[
  {
    "phenotype_id": "PH1870",
    "phenotype_version_id": 4422,
    "name": "Vasculitis",
    "definition": "This phenotype also used EPCC codes in its definition. These can be found at: [https://github.com/BHFDSC/CCU072_01/blob/main/phenotypes/ccu072_01_dcode_epcc_name_suppltable.csv](https://github.com/BHFDSC/CCU072_01/blob/main/phenotypes/ccu072_01_dcode_epcc_name_suppltable.csv)\n",
    "implementation": "",
    "publications": [
      {
        "doi": "10.2139/ssrn.5203816",
        "details": "Allara E, et al. Burden of cardiovascular diseases from the COVID-19 pandemic to 2024: a national cohort in NHS England. The Lancet.",
        "primary": 1
      }
    ],
    "validation": "",
    "citation_requirements": "",
    "created": "2025-06-10T13:52:21.058311Z",
    "author": "Elias Allara, Wen Shi, Thomas Bolton, Fionna Chalmers, Luigi Filippo Brizzi, Liam Musto, Anoop S.V. Shah, Christopher Tomlinson, Isabel Walter, Nathalie Conrad, John Danesh, Emanuele Di Angelantonio, Steffen E. Petersen, Kamlesh Khunti, Elena Raffetti, Genevieve Cezard, Spiros Denaxas, Angela M. Wood, William N. Whiteley",
    "collections": [
      {
        "name": "BHF Data Science Centre",
        "value": 20
      },
      {
        "name": "Phenotype Library",
        "value": 18
      }
    ],
    "tags": null,
    "organisation": {
      "id": 13,
      "slug": "bhf-data-science-centre",
      "name": "BHF Data Science Centre"
    },
    "world_access": 2,
    "updated": "2025-06-10T14:46:28.385737Z",
    "sex": [
      {
        "name": "Both",
        "value": "3"
      }
    ],
    "type": [
      {
        "name": "Disease or syndrome",
        "value": "2"
      }
    ],
    "trials": [],
    "ontology": null,
    "phenoflowid": "",
    "data_sources": null,
    "endorsements": [],
    "project_name": "CCU072_01",
    "coding_system": [
      {
        "name": "SNOMED  CT codes",
        "value": 9
      },
      {
        "name": "ICD10 codes",
        "value": 4
      }
    ],
    "corresp_author": "Elias Allara",
    "event_date_range": "",
    "concept_information": [
      {
        "concept_id": 4495,
        "concept_version_id": 11856,
        "concept_name": "Vasculitis",
        "coding_system": {
          "id": 4,
          "name": "ICD10 codes",
          "description": "ICD10 Codes"
        },
        "phenotype_id": "PH1870",
        "phenotype_version_id": 4422,
        "phenotype_name": "Vasculitis",
        "code_attribute_header": null,
        "codes": [
          {
            "code": "I677",
            "description": "Cerebral arteritis, not elsewhere classified",
            "attributes": null
          },
          {
            "code": "I731",
            "description": "Thromboangiitis obliterans Buerger",
            "attributes": null
          },
          {
            "code": "I776",
            "description": "Arteritis, unspecified",
            "attributes": null
          },
          {
            "code": "M300",
            "description": "Polyarteritis nodosa",
            "attributes": null
          },
          {
            "code": "M301",
            "description": "Polyarteritis with lung involvement Churg-Strauss",
            "attributes": null
          },
          {
            "code": "M302",
            "description": "Juvenile polyarteritis",
            "attributes": null
          },
          {
            "code": "M303",
            "description": "Mucocutaneous lymph node syndrome Kawasaki",
            "attributes": null
          },
          {
            "code": "M308",
            "description": "Other conditions related to polyarteritis nodosa",
            "attributes": null
          },
          {
            "code": "M310",
            "description": "Hypersensitivity angiitis",
            "attributes": null
          },
          {
            "code": "M311",
            "description": "Thrombotic microangiopathy",
            "attributes": null
          },
          {
            "code": "M312",
            "description": "Lethal midline granuloma",
            "attributes": null
          },
          {
            "code": "M313",
            "description": "Wegener granulomatosis",
            "attributes": null
          },
          {
            "code": "M314",
            "description": "Aortic arch syndrome Takayasu",
            "attributes": null
          },
          {
            "code": "M315",
            "description": "Giant cell arteritis with polymyalgia rheumatica",
            "attributes": null
          },
          {
            "code": "M316",
            "description": "Other giant cell arteritis",
            "attributes": null
          },
          {
            "code": "M317",
            "description": "Microscopic polyangiitis",
            "attributes": null
          }
        ]
      },
      {
        "concept_id": 4496,
        "concept_version_id": 11857,
        "concept_name": "Vasculitis",
        "coding_system": {
          "id": 9,
          "name": "SNOMED  CT codes",
          "description": "SNOMED CT codes"
        },
        "phenotype_id": "PH1870",
        "phenotype_version_id": 4422,
        "phenotype_name": "Vasculitis",
