nervous system",
          "primary angiitis of the central nervous system",
          "primary central nervous system vasculitis",
          "primary vasculitis of the central nervous system",
          "granulomatous angiitis of the central nervous system",
          "primary CNS vasculitis"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ]
      },
      "child_count": 1,
      "reference_id": "MONDO:0015374"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 16228,
      "label": "primary central nervous system vasculitis"
    }
  ]
}