        "code_attribute_header": null,
        "codes": [
          {
            "code": "101711000119105",
            "description": "Glomerulonephritis co-occurrent and due to antineutrophil cytoplasmic antibody positive vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "111199007",
            "description": "Purpura pigmentosa chronica (disorder)",
            "attributes": null
          },
          {
            "code": "111291001",
            "description": "Senile endarteritis (disorder)",
            "attributes": null
          },
          {
            "code": "11255009",
            "description": "Retinal arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "1142107003",
            "description": "Transient neonatal Behçet disease (disorder)",
            "attributes": null
          },
          {
            "code": "1144805008",
            "description": "Microscopic polyangiitis (disorder)",
            "attributes": null
          },
          {
            "code": "1144809002",
            "description": "Disorder of respiratory system due to microscopic polyangiitis (disorder)",
            "attributes": null
          },
          {
            "code": "1144912000",
            "description": "Chronic thrombotic microangiopathy (disorder)",
            "attributes": null
          },
          {
            "code": "1144914004",
            "description": "Behcet disease of skin (disorder)",
            "attributes": null
          },
          {
            "code": "1144919009",
            "description": "Behcet disease of eye (disorder)",
            "attributes": null
          },
          {
            "code": "1144932004",
            "description": "Immune complex small vessel vasculitis due to infectious disease (disorder)",
            "attributes": null
          },
          {
            "code": "1144950006",
            "description": "Vasculitis due to Sjögren syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "1144953008",
            "description": "Vasculitis due to malignant neoplastic disease (disorder)",
            "attributes": null
          },
          {
            "code": "1144955001",
            "description": "Vasculitis due to myeloproliferative disorder (disorder)",
            "attributes": null
          },
          {
            "code": "1144956000",
            "description": "Vasculitis due to inflammatory bowel disease (disorder)",
            "attributes": null
          },
          {
            "code": "1144957009",
            "description": "Vasculitis due to lymphoproliferative disorder (disorder)",
            "attributes": null
          },
          {
            "code": "1144964006",
            "description": "Acute intravascular thrombotic microangiopathy (disorder)",
            "attributes": null
          },
          {
            "code": "1149218009",
            "description": "Rheumatoid arthritis with isolated nailfold vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "1149219001",
            "description": "Rheumatoid arthritis with systemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "1155919006",
            "description": "Acute rheumatic fever with aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "1177015003",
            "description": "Cerebral arteritis caused by Mycobacterium tuberculosis complex (disorder)",
            "attributes": null
          },
          {
            "code": "11791001",
            "description": "Necrotizing vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "1187508009",
            "description": "Immunoglobulin G4 related aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "1197742004",
            "description": "Behçet disease of small intestine (disorder)",
            "attributes": null
          },
          {
            "code": "1222546002",
            "description": "Perivasculitis of retina of eye (disorder)",
            "attributes": null
          },
          {
            "code": "1230397006",
            "description": "Pigmented purpuric dermatosis (disorder)",
            "attributes": null
          },
          {
            "code": "1231140009",
            "description": "Lemierre syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "1231671001",
            "description": "Granulomatosis with polyangiitis of orbit (disorder)",
            "attributes": null
          },
          {
            "code": "1260127003",
            "description": "Granulomatous vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "1264001009",
            "description": "De novo thrombotic microangiopathy following transplant of kidney (disorder)",
            "attributes": null
          },
          {
            "code": "126729006",
            "description": "Thrombotic microangiopathy (disorder)",
            "attributes": null
          },
          {
            "code": "1268294009",
            "description": "Inflammation of systemic vasculature (disorder)",
            "attributes": null
          },
          {
            "code": "1268295005",
            "description": "Vasculitis due to systemic disease (disorder)",
            "attributes": null
          },
          {
            "code": "155441006",
            "description": "Polyarteritis nodosa (disorder)",
            "attributes": null
          },
          {
            "code": "17993000",
            "description": "Pulmonary arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "186317009",
            "description": "Listerial cerebral arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "190815001",
            "description": "Cryoglobulinemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "191306005",
            "description": "Immunoglobulin A vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "195299000",
            "description": "Presenile gangrene (disorder)",
            "attributes": null
          },
          {
            "code": "195353004",
            "description": "Granulomatosis with polyangiitis (disorder)",
            "attributes": null
          },
          {
            "code": "195363007",
            "description": "Juvenile polyarteritis (disorder)",
            "attributes": null
          },
          {
            "code": "197712008",
            "description": "Chronic nephritic syndrome, diffuse endocapillary proliferative glomerulonephritis (disorder)",
            "attributes": null
          },
          {
            "code": "20258000",
            "description": "Polyarteritis (disorder)",
            "attributes": null
          },
          {
            "code": "20343006",
            "description": "Pigmented purpuric lichenoid dermatitis of Gougerot and Blum (disorder)",
            "attributes": null
          },
          {
            "code": "20735004",
            "description": "Syphilitic aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "21542005",
            "description": "Behcet's syndrome, neurologic type (disorder)",
            "attributes": null
          },
          {
            "code": "230731002",
            "description": "Cerebral arteritis in systemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "230732009",
            "description": "Cerebral arteritis in giant cell arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "230733004",
            "description": "Isolated angiitis of central nervous system (disorder)",
            "attributes": null
          },
          {
            "code": "230734005",
            "description": "Granulomatous angiitis of central nervous system (disorder)",
            "attributes": null
          },
          {
            "code": "230735006",
            "description": "Syphilitic cerebral arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "232369001",
            "description": "Granulomatosis with polyangiitis of nose (disorder)",
            "attributes": null
          },
          {
            "code": "232460001",
            "description": "Granulomatosis with polyangiitis of larynx (disorder)",
            "attributes": null
          },
          {
            "code": "234019004",
            "description": "Secondary systemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "234020005",
            "description": "Vasculitis caused by drug (disorder)",
            "attributes": null
          },
          {
            "code": "235000001",
            "description": "Granulomatosis with polyangiitis of gingiva (disorder)",
            "attributes": null
          },
          {
            "code": "238780006",
            "description": "Idiopathic capillaritis (disorder)",
            "attributes": null
          },
          {
            "code": "238781005",
            "description": "Itching purpura (disorder)",
            "attributes": null
          },
          {
            "code": "238782003",
            "description": "Lichen aureus (disorder)",
            "attributes": null
          },
          {
            "code": "238785001",
            "description": "Primary cutaneous vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "238786000",
            "description": "Gougerot-Ruiter purpura (disorder)",
            "attributes": null
          },
          {
            "code": "238787009",
            "description": "Secondary cutaneous vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239921005",
            "description": "Behcet's disease with organ/system involvement (disorder)",
            "attributes": null
          },
          {
            "code": "239922003",
            "description": "Behcet's disease with multisystem involvement (disorder)",
            "attributes": null
          },
          {
            "code": "239924002",
            "description": "Primary necrotizing systemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239925001",
            "description": "Polyarteritis nodosa with single organ involvement (disorder)",
            "attributes": null
          },
          {
            "code": "239926000",
            "description": "Cutaneous polyarteritis nodosa (disorder)",
            "attributes": null
          },
          {
            "code": "239927009",
            "description": "Polyarteritis nodosa with multi-organ involvement (disorder)",
            "attributes": null
          },
          {
            "code": "239931003",
            "description": "Polyangiitis overlap syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "239935007",
            "description": "Limited granulomatosis with polyangiitis (disorder)",
            "attributes": null
          },
          {
            "code": "239936008",
            "description": "Granulomatosis with polyangiitis with multisystem involvement (disorder)",
            "attributes": null
          },
          {
            "code": "239937004",
            "description": "Idiopathic aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "239938009",
            "description": "Giant cell arteritis with polymyalgia rheumatica (disorder)",
            "attributes": null
          },
          {
            "code": "239939001",
            "description": "Giant cell arteritis without polymyalgia rheumatica (disorder)",
            "attributes": null
          },
          {
            "code": "239943002",
            "description": "Rheumatoid arthritis with necrotizing vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239944008",
            "description": "Lupus vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239945009",
            "description": "Hypocomplementemic urticarial vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239946005",
            "description": "Postinfective immunoglobulin A vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "239947001",
            "description": "Essential mixed cryoglobulinemia (disorder)",
            "attributes": null
          },
          {
            "code": "239948006",
            "description": "Secondary aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "254757003",
            "description": "Extracellular cholesterosis (disorder)",
            "attributes": null
          },
          {
            "code": "257812009",
            "description": "Chronic peri-aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "28366008",
            "description": "Cerebral arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "302728008",
            "description": "Endarteritis deformans (disorder)",
            "attributes": null
          },
          {
            "code": "302930003",
            "description": "Endarteritis obliterans (disorder)",
            "attributes": null
          },
          {
            "code": "310701003",
            "description": "Behcet's syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "312383007",
            "description": "Infective aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "314186008",
            "description": "Inflammatory abdominal aortic aneurysm (disorder)",
            "attributes": null
          },
          {
            "code": "31996006",
            "description": "Vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "3275009",
            "description": "Behcet's syndrome, vascular type (disorder)",
            "attributes": null
          },
          {
            "code": "332421000119101",
            "description": "Retinal vasculitis of right eye (disorder)",
            "attributes": null
          },
          {
            "code": "338031000119109",
            "description": "Retinal vasculitis of left eye (disorder)",
            "attributes": null
          },
          {
            "code": "33806008",
            "description": "Endarteritis (disorder)",
            "attributes": null
          },
          {
            "code": "343801000119100",
            "description": "Retinal vasculitis of bilateral eyes (disorder)",
            "attributes": null
          },
          {
            "code": "359789008",
            "description": "Takayasu's disease (disorder)",
            "attributes": null
          },
          {
            "code": "3704008",
            "description": "Diffuse endocapillary proliferative glomerulonephritis (disorder)",
            "attributes": null
          },
          {
            "code": "373420004",
            "description": "Upshaw-Schulman syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "38877003",
            "description": "Rheumatoid arthritis with aortitis (disorder)",
            "attributes": null
          },
          {
            "code": "399923009",
            "description": "Rheumatoid arthritis with arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "399980009",
            "description": "Necrotizing arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "400054000",
            "description": "Rheumatoid arthritis with vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "400130008",
            "description": "Temporal arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "402416000",
            "description": "Urticarial vasculitis with monoclonal immunoglobulin M component, Schnitzler (disorder)",
            "attributes": null
          },
          {
            "code": "402433007",
            "description": "Rheumatoid arthritis with nailfold and finger-pulp infarcts (disorder)",
            "attributes": null
          },
          {
            "code": "402655006",
            "description": "Necrotizing cutaneous vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402656007",
            "description": "Urticarial vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402657003",
            "description": "Necrotizing vasculitis secondary to connective tissue disease (disorder)",
            "attributes": null
          },
          {
            "code": "402658008",
            "description": "Serum sickness type vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402659000",
            "description": "Drug-induced necrotizing vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402660005",
            "description": "Necrotizing vasculitis secondary to infection (disorder)",
            "attributes": null
          },
          {
            "code": "402661009",
            "description": "Paraneoplastic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402662002",
            "description": "Necrotizing vasculitis due to mixed cryoglobulinemia (disorder)",
            "attributes": null
          },
          {
            "code": "402663007",
            "description": "Pustular vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402664001",
            "description": "Localized cutaneous vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402746001",
            "description": "Capillaritis caused by drug (disorder)",
            "attributes": null
          },
          {
            "code": "402855009",
            "description": "Normocomplementemic urticarial vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "402856005",
            "description": "Acute hemorrhagic edema of childhood (disorder)",
            "attributes": null
          },
          {
            "code": "402859003",
            "description": "Necrotizing vasculitis of undetermined etiology (disorder)",
            "attributes": null
          },
          {
            "code": "402958005",
            "description": "Pustular vasculitis caused by gonococcal bacteraemia (disorder)",
            "attributes": null
          },
          {
            "code": "403189002",
            "description": "Erythrocyanosis with nodules (disorder)",
            "attributes": null
          },
          {
            "code": "403443000",
            "description": "Behçet's disease affecting oral mucosa (disorder)",
            "attributes": null
          },
          {
            "code": "403510002",
            "description": "Lupus erythematosus-associated urticarial vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "403511003",
            "description": "Lupus erythematosus-associated necrotizing vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "403518009",
            "description": "Scleroderma-associated necrotizing vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "403616000",
            "description": "Drug-induced lymphocytic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "405810005",
            "description": "Cogan's syndrome (disorder)",
            "attributes": null
          },
          {
            "code": "407529009",
            "description": "Primary systemic arteritis (disorder)",
            "attributes": null
          },
          {
            "code": "407530004",
            "description": "Primary systemic vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "414297000",
            "description": "Frosted branch angiitis (disorder)",
            "attributes": null
          },
          {
            "code": "41486008",
            "description": "Eczematid-like purpura of Doucas and Kapetanakis (disorder)",
            "attributes": null
          },
          {
            "code": "416703007",
            "description": "Retinal vasculitis due to polyarteritis nodosa (disorder)",
            "attributes": null
          },
          {
            "code": "417019000",
            "description": "Retinal arteriolitis (disorder)",
            "attributes": null
          },
          {
            "code": "417303004",
            "description": "Retinal vasculitis due to systemic lupus erythematosus (disorder)",
            "attributes": null
          },
          {
            "code": "417544004",
            "description": "Segmental retinal periarteritis (disorder)",
            "attributes": null
          },
          {
            "code": "427213005",
            "description": "Autoimmune vasculitis (disorder)",
            "attributes": null
          },
          {
            "code": "427356003",
            "description": "Eosinophilic vasculitis of skin (disorder)",
            "attributes": null
          },
          {
            "code": "438476003",
            "description": "Autoimmune thrombotic thrombocytopenic purpura (disorder)",
            "attributes": null
          },
          {
            "code": "439007008",
            "description": "Acquired thrombotic thrombocytopenic purpura (disorder)",
            "attributes": null
          },
          {
            "code": "441322009",
            "description": "Drug induced thrombotic thrombocytopenic purpura (disorder)",
            "attributes": null
          },
          {
            "code": "444819004",
            "description": "Polyarteritis of kidney (disorder)",
            "attributes": null
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